Vutoli ndi Nthawizina Ophatikizidwa ndi Zina Zina za Rheumatic Diseases
Mwachidule
Vasculitis ndi vuto losafunika lomwe limaphatikizapo kutupa mitsempha ya magazi. Matenda a mthupi amayamba pamene ma chitetezo cha mthupi lanu amatha kuwononga mitsempha yanu. Zonse mwa mitsempha ya thupi ya mthupi-mitsempha (yomwe imanyamula magazi kutali ndi mtima wanu), mitsempha (yomwe imanyamula magazi kumtima mwako), ndi ma capillaries (omwe amagwirizanitsa mitsempha yaying'ono ndi mitsempha) - akhoza kuthandizidwa.
Kutupa kwa chotengera cha magazi kungayambitse kuperewera kapena kutseka, komwe kumachepetsa kapena kuteteza magazi. Kawirikawiri, chotengera cha magazi chomwe chimakhudzidwa chimatha kutambasula ndi kufooketsa, ndipo chimayambitsa aneurysm.
Zimayambitsa
Choyambitsa matenda a shuga sichidziwika bwino kapena kumveka. Amakhulupirira kuti matenda, machitidwe a mankhwala, ndi matenda omwe amadzimadzimitsa okha angathe kuchititsa. Vasculitis ingagwirizanitsidwe ndi matenda ena a rheumatic , monga lupus , nyamakazi ya nyamakazi , ndi matenda a Sjogren- koma odwala ambiri omwe ali ndi matenda a shuga alibe chilichonse mwa izi. Malingana ndi chifukwa chake, mankhwalawa amatha kukhala ofatsa, oopsa, kapena oopsa. Zitha kuchitika ngati chimodzi mwa zizindikiro kapena zochitika zambiri.
Zizindikiro ndi Zizindikiro
Zizindikiro ndi zizindikiro zosiyana ndi zizindikiro za vasculitis zimasiyana, malinga ndi mtundu wa magazi ndi ziwalo zomwe zimagwira ntchito. Zizindikiro zambiri zimaphatikizapo kutentha thupi, kusowa kwa njala, kufooka, kutopa, ndi ululu.
Zizindikiro zomwe zimagwirizana kwambiri ndi gawo la thupi lomwe likukhudzidwa ndi izi:
- Khungu - utoto wofiira / mawanga, mitsempha, kapena zilonda zam'mimba
- Mafungo - mpweya wochepa, kutsokomola
- Mitsempha - kufooka kapena kufooka pamapeto
- Mabala - mabala, ululu, ndi nyamakazi
- Matenda a m'mimba - zilonda zam'mimba, ululu wamimba, kutuluka m'mimba
- Sinus ndi ENT-kutupa kutupa, kutupa kwa khutu pakati, zilonda zamphuno, kutaya kwa kumva
- Maso - ofiira, okongola, kapena maso opsa, maso ophwanyika, kutengeka kowala, khungu
- Ubongo - kupweteka mutu, kusintha kwa maganizo, kusintha kwa ziwalo
Kudziwa
Monga momwe matenda ambiri amachitira, matenda a vasculitis amachokera pamagulu osiyanasiyana omwe amapeza zizindikiro ndi zizindikiro, mbiri yachipatala, kuunika kwa thupi, ndi zotsatira za mayesero. Mayeso ena amagazi angasonyeze zizindikiro za kuchepa kwa magazi (hemoglobin ndi hematocrit test ) ndi zizindikiro zosadziwika za kutupa ( mlingo wa erythrocyte sedimentation ndi pro-proactive protein ). Kuyezetsa magazi kwina, ANCA (anti-neutrophil antitopidomic antibodies), imagwiritsidwa ntchito ngati chizindikiro chodziƔika ndi mankhwala osokoneza bongo.
Kuponderezedwa kwa magazi kungakwezeke, makamaka pamene pali kugwirizana kwa impso. MaseƔera apamwamba a maselo kapena maselo a magazi omwe amapezeka mu urinalysis angathenso kusonyeza kugwiriridwa kwa impso. Electrocardiogram (EKG) kapena mtima echocardiogram imagwiritsidwa ntchito kuyang'ana zovuta zirizonse zokhudzana ndi mtima. Chifuwa cha X-ray, mapulogalamu a m'mapapo, mimba ya ultrasound, zilembo za CT, ndi MRI angiography kuyang'ana mitsempha ya magazi onse amayesedwa kuti athandizidwe.
Kufufuza minofu ndi njira ina yowunika mitsempha ya mthupi chifukwa cha ziphuphu kapena kuwonongeka kwa minofu.
Kuchiza
Mankhwala oyenera kutero adzadalira mtundu wa vasculitis ndi ziwalo zomwe zikukhudzidwa, komanso kukula ndi kukula kwa chikhalidwecho. Kawirikawiri, mankhwala amaperekedwa kuti athetse kutupa, ma immunosuppressants angagwiritsidwe ntchito pochiza chitetezo cha m'thupi, ndipo mankhwala ena amathandiza kuchepetsa zizindikiro zinazake. Glucocorticoids, omwe amatchulidwa kuti steroids , ndiwopambana kwambiri pochiza matenda a shuga.
Mitundu
Pali mitundu 20 yosiyana yomwe imatchedwa vasculitis, monga:
- Matenda a Behcet
- Matenda Ogwedeza
- Central Nervous System Vasculitis
- Churg-Strauss Syndrome
- Cryoglobulinemia
- Giant Cell Arteritis
- Henoch-Schonlein Purpura
- Microscopic Polyangiitis
- Polyarteritis Nodosa
- Polymyalgia Rheumatica
- Chifuwa chachikulu cha Vasuluitis
- Arthaitis wa Takayasu
- Granulomatosis ya Wegener
Mfundo Yofunika Kwambiri
Ngakhale kuti mankhwala a vasculitis amaonedwa kuti ndi osowa kwambiri, pali vuto lodziwika bwino lomwe limagwirizana ndi matendawa. Palibe mankhwala ochizira mthupi, koma matenda oyambirira ndi mankhwala amatha kuthandizira kuthetsa zizindikiro komanso kuyendetsa chiwonongeko cha minofu ndi ziwalo.
Zotsatira:
> Paul A. Monach, MD, PhD ndi Peter A. Merkel, MD, MPH. Vasculitis. American College of Rheumatology Patient Education. Kusinthidwa May May 2015.
Kodi Vasculitis Ndi Chiyani? Johns Hopkins Vasculitis Center. Johns Hopkins Mankhwala.