Matenda otuluka m'magazi, omwe nthawi zina amatchedwa coagulopathy, ndizochitika zomwe zimakupangitsani kukhala ndi magazi kusiyana ndi munthu wamba. Thupi silingathe kupanga chovala bwino. Izi zimaphatikizapo chimodzi mwa ziwalo za coagulation (kutaya magazi ndi kutseka).
Chipangizo cha coagulation chiyenera kukhala chokwanira, osati kuchuluka kwa magazi komanso osati kutseka kwambiri.
Mbali imodzi ya ndondomekoyi imaphatikizapo mapiritsi , limodzi la maselo athu. Gawo lachiwiri likupezeka mu gawo la madzi mwazi wathu wotchedwa coagulation. Nthawi zina anthu amatchula anthu omwe ali ndi matenda otha magazi monga "azungu omasuka."
Zizindikiro
Zizindikiro za matenda a magazi zimasiyana kwambiri. Si odwala onse omwe ali ndi matenda otha magazi omwe ali ndi zizindikiro zonsezi.
- Mphuno yamphongo kapena nthawi yaitali
- Kutuluka magazi kwa nthawi yaitali kapena kwa nthawi yaitali
- Kuchita msambo nthawi zambiri kumatchedwa menorrhagia komanso kumwa magazi pambuyo pa kubereka (pambuyo pa kubadwa)
- Kuthamanga kwanthawi yaitali pambuyo pa ndodo ya singano (magazi atenge kapena jekeseni ngati katemera)
- Kuthamanga magazi kwambiri pakapita kapena pambuyo pa opaleshoni kumafuna kuyesetsa kwina kuti asiye magazi
- Kuvunda kwakukulu kwambiri
Chifukwa chakuti mungapeze chimodzi mwa zizindikiro izi sizikutanthauza kuti muli ndi matenda a magazi. Muyenera kukambirana ndi nkhawa yanu ndi wothandizira zaumoyo wanu.
Zimayambitsa
- Olowa : Matenda ena a magazi monga hemophilia ndi Von Willebrand matenda amabadwa, kutanthauza kuti munthu wabadwa ndi matendawa.
- Matenda a chiwindi : Zokwanira za coagulation zimapangidwa kwambiri m'chiwindi. Anthu omwe ali ndi matenda akuluakulu a chiwindi sangathe kupanga zinthu zokwanira zogawanika ndipo motero amatha kutuluka magazi.
- Vuto la Vitamini K : Zambiri mwazigawo zimagwiritsa ntchito Vitamin K kuti ikhale yoyenera kotero anthu omwe Vitamini K amalephera amakhala osowa magazi.
- Thandizo la antiticoagulation : Anthu omwe amagwiritsa ntchito mankhwala osokoneza bongo (mankhwala omwe amaletsa kutsekemera) ali pangozi yowononga magazi.
- Matenda a Platelet : Ngati mapuloteni sangathe kugwira ntchito bwino, sangathe kupanga chovala choyenera chomwe chingayambitse magazi.
Mitundu
- Hemophilia : Mwinamwake vuto lodziwika kwambiri la magazi ndi hemophilia. Anthu omwe ali ndi haemophilia akusowa chimodzi mwazifukwa zawo. Dzina la mtundu wawo wa hemophilia zimadalira chomwe chikusowa. Mtundu wochuluka kwambiri ndi hemophilia A; odwala awa akusowapo 8 kuchokera ku coagulation system. Palinso hemophilia B (vuto 9 losowa) ndi hemophilia C (chosowa 11). Hemophilia imachotsedwa (kudutsa m'mabanja). Zimakhudza chromosome Y kuti anthu ambiri asokonezeke. Anthu omwe ali ndi hemophilia amatha kutuluka mwadzidzidzi kuvulala kapena mwadzidzidzi (popanda kuvulala) kutuluka magazi.
- Von Willebrand matenda : Von Willebrand matenda (VWD) matenda ambiri omwe amabwera m'magazi padziko lapansi. Zikuoneka kuti 1% mwa anthu ali ndi mtundu wina wa Von Willebrand matenda. VWD imalandiridwa komanso amuna ndi akazi akhoza kuthandizidwa chimodzimodzi. Kuchuluka kwa magazi kumasiyana kwambiri malinga ndi mtundu wa VWD umene munthu amabadwa nawo.
- Matenda a chiwindi : Pamene chiwindi sichigwira bwino bwino, sichikhoza kupanga zinthu zogwirizana. Popanda izi, odwala akhoza kukhala ndi magazi ambiri.
- Mawerengero ochepa a platelet (thrombocytopenia) : Pali zifukwa zambiri zowerengera za platelet ndizochepa kuphatikizapo khansa ya m'magazi , zotsatira za mankhwala a chemotherapy, immune thrombocytopenia (kumene chitetezo cha mthupi chimawononga mapepala).
- Matenda a Platelet : Kuphatikiza pa manambala otsika apulaneti omwe amachititsa magazi, ngati mapuloteni samagwira ntchito bwino, magazi akhoza kuchitika.
Chithandizo
Pali mankhwala ochulukirapo omwe amapezeka chifukwa cha magazi mwa munthu amene ali ndi matenda a magazi.
Mankhwala omwe asankhidwa amachokera ku chifukwa cha matenda a magazi kapena malo omwe magazi amachokera.
- Kusintha kwina : Odwala omwe ali ndi hemophilia akhoza kudzidzimitsa okha ndi mankhwala omwe amatha kuika magazi m'magazi. Masiku ano, odwala ambiri omwe ali ndi haemophilia amapereka malo omwe amathandiza kuti magazi asatayike.
- Desmopressin (yomwe imadziwikanso ndi dzina lakuti Stimate): Desmopressin ndi mankhwala omwe amachokera ku hormone vasopressin. Kuchotsa nyamakazi kumabweretsa kuwonjezereka kwa kanthawi kochepa kwa VW Wardbrand antigen ndi chinthu 8 chomwe chingalepheretse kutuluka kwa odwala omwe ali ndi hemophilia yochepa A kapena von Willebrand.
- Kupatsirana kwa Platelet : Ngati mtengo wa platelet uli wotsika kapena mapiritsi sangagwire ntchito molondola, kupatsirana kwaplatela kumaperekedwa pofuna kupewa / kuchiza magazi.
- Mazira a pulasitiki atsopano : Zosakanikirana zimapezeka mu plasma (gawo limodzi la magazi). Ngati munthu akusowa zinthu zingapo, monga chiwindi chosalimba, kulowetsedwa kwa madzi a m'madzi ozizira atsopano kungaperekedwe.
- Vitamini K : Ngati wodwalayo ngati Vitamini K akulephera, supplementation angaperekedwe.
- Antifibrinolytics : Mankhwalawa amachititsa kuti magazi asatengeke kwambiri mwa kukhazikika. Izi zimagwiritsidwa ntchito kwambiri kuti magazi asatuluke pakamwa kapena nthawi ya msambo.
Nthawi Yomwe Muwone Dokotala Wanu
Ngati mukuganiza kuti muli ndi magazi ochulukirapo, makamaka ngati anthu ena mumtundu wanu amachitanso bwino, muyenera kukambirana ndi dokotala wanu. Ngati dokotala wanu akudandaula, akhoza kuyambitsa ntchito yoyamba magazi kapena kukupatsani mankhwala a chifuwa chachikulu, dokotala yemwe amadziwika kwambiri ndi matenda a magazi.