Phunzirani Zambiri Zokhudza Zosiyana, Mavuto Omwe Amayambitsa Kuchulukitsa Matenda a Edzi
Matenda a Prune Belly, omwe amadziwikanso kuti Eagle-Barrett kapena matenda a triad, ndi vuto lobadwa limodzi ndi mavuto osiyanasiyana omwe mwana amabadwa nawo. Mavuto awa ndi awa:
- Minofu ya m'mimba kutsogolo kwa thupi ndi yofooka kapena ikusowa
- Mbali za tsamba la urinary zimakhala zosavomerezeka. Izi zimaphatikizapo kufalikira kwachilendo (kuchepa) kwa mitsempha ya mkodzo, kuwonjezeka kwa mkodzo m'mphepete zomwe zimadutsa mkodzo kuchokera ku impso kupita ku chikhodzodzo, ndi / kapena kubwerera kwa mkodzo kuchokera ku chikhodzodzo kupita ku machubu ndi mazira (otchedwa reflux vesicoureteral).
- Mwa amuna (95%), ma testes amakhala mmimba mwathu ndipo samatsikira kumtunda.
Mwina pangakhale mavuto ena a khanda m'mimba, monga msana, kupsepuka kwa m'chiuno, clubfoot, mavuto a kupuma kapena mtima, ndi mavuto a m'mimba.
Zimayambitsa Kuchulukitsa Matenda a Edzi
Chifukwa cha matendawa sichidziwika, koma ochita kafukufuku amakhulupirira kuti kusokonezeka kwa kukula kwa fetus kumayambitsa mavuto. Zikuganiziridwa kuti chinachake chimatseka gawo la fetus m'kati mwake, ndipo izi zimachititsa mbali zina za kapepalaka kukhala zopanda pake. Matenda a Prune Belly amapezeka mu 1 mwa 40,000 kubadwa kumene ku US
Kuzindikira kwa Chikhalidwe
Ultrasound pa nthawi ya mimba nthawi zina amatha kuona chitukuko chosachiritsika cha chikhodzodzo ndi mkodzo. Pamene mwanayo amakula, madzi amakula m'mimba mwake, yomwe imakhala yaikulu komanso yayikulu. Madzi amatsitsidwanso asanabereke, choncho pa nthawi ya kubadwa, mwana wakhanda amakhala ndi mimba yodwala kapena yowumitsa (motero dzina la "mimba").
Pambuyo pa kubadwa, ultrasound ndi x-ray zimatha kudziwa mtundu wa vuto la mkodzo. Matenda a Prune Belly amadziwika ndi:
- Zina kapena minofu zambiri za m'mimba sizingatheke. Izi zimapanga mawonekedwe a makwinya kapena odulira.
- Ngakhale ziwalo za minofu mpaka mafupa zikhalepo, minofu ndi yaing'ono ndi yochepa kwambiri pa chikhodzodzo.
- Khoma la m'mimba ndi lochepa thupi, mimba imasonyeza kuti ndi yaikulu komanso yotayirira, ndipo matumbo amatha kupyolera pamtambo wochepa thupi.
- Mapepala a khungu amaoneka ngati akuwoneka kuchokera mimba ya mimba kapena akudutsa m'mimba.
- Nthawi zina phokoso lochokera kumtunda kupita kumalo osungirako amatha kukhalapo ndipo nthawi zina mimba imakhala yolumikizidwa ndi chikhodzodzo kudzera mumtsinje (urachus) kapena chimbudzi.
- Kuwombera kwa nthiti kapena kupyapyala kwa chifuwa kungachititse chifuwa kukhala chopunduka kwa ana omwe ali ndi matenda.
- Chikhodzodzo chokulitsa chiripo pafupifupi nthawi zonse.
Mwatsoka, matenda a Prune Belly angakhale ndi zotsatira zoopsa pa khanda. Ziwerengero zimasonyeza kuti ana 20% amafa asanabadwe, ndipo 30% amafa chifukwa cha mavuto a impso ndi zaka ziwiri zoyambirira za moyo. Pa otsala 50% a makanda, pali mavuto osiyanasiyana okhudzana ndi ukodzo.
Prune Belly Syndrome kawirikawiri imapezeka kuti ili ndi mayina osiyanasiyana, monga mimba ya m'mimba yofooka, kupweteka kwa m'mimba m'mimba, kutaya mimba, Eagle-Barrett matenda, Obrinsky syndrome kapena triad syndrome.
Kuchiza kwa Eagle-Barrett
Palibe mankhwala a Eagle-Barrett (prune belly syndrome), koma kukonza kwa kapangidwe ka mkodzo kungapangidwe.
Madokotala ena amayesa kukonza mavuto pa mwanayo asanabadwe, koma izi zakhala ndi zotsatira zosiyana. Ana omwe amatha kugwidwa ndi matenda a mitsempha amapatsidwa mankhwala opha tizilombo komanso opaleshoni angabweretse mayesero a mnyamata kumalo ake.
Nthawi zina ngakhale mankhwala opambana, impso za mwana zimasiya kugwira ntchito (kulephereka kwa chiwerewere). Chithandizo cha izi ndi dialysis kapena kusintha kwa impso.
Njira zothandizira opaleshoni, makamaka pogwiritsira ntchito laparoscopy, zimapanga ntchito zoyenera kukonza kuti mwanayo ali ndi matenda a Prune Belly ovuta. Ngati zambiri zimaphunzira za matendawa, mankhwala amatha kuwongolera ndipo ana amathandizidwa kukhala ndi moyo wautali.
Zotsatira:
Prune Belly Syndrome Network. About Prune Belly.
Franco, I. (2001). Matenda a Prune Belly. eMedicine imapezeka pa http://www.emedicine.com/med/topic3055.htm
Leeners, B., Sauer, I., Schefels, J., Cotarelo, CL, Funk, A. (2000). Matenda a m'mimba: Njira zochiritsira zomwe zimaphatikizidwepo poyikirapo mankhwala a vesica amniotic shunt. J Clin Ultrasound, Vol. 28, No. 9, masamba 500-507.