Matenda a Sturge-Weber ndi matenda a khungu ndi manjenje. Chizindikiro chake chodziwika kwambiri ndi pinki yofiira kuonekera kofiira kwambiri pa nkhope yomwe imatchedwa kuti doko la vinyo. Komabe, sikuti anthu onse omwe ali ndi banga la vinyo wamatope ali ndi matenda a Sturge-Weber. Matenda a Sturge-Weber alipo pomwe anabadwira, koma sadziwika chomwe chimayambitsa kapena ndendende momwe zimakhalira.
Zimakhudza onse amuna ndi akazi a mafuko onse.
Pali mitundu itatu ya matenda a Sturge-Weber:
- Lembani I - mtundu wochuluka kwambiri, umaphatikizapo utoto wa vinyo wa piritsi ndi angiomas ya ubongo
- Mtundu Wachiwiri - chiwonongeko cha vinyo koma palibe ubongo angioma
- Mtundu Wachitatu - ubongo angioma koma palibe vinyo wa vinyo
Zizindikiro
Zizindikiro za matenda a Weber Sturge ndi awa:
- Dothi la vinyo wamtundu - Chizindikiro ichi chokhala ndi nkhope chikhoza kukula mosiyana, koma nthawi zambiri chimakwirira khungu limodzi lapamwamba komanso pamphumi. Ikhoza kukhala yochokera ku pinki yofiira mpaka kufiira kwambiri ndipo imayambitsidwa ndi kukula kwa mitsempha yaing'ono yamagazi (capillaries) pansi pa khungu. Dothi la vinyo la piritsi likhoza kukhala lovuta kuti liwone anthu omwe ali ndi khungu lamdima.
- Kugonjetsa - Pafupifupi 75 mpaka 90 peresenti ya anthu omwe ali ndi matenda a Sturge-Weber amayamba kugunda, nthawi zambiri amayamba ndi chaka chimodzi. Mavutowa amayamba chifukwa cha kukula kwa mitsempha ya magazi (angioma) pamwamba pa ubongo, kawirikawiri kumbuyo kwa ubongo kumbali imodzimodzi ndi madontho a vinyo.
- Zofooka - Pafupifupi 25 mpaka 56 peresenti ya anthu amayamba kukhala ofooka kapena kutaya ntchito mbali imodzi ya thupi (hemiparesis), kawirikawiri kumbali yotsutsana ndi doko la vinyo.
- Kuchedwa kuchepa ndi kuchepetsa maganizo kumakhuza pafupifupi 50 mpaka 60 peresenti ya anthu.
- Mutu
- Kuwonjezeka kwa diso (glaucoma) - Pafupifupi anthu 70 pa 100 aliwonse amapanga glaucoma m'diso pafupi ndi dothi la vinyo.
Kudziwa
Matenda a Sturge-Weber angakhalepo chifukwa cha kukhalapo kwa doko la vinyo pamtunda pa diso limodzi ndi pamphumi. Kujambula tomato (CT) kapena kujambula kwa magnetic resonance (MRI) kungathe kufufuza ubongo kuti ukhalepo ndi amodzi kapena angiomas, omwe amatsimikiziridwa kuti ali ndi matendawa. Mwana amene ali ndi matenda a Sturge-Weber adzakhala ndi kafukufuku wamaganizo kuti ayang'ane zovuta za ubongo angioma, monga kugwedezeka kapena kufooka.
Chithandizo
Kuchiza kwa matenda a Sturge-Weber kumayang'ana pa zizindikiro. Ngati kugwidwa kumapezeka, mankhwala ochepetsa mankhwala osokoneza bongo monga carbamazepine (Tegretol), phenytoin (Dilantin), kapena valproic acid (Depakote, Depakene) amaperekedwa. Mankhwala amagwiritsidwa ntchito kuchepetsa ndi kulamulira glaucoma ndi mutu. Mankhwalawa amatha kuyatsa kapena kuchotsa dothi la vinyo pamasom'pamaso. Mankhwala ambiri angapangidwe.
Chitsime:
> "Kodi Sturge-Weber Syndrome ndi chiyani?" About SWS / KT / PWS. Foundation Sturge-Weber. 10 May 2007