Maselo amkati mwa thupi ndi mbali zing'onozing'ono zomwe zimatchedwa mitochondria (pafupifupi 1,000 pa selo). Mitochondria imapangitsa mphamvu maselo athu ayenera kukula ndikugwira ntchito. Ngati mitochondria yowonongeka kapena yosagwira ntchito, maselo sangathe kuchita ntchito zawo ndipo akhoza kuvulala kapena kufa. Maselo ovulala kapena operewera amawononga matenda a mitochondrial.
Matenda a Mitochondrial angakhale ovuta kudziwa chifukwa matendawa amatha kukhala ndi zizindikiro zosiyanasiyana, kuyambira wofatsa mpaka wolimba. Pali mazana a mitundu yosiyanasiyana ya matenda a mitochondrial. Mtundu umene mumadalira ndi omwe maselo amakhudzidwa. Mavuto angayambe pa kubadwa kapena kuchitika mtsogolo. Ambiri amapezeka ali mwana, ngakhale kuti akuluakulu amayamba kukhala ofala kwambiri. Matenda a Mitochondrial amakhudza pakati pa 40,000 ndi 70,000 Achimereka, omwe amapezeka m'modzi mwa obadwa 2,500 mpaka 4,000.
Matenda a Mitochondrial ndi matenda . Matendawa amatha kulandira kuchokera kwa makolo anu kapena chifukwa cha kusintha kwadzidzidzi mu DNA yanu. Mankhwala a mitochondria amatha kuvulala ndi mankhwala osokoneza bongo kapena kuwonongeka kwa mamasulidwe aulere (ma molekyulu owononga). Mitundu yambiri ya kusintha kwa majini ingayambitse matendawa. Komabe, kusinthika komweko mwa anthu awiri osiyana sikutheka kuwonetsa zizindikiro zomwezo.
Zizindikiro ndi Zizindikiro
Chifukwa mitochondria alipo 90 peresenti ya maselo athu, ziwalo zosiyanasiyana zingakhudzidwe kuphatikizapo ubongo ndi minofu. Machitidwe okhudzidwa kwambiri ndiwo ubongo, mtima, chiwindi, mafupa a chifuwa, impso, ndi endocrine ndi machitidwe opuma. Zizindikiro zomwe mumadalira kuti maselo ndi ziwalo zimakhudzidwa bwanji, izi zingaphatikizepo:
- Ubongo: kuchepa kwachitukuko, kutaya mtima, kupweteka , kugwidwa maganizo
- Mitsempha: zofooka, zopweteka
- Minofu: zofooka, mawu otsika, kupweteka, kupweteka
- Matenda a mtima
- Maso: kusokoneza , kutayika kwa masomphenya
- Matenda a impso
- Matenda a kupuma
- Kumva kutayika
Zizindikiro zina zimaphatikizapo matenda a m'mimba , zovuta kumeza, matenda a mtima, matenda a chiwindi, shuga , lactic acidosis, ndi kuwonjezeka kwa kutenga matenda. Kwa ana, matendawa angayambitsenso kukulirakulira ndi kuchepa kwachitukuko. Kuzindikira matenda a mitochondrial nthawi zambiri zimakhala zovuta chifukwa zizindikiro zimasiyana ndipo zimatha kufanana ndi zina. Njira zambiri zogwirira ntchito m'thupi, malo atatu kapena ambiri, nthawi zambiri zimasonyeza matenda a mitochondrial.
Chithandizo
Matenda ambiri a mitochondrial matenda amatha kupezeka kupyolera mu mitsempha yambiri. Njira zina zoyesera zimaphatikizapo kuyesedwa kwa magazi , kuyezetsa magazi , ndi kuyesa kwa enzyme. Zosokoneza minofu ndi mayesero ena zingakhale zodula kwambiri, ndipo zimachititsa kuti milandu ipezedwe pazinthu zachipatala zokha.
Palibe mankhwala a mitochondrial matenda. Mavitamini-thiamine ( B1 ), riboflavin (B12), vitamini C , vitamini E, Lipoic acid , ndi coenzyme Q10 - angathandize kuthana ndi matenda ena. Kupewa nkhawa kungathandizenso kuchepetsa zizindikiro.
Ofufuza tsopano akuyang'ana mankhwala omwe angalepheretse lactic acid buildup yokhudzana ndi matenda a mitochondrial. Ena akuyesa zakudya zochepa kwambiri za kagawidini kuti achepetse ntchito ya mitochondria.
Kugwirizanitsa Kulephera kwa Mitochondrial kwa Matenda Ena
Ochita kafukufuku akuphunzira matenda a mitochondrial chifukwa cha zizindikiro zina monga khansa, matenda a Parkinson , matenda a Alzheimer , ndi matenda a mtima. Kuwonongeka kwa mitochondria kumalingaliridwa kuti ikugwirizana ndi zonsezi. Kuwonongeka kwa mitochondrial kungakhale mbali ya ukalamba.
> Zotsatira:
> Foreman, J. Matenda angakhudze mphamvu mu maselo athu. The Boston Globe , June 17, 2003.
> Mgwirizano wa Mitochondrial Disease Foundation.