Lymphangiomatosis ndi Lymph System

Lymphangiomatosis ndi matenda omwe matumbo ambiri (lymphangiomas) kapena kststs amakula mu thupi la thupi. Ngakhale kuti zotupazi sizili ndi khansa, zimayambitsa ziwalo za thupi ndikupweteka, kupuma kovuta, ndi zizindikiro zina zosiyanasiyana malingana ndi kumene zikuchitika. Lymphangiomas ikhoza kukula m'mafupa, ziwalo zogwirizana, ndi ziwalo za thupi, ndipo zimatha kulepheretsa, kupondereza, kapena kuwononga ziphuphu.

Chimene chimayambitsa lymphangiomatosis sichinadziwikebe.

Lymphangiomatosis kawirikawiri imapezeka mu makanda ndi ana ang'onoang'ono koma imachitika pa msinkhu uliwonse. Zimakhudza onse amuna ndi akazi a mafuko onse. Chifukwa lymphangiomatosis ndi yosavuta komanso yovuta kudziwa bwino, sizidziwika kuti ndi anthu angati omwe akukhudzidwa ndi izo padziko lonse lapansi.

Zizindikiro

Zizindikiro za lymphangiomatosis zimadalira kumene zilonda zikukula m'thupi.

Patapita nthaŵi, mafupa amodzi kapena angapo amalowetsedwa ndi minofu ya lymphangioma, yomwe imatchedwa matenda a Gorham. Lymphangiomas siimakula mu ubongo chifukwa thupi la lymph silikula.

Kudziwa

Kuzindikira kwa lymphangiomatosis kumadalira zizindikiro ndi kukhalapo kwa lymphangiomas ambiri m'thupi. CT (computed tomography) scan ndi maginito imaging (MRI) amagwiritsidwa ntchito poyesa matendawa. Chitsanzo cha mankhwala (biopsy) chimatengedwa kuti chithandize kutsimikizira kuti zotupa ndi lymphangiomas.

Chithandizo

Lymphangiomatosis pang'onopang'ono imafalikira patapita nthawi. Pamene zotupa zikukula, zingayambitse zizindikiro zoyipa, zina zomwe zingakhale zowopsya, monga kuchititsa kuti madzi akuyendayenda m'mapapo omwe amaletsa kupuma. Kuchotsa opaleshoni kumatuluka, koma zotupa zina zingakhale zovuta kuchotsa ngati zitayika. Mankhwala otchedwa Intron A (interferon alfa), chemotherapy, kapena mankhwala othandizira kutentha kwa dzuwa angakhale othandiza pochiza matendawa. Mankhwala ena kapena opaleshoni angakhale othandiza kuthetsa zina mwa zizindikiro kapena mavuto omwe amachititsidwa ndi lymphangiomatosis. Mwachitsanzo, chubu ikhoza kuikidwa mu chifuwa (thoracentesis) kuchotsa madzi, kapena opaleshoni ikhoza kuchitidwa msana kuti athetse mitsempha.

Zotsatira:

> "Za Lymphangiomatosis." Lymphangiomatosis & Gorham's Disease Alliance. 06 Sep 2007. Lymphangiomatosis & Gorham's Disease Alliance.

> Marom, Edith, Cesar Moran, ndi Reginald Munden. "Generally Lymphangiomatosis." American Journal of Roentgenology 182 (2004): 1068.

> Rostom, Y. "Kuchiza kwa thoracic lymphangiomatosis." Archives of Diseases Childhood 83 (2000): 138-139.