Matenda a mtima wa Kawasaki Matenda

Matenda a Kawasaki (KD), omwe amatchedwanso kuti mucocutaneous lymph node syndrome, ndi matenda opweteka kwambiri osadziwika, omwe nthawi zambiri amakhudza ana ndi ana. Matenda a Kawasaki ndi matenda osadziwika, omwe amakhalapo kwa masiku khumi ndi awiri. Koma mwatsoka, ana omwe ali ndi matenda a Kawasaki omwe sagwidwa ndi nkhanza akhoza kukhala ndi mavuto osatha a mtima, makamaka kuvutika kwa mitsempha yamtendere , yomwe ingayambitse matenda a mtima komanso imfa yadzidzidzi .

Zizindikiro

Mwamtheradi, zizindikiro za matenda a Kawasaki zimaphatikizapo kutentha thupi, kuthamanga, kupukuta kwa maso, kutupa kwa mitsempha yotupa m'kati mwa khosi, mitengo ya kanjedza yofiira ndi michere, kutupa kwa manja ndi mapazi, ndi tachycardia (kuthamanga kwa mtima mwamsanga) komwe sikuli mpaka kutentha kwa malungo. Ana awa nthawi zambiri amadwala, ndipo makolo awo nthawi zambiri amazindikira kufunika kowatengera kwa dokotala.

Ichi ndi chinthu chabwino chifukwa chodziŵa bwino ndi kuchiza mwanayo mofulumira ndi gamma globulin (IVIG) yomwe imakhala yowonongeka ingathandize kwambiri poteteza mavuto a mtima wa nthawi yaitali.

Zovuta Zovuta za Cardiac

Pa matenda aakulu, mitsempha ya mthupi yonse imatenthedwa (matenda otchedwa vasculitis ). Matendawa amatha kupanga mavuto ambiri a mtima, kuphatikizapo tachycardia; kutupa kwa mtima ( myocarditis ), yomwe nthawi zina ingayambitse kuopsa kwa mtima, kuopseza moyo ; ndi kuchepetsa mitral kubwerera .

Matendawa akatha, nthawi zambiri mavutowa amatha.

Zovuta Zotsatira za Katemera

Nthaŵi zambiri, ana omwe ali ndi matenda a Kawasaki, omwe ali odwala monga momwe alili, amachita bwino pamene matenda aakulu akuyenda. Komabe, pafupifupi mwana mmodzi mwa ana asanu omwe ali ndi matenda a Kawasaki omwe sagwilitsidwe ndi IVIG adzakhala ndi zochitika zogwiritsira ntchito mitsempha yamakono (CAA).

Matenda amenewa - kutulutsa gawo la mitsempha - amatha kuwonetsa mitsempha yotsekemera, ndipo imayambitsa matenda a mtima. Matenda a mtima akhoza kuchitika nthawi iliyonse, koma chiopsezo chimakhala chapamwamba pa mwezi umodzi kapena ziwiri pambuyo pa matenda a Kawasaki. Chiopsezocho chimakhala chokwanira kwa zaka pafupifupi ziwiri, ndiye chimachepa kwambiri.

Ngati CAA yakhazikitsa, chiopsezo cha matenda a mtima chimakhala chokwera kwamuyaya. Kuwonjezera apo, anthu omwe ali ndi CAA amawoneka kuti amakhala okonzeka kukhala ndi matenda a mitsempha yambiri yosafika nthawi yayitali pafupi kapena pafupi ndi malo a aneurysm.

CAA chifukwa cha matenda a Kawasaki zikuwoneka kuti ndi ofala kwambiri kwa anthu omwe ali a ku Asia, Pacific Islander, Puerto Rico, kapena mbadwa za ku America.

Anthu omwe amavutika ndi matenda a mtima chifukwa cha CAA amakhala ndi mavuto omwewo monga omwe ali ndi matenda ena amtundu waumphawi - kuphatikizapo mtima wosalimba komanso kufa kwadzidzidzi imfa.

Kupewa Matenda a Cardiac

Kuchedwa koyamba ndi IVIG kwasonyezedwa kuti ndi kotheka kwambiri popewera mphamvu zamakono zamagetsi. Koma ngakhale pamene IVIG imagwiritsidwa ntchito moyenera, nkofunika kufufuza ana omwe ali ndi matenda a Kawasaki kuti athe kukhala ndi CAA.

Zojambula zojambula zithunzi zimathandiza kwambiri pankhaniyi popeza CAA kawirikawiri ikhoza kudziwika ndi mayeso a echo.

Mayeso oyenera ayeneranso kuchitidwa mwamsanga pamene matenda a Kawasaki apangidwa, ndipo patapita milungu ingapo kwa miyezi iwiri yotsatira. Ngati CAA ikupezeka kuti ilipo, chiwerengerocho chikhoza kulingalira kukula kwake (zikuluzikulu zamadzimadzi ndizoopsa). N'zotheka kuti pitirizani kuwunikira, mwinamwake ndi mayesero opsinjika maganizo kapena catheterization ya mtima , kuti muthe kuwunika kulemera kwake kwa thupi.

Ngati CAA ilipo, mankhwala opatsirana ndi aspirin ochepa (kuteteza thrombosis) kawirikawiri amalembedwa. Pankhaniyi, mwanayo ayenera kukhala ndi katemera wa pachakudya kuti asatenge fuluwenza komanso kupewa Reye's Syndrome .

Nthaŵi zina CAA ndi yochuluka kwambiri moti mitsempha yamakono opitirira opaleshoni iyenera kuganiziridwa.

Makolo a ana omwe ali ndi CAA ayenera kukhala atcheru ku zizindikiro za angina kapena matenda a mtima. Kwa ana aang'ono kwambiri, izi zingakhale zovuta, ndipo makolo ayenera kuyang'ana kusunthira kapena kusanza kosadziwika bwino, kupsa mtima kosadziwika kapena thukuta, kapena kulira kosawerengeka komanso kwanthawi yaitali.

Chidule

Ndi chithandizo chamakono cha matenda a Kawasaki, mavuto aakulu a mtima wam'tsogolo nthawi zambiri amatha kupeŵa. Ngati matenda a Kawasaki amatsogolera ku CAA, komabe kuyesa ndi chithandizo chamanyazi kungalepheretse zotsatira zoopsa.

Chinsinsi choletsa matenda a mtima ndi matenda a Kawasaki ndi makolo kuti atsimikizire kuti ana awo ayesedwa mwamsanga pa matenda alionse omwe amafanana ndi matenda a Kawasaki, kapena chifukwa cha matenda alionse omwe amawawoneka kuti ndi oopsa kwambiri.

Chitsime:

Newburger JW, Takahashi M, Gerber MA, ndi al. Kuzindikira, chithandizo, ndi chithandizo cha nthawi yaitali cha matenda a Kawasaki: ndemanga kwa akatswiri a zaumoyo ku Komiti Yachiwombankhanga, Matenda a Endocarditis ndi Matenda a Kawasaki, Bungwe la Matenda a Maganizo ku Young, American Heart Association. Chizungulire 2004; 110: 2747.

Matenda a Kawasaki. Mu: Buku Lofiira: 2015 Lipoti la Komiti Yothetsera Matenda Opatsirana, 30th, Kimberlin DW, Brady MT, Jackson MA, Long SS (Eds), American Academy of Pediatrics, Elk Grove Village, IL 2015. p.49