Mavuto Ambiri Amene Amakhala nawo Amachititsa Nkhani Zokhazikika
Matenda a Kartagen, ndi matenda omwe sakhala obadwa nawo omwe amayamba chifukwa cha zofooka m'magazi . Ndi autosomal recessive , kutanthauza kuti zimangochitika ngati makolo onse ali ndi jini. Matenda a Kartagen amakhudza pafupifupi anthu 30,000, kuphatikizapo amuna onse.
Zimadziwikiratu chifukwa cha zinthu ziwirizikuluzikuluzikulu: choyambirira ciliary dyskinesia ndi inversus.
Ciliary Dyskinesia
Mankhwala opuma akupuma mphuno, uchimo, khutu la pakati, mazira a eustachian , mmero, ndi mpweya wopuma ( trachea , bronchi , ndi bronchioles ). Tsamba lonseli lili ndi maselo apadera omwe amawoneka ngati tsitsi, otchedwa cilia. Cilia inafuta mamolekyulu a fumbi, utsi, ndi mabakiteriya pamwamba ndi pamphuno.
Pankhani ya ciliary cysary dyskinesia yokhudzana ndi Kartagener Syndrome, cilia ndi yopanda pake ndipo siigwira bwino. Izi zikutanthauza kuti manyowa ndi mabakiteriya m'mapapu sangathe kuthamangitsidwa, ndipo chifukwa chake, matenda opatsirana nthawi zambiri, monga chibayo, amayamba.
Cilia amakhalansopo m'magulu a ubongo komanso m'thupi. Anthu omwe ali ndi matenda a Kartagener angakhale ndi mutu komanso mavuto.
Sitima Inversus
Inversus imachitika pamene mwanayo ali m'mimba. Zimayambitsa ziwalo kukhala ndi mbali yolakwika ya thupi, kusintha malo oyenera.
Nthaŵi zina, ziwalo zonse zingakhale chiwonetsero cha galasi, pomwe nthawi zina ziwalo zina zimasinthidwa.
Zizindikiro
Zambiri mwa zizindikiro za Kartagener Syndrome zimachokera ku kusatheka kwa kupuma kwa cilia kugwira ntchito molondola, monga:
- Matenda a sinus
- Matenda afupipafupi a m'mapapo, monga chibayo ndi bronchitis
- Bronchiectasis - kupweteka kwa mapapo kuchokera ku matenda opatsirana
- Matenda afupipafupi
Chizindikiro chofunika chomwe chimasiyanitsa matenda a Kartagener kuchokera ku mitundu ina ya ciliary cysary dyskinesia ndi kuika ziwalo zamkati kumbali yotsutsana ndi zachibadwa (zotchedwa inversus). Mwachitsanzo, mtima uli kumbali yoyenera ya chifuwa m'malo mwamanzere.
Kudziwa
Matenda a Kartagen amadziwika ndi zizindikiro zitatu zazikulu za sinusitis, bronchiectasis ndi inversus. Chifuwa cha x-rays kapena computed tomography (CT) amawunikira amatha kuona kusintha kwa mapapu kukhala ndi matenda a matenda. Kutenga kachidutswa ka chipinda cha trachea, mapapo kapena machimo amatha kulola kuunika kochepa kwa maselo omwe amayendera njira yopuma, yomwe imatha kuzindikira chosowa cilia.
Chithandizo
Kusamalidwa kwa munthu amene ali ndi matenda a Kartagener kumaphatikizapo kupewa kupewa matenda opatsirana komanso kuyambitsa chithandizo chilichonse chomwe chingachitike. Maantibayotiki amatha kuthetsa sinusitis, ndipo kupatsirana mankhwala ndi kupuma kumathandiza ngati matenda aakulu a mapapu akuphulika. Miphika yaying'ono ikhonza kuperekedwa kudzera m'matope kuti alole matenda ndi madzi akumwa kuchokera pakati pa khutu. Akuluakulu, makamaka abambo, akhoza kukhala ovuta kubereka ndipo angapindule ndi kufunsa katswiri wa chonde. Muzochitika zazikulu, anthu ena angafunike kuika mapepala onse.
Kwa anthu ambiri, chiwerengero cha matenda opuma amayamba kuchepa pafupi ndi zaka makumi awiri, ndipo chifukwa chake, anthu ambiri omwe ali ndi matenda a Kartagener amakhala pafupi ndi moyo wachikulire.
Chitsime:
"Kodi Primary Ciliary Dyskinesia Ndi Chiyani?" PCD Foundation . 24 Nov 2008
Mpunga, S. "Kartagener Syndrome". Healthline , 2013.