CAH Zizindikiro Zingatheke Mimic PCOS
Poganizira kafukufuku wa polycystic ovary syndrome ( PCOS ), ndiye kuti dokotala ayenera kuganizira mofulumira-kubwezeretsa congenital adrenal hyperplasia (CAH), nayenso. Ichi ndi chifukwa chakuti matenda awiriwa amakhala ndi zizindikiro zomwezo.
Kutha kwa masiku ochedwa Congenital Adrenal Hyperplasia
Congenital adrenal hyperplasia ndi kagulu kamene kamatengera matenda omwe imayambitsa matenda a enzyme.
Ziphuphu zamtunduwu zomwe zimapezeka panopa (kubadwa) zimakhudza mavitamini angapo omwe amafunikira kuti apange mahomoni oyenera a adrenal cortex.
Pafupifupi 95 peresenti ya CAH milandu imayambitsidwa ndi kusowa kwa enzyme 21-hydroxylase. Thupi silingakhoze kupanga kuchuluka kokwanira kwa ma makoni awiri adrenal steroid-cortisol ndi aldosterone-pamene ma enzyme 21-hydroxylase akusowa kapena akugwira ntchito pamunsi wochepa. Izi zimapangitsa kuti mahomoni asamayende bwino, kuteteza kapangidwe kake ka aldosterone ndi cortisol, ndipo adrenal cortex imayamba kupanga androgens (mahomoni amphongo a steroid), zomwe zimayambitsa zikhalidwe zachikazi pakati pa akazi. Mu kachitidwe kameneka ka CAH, kuchepetsa mchere kumatha kusintha kwambiri, kumabweretsa kusamvana kwa electrolyte, kutaya madzi, ndi chikhalidwe cha mtima.
Ngakhale odwala ambiri atapezeka kuti atangobereka kumene, pali mtundu wa matendawa omwe amayamba mtsogolo, nthawi zambiri ali wachinyamata kapena akukula-amatchedwa kuti si yachikale kapena yochedwa CAH.
Anthuwa akusowa mavitamini omwe ali oyenera pa kupanga cortisol. Kupanga mankhwala a Aldosterone sikunakhudzidwe, choncho mtundu uwu wa matendawo ndi wochepa kwambiri kusiyana ndi mawonekedwe obadwa nawo ndipo amasonyeza zizindikiro zomwe nthawi zambiri zimalakwika ndi PCOS monga:
- Kukula msanga kwa ubweya wa pubic
- Nthawi yosasamba
- Hirsutism (tsitsi losafuna kapena lowonjezera)
- Ziphuphu zazikulu (pamaso ndi / kapena thupi)
- Matenda okhuta pakati pa 10 peresenti mpaka 15 peresenti ya atsikana omwe ali ndi CAH
Kuzindikira kwa CAH
Congenital adrenal hyperplasia imafalitsidwa ndi majini. Ayuda a ku Eastern Europe (Ashkenazi) ali ndi chiopsezo chowonjezereka chokhala ndi matendawa, poyerekeza ndi anthu ambiri. Popeza kuti CAH ndi matenda obwera chifukwa cha autosomal , makolo onse ayenera kunyamula njira yowonongeka yoperekera kwa mwana wawo.
Chifukwa cha kufala kwa chikhalidwechi, anthu ambiri amadziwa kuti ali ndi chiopsezo m'banja lawo ndipo amadziwa dokotala wawo kuti adziwe kuti akufunikira kuyang'ana mavitamini. Dokotala akhoza kuyambitsa mkodzo ndi kuyezetsa magazi kuti ayang'ane mawonekedwe osayenera a cortisol kapena mahomoni ena. Maseŵera owonjezereka a androjeni angathenso kuganiziridwa pamene akufufuza. Mbiri yokhudza mbiri ya banja komanso matenda a thupi ndizofunikira kuti dokotala adziwe bwinobwino.
Njira Zothandizira
Mapiritsi oletsa kubereka amakhala othandiza kuthetsa kusamba, kuchepa kwa achule, komanso nthawi zina kutaya tsitsi. Ngati izi sizili zogwira mtima pochita zizindikiro, kapena dokotala amamva kuti mapiritsi oletsa kubereka sakuyenera, angaganize kuti akukupatsani mankhwala ochepa a mankhwalawa.
Komabe, mankhwala samakhala a moyo nthawi zonse.
Kwa anthu omwe ali ndi CAH yachilendo ndi vuto la aldosterone, mankhwala monga fludrocortisone (Florinef) adzasunga mchere m'thupi. Makanda amalandira mchere wothandizira (monga mapiritsi osweka kapena njira), pamene okalamba omwe ali ndi mitundu ya CAH amadya zakudya zamchere.
Mankhwala osokoneza bongo ndi regimen nthawi zambiri amadziwika ndi dokotala wanu ndipo amadalira kukula kwa zizindikiro.
> Chitsime:
> National Adrenal Diseases Foundation. Congenital Adrenal Hyperplasia (CAH).