Munthu Wosagwirizana ndi Zizindikiro Zoopsa
Megacystis microcolon intestinal hypoperistalsis syndrome (MMIH), yomwe imatchedwanso Berdon syndrome, imachokera ku matenda a minofu yosalala m'mimba ndi m'mimba. Matendawa amaletsa m'mimba, matumbo, impso, ndi chikhodzodzo kuti zisagwire bwino ntchito.
Sikudziwika bwino momwe amachitira matenda a MMIH kapena chifukwa chake. Ofufuza ena amakhulupirira kuti adzalandira cholowa chifukwa chakuti nthawi zina abale ndi alongo amakhudzidwa.
Pafupifupi milandu yonse yodziwika ndi ya atsikana. Chifukwa chimodzi chomwe chingakhale chiri chakuti MMIH ikhoza kusokonezedwa ngati kutsegula m'mimba matenda , makamaka kwa anyamata.
Zizindikiro
Zizindikiro za MMIH zimachokera ku matenda a mitsempha yosalala. Minofu ya ziwalo za mkati ndizosalala ndipo sizikula bwino mutero. Zizindikiro za MMIH ndi:
- megacystis - chikhodzodzo chachikulu chomwe chili chofooka
- microcolon - chimbudzi chachikulu kwambiri
- m'mimba hypoperistalsis - matumbo aang'ono ndi aakulu ndipo minofu yake yofooka siidya chakudya mwabwino kwambiri
Minofu ya m'mimba ndi yovuta, kumapangitsa mimba ya mwana kuyang'ana makwinya, ngati kudulira. The hypoperistalsis amachititsa kudzimbidwa ndi kutseka m'matumbo.
Kudziwa
MMIH ndi zovuta kudziwa kuti mwanayo asanabadwe. Ziwalo zosaoneka bwino monga chikhodzodzo chofutukuka komanso chosatsekedwa chikhoza kuwonedwa pa fetus ultrasound, koma sizingakhale zomveka kuti mwanayo ali ndi MMIH, kupatula ngati mwanayo ali ndi mchimwene wake ali ndi vutoli.
Mwanayo atabadwa, kuyesa thupi ndi ultrasound kumatha kudziwa ngati MMIH ilipo.
Pofufuza, madokotala akhala akuyang'ana zotsatirazi zotsatira za zizindikiro zomwe zikuwonetseratu kuti:
- Mimba yochuluka kapena yowonjezera
- Kusanza kosalala ndi kulephera kudutsa meconium (chinthu chobiriwira chakuda chopanga nyansi yoyamba ya khanda).
- Mavuto osiyanasiyana a mitsempha (omwe amachititsa kuti minofu ikhale yofewa, minofu ya mtima, ndi maselo a gland)
- Nkhani zamagetsi zimaphatikizapo microcolon, kupweteka kwa matumbo, ndi matumbo ochepa.
- Malingaliro a tsamba la mkodzo
- Nthawi zina sitimayesedwa
Chithandizo
Mwatsoka, palibe mankhwala a MMIH (Berdon Syndrome), ndipo malingaliro ndi osauka kwa ana obadwa nawo; ambiri amafa m'chaka choyamba cha moyo. Makanda angathe kudyetsedwa mwachangu ndi ming'anga yapadera, koma mtundu uwu wa mankhwala nthawi zambiri umayambitsa chiwindi chosalimba.
Madokotala ayesera kubwezera ziwalo zonse zowonongeka pakati pa makanda ndi MMIH mwa kuika. Nkhani ina mu nyuzipepala yotchedwa Transplantation mu 1999 inafotokoza atsikana atatu omwe ali ndi MMIH omwe analandira ziwalo zosiyanasiyana. Zosinthazo zinalephera mwana mmodzi, yemwe adamwalira; Mwana mmodzi anamwalira patatha miyezi 17 kuchokera ku chibayo , koma mwana wachitatu anali wamoyo ndipo panthaŵiyi.
Kuyesanso kwina kuikidwa m'magulu osiyanasiyana kwa MMIH kunachitika pa January 31, 2004. Alessia Di Matteo wa ku Genoa, Italy, analandira ziwalo zisanu ndi zitatu kuchokera kwa khanda lina: chiwindi, m'mimba, mphukira, matumbo aang'ono, matumbo akulu, matumbo, ndi awiri impso. Madokotala ku University of Miami / Jackson Memorial Hospital, kumene opaleshoniyo inachitika, patapita milungu 7 kuti Alessia ayambe bwino.
Adzafunika kupitiliza kumwa mankhwala osatsutsa kwa moyo wake wonse, koma makolo ake amaona kuti mtengo wapatali wopelekera mphatso ya moyo wapatsidwa.
Zotsatira:
Brecher, EJ Mwana amatenga ziwalo zatsopano 8 ku Miami. The Miami Herald, Lachisanu, March 19, 2004.
InfoBiogen. Matenda a Megacystis-microcolon-intestinal-hypoperistalsis.
Masetti, M., Rodrigues, MM, Thompson, JF, Pinna, AD, Kato, T., Romaguera, R. l., Nery, JR, De Faria W., Khan, MF, Verzaro, R., Ruiz, P ., Tzakis, AG (1999). Kukonzekera kwa multifisceral kwa megacystis microcolon m'mimba hypoperistalsis matenda. Kusindikiza , 68 (2), pp. 228-232.