Extranodal Lymphoma

Ngakhale ma lymphoma ali khansa zonse zomwe zimakhudza ma lymphocytes - mtundu wa selo loyera la magazi - nthawizina ndi pamene kufanana kumatha. Pali mitundu yambiri yosiyanasiyana ya ma lymphoma. Mitundu ikuluikulu ikuluikulu ndi Hodgkin's lymphoma , kapena HL, osati ya Hodgkin's lymphoma, kapena NHL . Ambiri a NHL ndi HL ali ndi mitsempha yotchedwa nodal lymphomas, kutanthauza kuti imachokera m'matumbo.

Komabe n'zotheka kuti malimymasi akwere kulikonse.

Tanthauzo: Lidphoma Yaikulu ya Extranodal

Pamene lymphoma imakhulupirira kuti inachokera kunja kwa maselo am'mimba , imatchedwa extranodal lymphoma, kapena makamaka, primary extranodal lymphoma. Nthaŵi zina, zimakhala zovuta kufotokoza komwe thupi limayamba. Pazochitikazi, madokotala angatsatire tsatanetsatane yowonjezera: Ngati lymphoma nthawi imodzi inali ndi chotupa chachikulu chachikulu - chowonekera kwambiri - pamalo otchedwa extranodal, ndiye kuti ikhoza kuonedwa ngati extranodal lymphoma.

Kusiyana Kofunika Kwambiri

Pa ma lymphomas omwe amayamba m'ziwalo zam'mimba , kapena maselo am'mimba , pafupifupi onse angathe kutenga nawo mbali - ndiko kuti, akhoza kufalikira kumalo osokoneza bongo. Kachilombo kamene kakufalikira ku ziwalo zina za mitsempha sichimayesedwa kuti ndi chofunika kwambiri pachimake extranodal lymphoma. Pofuna kuti likhale loyamba extranodal, lymphoma iyenera kuti inayambira kunja kwa maselo am'mimba.

Mwachidule

Matenda akuluakulu otchedwa extronodal lymphomas amapezeka kwambiri ku NHL kusiyana ndi Hodgkin's lymphoma. Kufikira 33 peresenti ya NHL yonse imatengedwa kuti ndiyambe yopambana extranodal lymphoma, pamene ali mu HL, matenda oyamba extranodal amaganiza kuti ndi ovuta.

Malo otchuka kwambiri otchedwa extranodal lymphoma ali m'matumbo, ndipo pafupifupi onsewa ndi NHL.

Tsamba lotsatira kawirikawiri pambuyo papepala la GI ndi khungu . Komabe, pamene NHL imayamba khungu kokha, limatchedwa khungu lymphoma, kapena lymphoma ya cutaneous.

Extranodal lymphoma imatha kupezeka minofu ya lymphoid ya mphuno, fupa, fupa, teteils, ndi adenoids - timagulu tating'ono tomwe timabisala pamutu.

Maselo apachimwena kapena am'mimba a m'mimba m'mimba, m'mapapo, m'mapangidwe ozungulira, m'matumbo a chithokomiro, m'mitsempha yambiri, ndi m'mimba mwazing'ono angapangitsenso maimymphoma oyambirira. Mabala am'mimba m'maderawa akuphatikizapo 'malo a m'mphepete mwa nyanja B-cell lymphomas of mucosa-yogwirizana ndi minofu ya mymphoid,' kapena MZBCL ya MALT, mwachidule.

Mafupa akuluakulu a m'mphuno ndi mmphuno amaphatikizapo MZBCL ya MALT, yomwe imakhala yaikulu kwambiri ya B-cell lymphoma kapena DLBCL , komanso kupha thupi / T-cell lymphomas.

Maimymphomas oyambirira angakhudze ma testes mwa amuna ndipo amatchedwa primary testicular lymphomas. Lymphoma mu ubongo, kapena CNS lymphoma, ingakhalenso yopambana. Ngakhale kuti primary extranodal lymphoma ya ubongo ndi testes yakhala ikugwiridwa ndi matenda ovuta kwambiri, kafukufuku waposachedwapa awonetsa kuti chithandizo chomwe chikugwirizana ndi malowa chingapangitse kusintha kwakukulu.

Matenda akuluakulu otchedwa "extranodal follicular lymphomas" omwe sali ndi khungu lamagulu amadzimadzi amapezeka m'malo mopitirira nthawi zambiri.

Primary bone lymphoma ndizosazolowereka kwambiri pamene mphutsi imayamba m'fupa.

