Chizindikiro cha Ataxia cha Gluten: Zimene Mungayembekezere

Mavuto ndi Gawo, Kusinkhasinkha M'zoopsa, Zizindikiro Zina

Zizindikiro za atxia ya gluteni, matenda a ubongo omwe amayamba chifukwa cha mapuloteni a gluten , amatha kuchoka ku mavuto osagwedera komanso kusagwedezeka kwa mapazi kuti akule. Mukhoza kukhala ndi masomphenya awiri, kapena nkhani zowononga chikhodzodzo.

Zizindikiro zanu zingayambe pang'onopang'ono kapena zikhoza kuwoneka mwadzidzidzi, koma mwina siziphatikizapo zizindikiro za kugaya zomwe zingasonyeze matenda a celiac .

Ochita kafukufuku amayamba kufotokozera atxia ya gluteni , ndipo si madokotala onse omwe amavomereza kuti ndizovomerezeka. Kuonjezerapo, palibe mayesero ochiritsidwa azachipatala kuti azindikire a gluten acyxia, ngakhale afufuzidwe apamwamba pa matenda a celiac ndi chisamaliro cha gluten chomwe sichinafuneke kuti apange njira yodziwira anthu omwe akudandaula kuti ali nawo.

Komabe, maphunziro osiyanasiyana azachipatala afotokoza zizindikiro za atxia ya gluten, ndipo aganiza kuti ndi angati omwe angakhale ndi atxia ya gluten .

Zizindikiro za Ataxia za Gluten Phatikizani Mavuto Okhazikika, Osakhazikika

Zizindikiro za alexia ya gluteni ndi zofanana ndi za mitundu ina ya atazia, zomwe zimapangitsa kuti zikhale zovuta kwambiri kupereka chithandizo choyenera. Odwala a gluten alixia amakhala m'ma 40s kapena m'ma 50s pamene akupezeka, ngakhale kuti mabuku a zachipatala amalembetsa maulendo angapo omwe ali ndi ana kapena achinyamata. Amuna ndi akazi amaimirira mofananamo (mosiyana ndi matenda a celiac, kumene amayi amawerengeratu amuna ).

Kawirikawiri, anthu amazindikira mavuto awo ndi luso lawo loyendetsa galimoto yoyamba-mwazinthu zina, adzakhala ovuta kwambiri, amayenda mosagwirizana ndi chizoloƔezi chokhumudwitsa kapena kuchita zinthu zolakwika, ndipo nthawi zambiri amakhala osagwirizana kwambiri.

Odwala a gluten ataxia angayang'anenso mavuto ndi maluso abwino-motero, munthu amene ali ndi vutoli sangavutike kumangirira shati kapena kugwiritsa ntchito pensulo polemba nthawi yaitali.

Odwala ena amanenanso mawu awo kapena amavutika kulankhula, ndipo ena amavutika kumeza.

Kupeza Mavuto Kubwera Choyamba

Kafukufuku wamankhwala akufotokoza kuti aliyense amene ali ndi gluten ataxia ali ndi zizindikiro za kuchepetsa ataxia, ndipo kuti mavutowa nthawi zambiri amayenda limodzi ndi zizindikiro zokhudzana ndi matenda a mphutsi (mwachitsanzo, kumangirira pamapeto ako). Pafupifupi 80% ali ndi vuto ndi maso awo, momwe maso awo amasunthira mobwerezabwereza.

Odwala pafupifupi 60% amasonyeza umboni wa zomwe zimatchedwa "sensorimotor axonal neuropathy," zomwe zimatanthawuza kuwonongeka kwa mitsempha yomwe imayambitsa zowawa, kukhumudwa komanso kumva ululu pamapeto. Komabe, zizindikirozi nthawi zambiri zimakhala zofewa, ndipo sizikuthandizira kuti athexia, ofufuza amati.

Ngakhale kuti anthu ambiri omwe ali ndi gluten ataxia amatha kukhala ndi zizindikiro za m'mimba monga zilonda, kutsekula, kupweteka m'mimba, kupweteka m'mimba, mpweya ndi reflux . Ngakhale kuti pali zizindikiro zochepa kwambirizi, kafukufuku wina anapeza kuti odwala 24% a atxia amatha kukhala ndi matenda oopsa a matendawa.

Zizindikiro Zimalingalira Kuwonongeka Kwa Ubongo Wanu

Zizindikiro zonse za gluten za atxia zimachokera ku kuwonongeka kwa cerebellum yanu, gawo la ubongo wanu lomwe limaperekedwa poonetsetsa kuti minofu yanu ikugwira ntchito mogwirizana.

Ndipotu, 60 peresenti ya odwala omwe ali ndi gluten ataxia ali ndi umboni wa cerebellar atrophy-kwenikweni, shrinkage ya gawolo la ubongo wawo-pamene iwo amafufuzidwa ndi maginito resonance imaging (MRI). Odwala omwe sakhala ndi shrinkage yowonekera mumakono awo amasonyezabe zosavuta m'zofukufuku zachipatala kwambiri, malinga ndi ofufuza.

Matendawa amayamba kupitirira pang'onopang'ono, koma n'zotheka kuti ayende mofulumira, komanso ndi matenda a cerebellar atrophy omwe amayamba chaka chimodzi choyamba cha zizindikiro, malinga ndi Dr. Marios Hadjivassiliou, katswiri wa sayansi ya ubongo ku UK komanso wofufuzira wapamwamba mu munda wa gluten ataxia.

Kafukufuku wochitidwa ndi Dr. Hadjivassiliou akuyang'ana odwala 68 omwe ali ndi ayatini ya gluten adanena kuti 78% mwa anthu amenewo anatenga chimodzi kapena zonse ziwiri zapachilombo toyambitsa matenda , HLA-DQ2 ndi HLA-DQ8 . Zotsala za gululo zinanyamula HLA-DQ1, zomwe Dr Hadjivassiliou adaziganizira zikukhudzana ndi zizindikiro za ubongo zomwe zimachokera ku zakudya zowonongeka .

Mawu ochokera

Mu pepala lofalitsidwa mu nyuzipepala ya BMC Medicine , Dr. Hadjivassiliou ndi ena ochita kafukufuku wapamwamba anafotokoza zizindikiro zowonjezereka za gluten ataxia ndipo analongosola njira yothetsera matenda yomwe imapanga kusiyanitsa chikhalidwecho ndi matenda ena a gluten ndi a tirigu: matenda a celiac, gluten kukhudzidwa , dermatitis herpetiformis ndi zokolola za tirigu.

Komabe, kafufuzidwe ndi mgwirizano zambiri zidzafunika kuti adokotala asamalandile kuti adatetezedwe ndi gluten ngati matenda, ndipo ayesetse anthu nthawi zonse ngati akusonyeza zizindikiro.

Ngati mumakhulupirira kuti muli ndi zizindikiro za atxia ya gluteni, choyamba muyenera kukambirana ndi dokotala wanu za vutoli komanso zomwe mwakumana nazo. Zinthu zambiri, kuphatikizapo mitundu ina ya ataxia, zingachititse zizindikiro zofanana. Komanso, musayambe kudya zakudya za gluten musanalankhule ndi dokotala wanu, popeza kuchotsa mchere kungapangitse zotsatira zanu zowononga matenda osakwanira.

Zotsatira:

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Hadjivassiliou M. et al. Katemera wa Gluten Ataxia. Journal of Neurology, Neurosurgery ndi Psychiatry. 2003; 74: 1221-1224.

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