Zinthu 10 Zomwe Mukuyenera Kudziwa Zokhudza Matenda a Silima Odwala

Chilombo cha matenda odwala matendawa ndi mtundu wobadwa nawo wa magazi m'thupi kumene maselo ofiira amakhala aakulu kwambiri ndipo amawoneka, ofanana ndi mawonekedwe a nthochi. Zimakhudza anthu pafupifupi 100,000 ku United States ndi mamiliyoni ambiri padziko lonse lapansi. Ku US kumapezeka pafupifupi mmodzi mwa onse 365 a ku America ndi America ndipo amapezeka nthawi zambiri m'mabanja a ku Puerto Rico ndi America. Ngakhale matenda a sickle sali ovuta kwambiri, pali zina zochepa zomwe zimadziwika ndi zolakwika zomwe aliyense ayenera kudziwa.

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Ikhoza Kuchita Mliri uliwonse kapena Gulu Loyamba
Jens Magnusson / Ikon Images / Getty Images

Ngakhale matenda a sickle cell akhala akugwirizanitsidwa ndi anthu a ku Africa, amapezeka m'mitundu yambiri komanso mafuko ambiri, kuphatikizapo Spanish, Brazil, Indian, komanso Caucasus. Chifukwa cha ichi, ana onse obadwa ku United States amayesedwa kuti ali ndi vutoli.

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Matenda Olowa
Filo / Creative RF / Getty Images

Matenda a tizilombo toyambitsa matenda sali otheka ngati chimfine. Anthu amabadwa nawo kapena iwo sali. Ngati mwabadwa ndi matenda a sickle cell onse a makolo anu ali ndi kachilombo ka HIV (kapena kholo limodzi lokhala ndi kachilombo kakang'ono kake ndipo ena ali ndi khalidwe lina la hemoglobin). Anthu omwe ali ndi kachilombo ka khungu sangathe kukhala ndi matenda a sickle cell.

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Odziwika pa Kubadwa
Scientifica / Creative RM / Getty Zithunzi

Ku United States, mwana aliyense amayesedwa ku matenda a sickle cell. Ichi ndi gawo la kanema kakang'ono kamene kamapangidwa posachedwa atangobereka. Anthu ena akhoza kutchula izi ngati mayeso a PKU. Kuzindikira ana omwe ali ndi matenda a sickle cell kuyambira ali wakhanda akhoza kuteteza mavuto aakulu.

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Kulumikizana pakati pa Mchitidwe wa Sickle Cell ndi Malaria
Benjamin Van Der Spek / EyeEm / Creative RF / Getty Images

Anthu omwe ali ndi kachilombo kakang'ono angapezeke kwambiri m'madera omwe ali ndi malungo. Izi zili choncho chifukwa chingwe cha ngodya chikhoza kuteteza munthu kuti asatenge kachilombo ka malungo. Izi sizikutanthawuza kuti munthu yemwe ali ndi kachilombo ka HIV sangathe kutenga kachilombo ka malungo, koma ndi wamba kusiyana ndi munthu wopanda khalidwe lachilonda.

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Palibe Mitundu Yomwe Yapangidwa Mofanana
Vladimir Godnik / Creative RF / Getty Images

Pali mitundu yosiyana ya matenda a sickle cell amene amasiyana kwambiri. Hemoglobin SS (komanso mtundu wochuluka kwambiri) ndi ngodya za betala zowopsa kwambiri ndi zotsatira za hemoglobin SC ndi sickle beta kuphatikizapo thalassemia.

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Sikumangopweteka Kwambiri
JGI / Jamie Grill / Creative RF / Getty Images

Pali zambiri zowononga matenda osokoneza bongo kusiyana ndi zopweteka zopweteka. Sickle matenda matenda ndi matenda a maselo ofiira a magazi, omwe amapereka mpweya ku ziwalo zonse. Chifukwa nthendayi yamatenda imapezeka m'magazi, chiwalo chilichonse m'thupi chimakhudzidwa. Odwala omwe ali ndi SCD ali pachiopsezo cha matenda, matenda a maso, zilonda zam'mimba, matenda akuluakulu a bakiteriya, ndi kuchepa kwa magazi, kutchula ochepa.

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Ana Ali Pangozi Chifukwa cha Sitiroko
BSIP / UIG / Getty Images

Ngakhale kuti anthu onse okhala ndi matenda a ngodya ali pangozi yoti aphedwe, ana omwe ali ndi matenda a sickle omwe ali ndi chiopsezo chachikulu kuposa ana omwe alibe matenda a cellle. Chifukwa cha chiopsezo chimenechi, madokotala amene amapereka ana ndi matenda a ngodya amagwiritsa ntchito ubongo kuti ayang'ane ndikudziwa omwe ali ndi chiopsezo chachikulu choyambitsa matendawa ndi kuyamba mankhwala kuti athetse vutoli.

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Kusintha Kwambiri kwa Antibiotic Kusintha kwa Moyo
Jose Luis Pelaez Inc / Creative RF / Getty Images

Mankhwala a antibiotic penicillin ndi opulumutsa moyo. Anthu okhala ndi matenda a sickle cell ali pangozi yaikulu ya matenda akuluakulu a bakiteriya. Kuyamba penicillin kawiri patsiku kwa zaka zisanu zoyambirira za moyo zasintha mkhalidwe wa chikhalidwe ichi kuchokera ku china chowoneka mwa ana kuti chikhale chikhalidwe cha anthu kukhala akuluakulu.

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Mankhwala Akupezeka
GP Kidd / Blend Images / Getty Images

Pali mankhwala opweteka kwambiri ochizira matenda odwala khungu. Lero, kuikidwa magazi ndi mankhwala otchedwa hydroxyurea akusintha miyoyo ya anthu okhala ndi cell sickle. Mankhwalawa akuloleza anthu okhala ndi matenda a sickle cell kukhala ndi moyo wautali ndi zovuta zochepa. Kafukufuku wochuluka wochuluka akupitirira kuti mupeze njira zina zothandizira chithandizo.

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Pali mankhwala
Thomas Barwick / Creative RM / Getty Images

Msuzi wa mafupa (womwe umatchedwanso kuti stem cell) ndi mankhwala okhawo. Kupambana kopambana kunachokera kwa opereka omwe ali abale omwe maonekedwe awo amafanana ndi munthu yemwe ali ndi matenda a sickle cell. Nthawi zina mitundu ya zopereka, monga anthu osagwirizana kapena makolo, amagwiritsidwa ntchito koma makamaka m'maphunziro a kafukufuku wathandizira. M'zaka zikubwerazi, mankhwala opatsirana amaoneka ngati mankhwala othandiza.

Ngati inu kapena wachibale wanu muli ndi matenda a cellle, ndikofunika kuti muzitsatira nthawi zonse ndi dokotala kuti muonetsetse kuti mukusamalira.

> Chitsime:
National Heart, Lung, ndi Blood Institute. Utsogolere wotsogoleredwa kwa Matenda a Sickle Cell: Report of Panel Panel, 2014.