Primary cardiac lymphoma ndi imodzi mwa zipsinjo za mtima. Primary cardiac lymphoma amaganiza kuti ndi 1.3 peresenti ya matumbo onse a mtima ndipo ndi 0.5 peresenti ya maselo onse a extranodal. Izi zikachitika, mtundu wofala kwambiri wa chotupachi umapangitsa kuti maselo ambiri a B cell alowe, ndipo kawirikawiri, mavitriki abwino ndi oyenera.

Chimodzi mwa machitidwe a primary extranodal lymphomas, ambiri, ndi chakuti iwo adakula kwambiri ndi kutuluka kwa HIV ndi Edzi.

Primary Extranodal Lymphoma - Kugonjetsa

Mfundo yakuti lymphoma ndilopambana extranodal lymphoma ingakhale yofunikira pa dongosolo la chithandizo ndi kufotokozera, koma zinthu zina zingakhale zofunikira kapena zofunikira kwambiri.

Lymphoma subtype, B cell kapena T cell mtundu, ndi chiwalo chachikulu kapena minofu ya chiyambi akhoza zonse kukhala zofunika zizindikiro.

Kuphatikizidwa Kwachangu - Kuwonetsa

Pafupifupi onse amtundu wa lymphomas akhoza kufalikira kumalo osokoneza bongo, koma pazifukwazi, iwo saganiziridwa kuti ndi oyamba extranodal lymphomas.

Mu NHL, ndondomeko zothandizira kwambiri zothandizira zimadalira pazinthu zingapo, ndipo kugwirizana kwa extranodal kungakhale imodzi mwa iwo. Nthawi zina ma lymphoma omwe amapezeka m'magulu am'mimba amatha kuchiritsidwa ndipo amatha kulandira chithandizo chokwanira kusiyana ndi lymphoma yomwe yafalikira kunja kwa maselo am'mimba. Komabe, njira zosiyanasiyana zowonjezereka za NHL - pamodzi ndi zina zambiri zomwe zimakhudza mankhwala ndi zotsatira - zikutanthauza kuti ndondomeko ya chithandizo ndi majekesi akhoza kukhala apamwamba kwambiri.

Nthawi zina, kutenga nawo mbali kwapadera kumaonetsa kwambiri matenda opatsirana. Mwachitsanzo, mu matenda a Hodgkin , kutengeka kwina kwapakati - kupatula mu ntchentche ndi thymus - kumasonyeza chigawo cha IV Hodgkin matenda. Ngakhale kumapeto kwa nthawi ya Hodgkin matenda angakhale ochiritsidwa, komabe.

Zotsatira:

Mapulaneti ake a Nodal ndi Exymododal Non-Hodgkin's Lymphomas; Alfred C. Feller, Jacques Diebold; Springer Science & Business Media, Jun 27, 2011

Campo E, Chott A, Kinney M, et al. Sinthani pa maseŵera a extranodal. Zomwe Msonkhanowu unagwiridwa ndi EAHP ndi SH ku Thessaloniki, Greece. Matenda Ake . 2006; 48 (5): 481-504.

Troppan K, Wenzl K, Neumeister P, Deutsch A. Mapuloteni Achilengedwe a MALT Lymphoma. Kafukufuku Wosaka ndi Kuchita . 2015

Zucca E, Gregorini A, Cavalli F. Kulamulira kwa maselo ena osakhala a Hodgkin omwe amachokera kumalo otchedwa extranodal. Therapeutische Umschau. 2010; 67 (10): 517-25.

Krol AD, le Cessie S, Snijder S et al. Nthenda yotchedwa Extronodal Primary non-Hodgkin's lymphoma (NHL): zotsatira za kutanthauzira kwina zomwe zayesedwa mu zolembera za NHL za Comprehensive Cancer Center West. Annals of Oncology . 2003; 14 (1): 131-139.

Primary malignant lymphoma wa m'mawere: Kuphunzira kwa Clinicopathological ya milandu isanu ndi iwiri. Khansa ya m'magazi ndi Lymphoma . 2004 Feb; 45 (2): 327-30.

Matumbo apamimba am'mimba. World J Gastroenterol . 2004 Jan; 10 (1): 5-11. Onaninso.

Intra-Vascular Large B-Cell Lymphoma Yovumbulutsidwa ndi Matenda a Chifilosoti: Kuchokera kwa Chaka chimodzi Kuchokera kwa Frequency Frequency CHOP ndi Rituximab. Khansa ya m'magazi ndi Lymphoma . 2004; 45 (8): 1703-1705.

Jonavicius K, Salcius K, Meskauskas R, Valeviciene N, Tarutis V, Sirvydis V. Primary cardiac lymphoma: milandu iŵiri ndi kubwereza mabuku. J Cardiothorac Surg . 2015; 10: 138.