Ngati iwe kapena wokondedwa wamuuza kuti uli ndi matenda a Rasmussen kapena encephalitis ya Rasmussen, ukhoza kukhala ndi mpumulo podziwa kuti pamapeto pake muli ndi matenda omwe amasonyeza zizindikiro zanu. Koma mungakhalenso ndi nkhawa zambiri zomwe muyenera kuyembekezera ku chikhalidwe ichi.
Matenda a Rasmussen kapena encephalitis ya Rasmussen sizolowereka, ndipo akuti anthu angapo osapitirira 2000 amakhala ndi vutoli ku United States.
Ngakhale kuti n'zosatheka, pali chithandizo chachipatala cha Rasmussen's syndrome ndi Rasmussen's encephalitis, ngakhale kuti pali mwayi waukulu kuti mupitirize kukhala ndi zotsatira za nthawi yaitali ngakhale mutalandira chithandizo ndipo muyenera kusunga chithandizo kwa zaka zambiri.
Kodi Rasmussen's Syndrome ndi Rasmussen's Encephalitis Ndi Chiyani?
Matenda a Rasmussen ndi mawu omwe amagwiritsidwa ntchito pofotokozera chikhalidwe nthawi iliyonse panthawi ya matenda. Zimakhulupirira kuti matenda a Rasmussen nthawi zina amayamba chifukwa cha mtundu wa kutupa kwa ubongo wotchedwa encephalitis ya Rasmussen.
Encephalitis ya Rasmussen yokha ndiyo vuto limene ubongo uli ndi mphamvu yowonongeka kwambiri ya thupi yomwe imayambitsa kusokonezeka kwakukulu kwa ubongo kumbali imodzi. Izi zikhoza kuwonetsa ngati kukhumudwa , kufooka, mavuto a chinenero kapena kuperewera kwa malingaliro (kulingalira ndi kuthetsa mavuto).
Kawirikawiri, kutentha kotentha sikupitirirabe kwa nthawi yayitali, koma kutupa kutatha, nthawi zambiri anthu amapitirizabe kuona zizindikiro. Zizindikirozi zimatchedwa matenda a Rasmussen m'malo mojambulidwa ndi Rasmussen's encephalitis ngati palibe umboni wa kutupa kwabongo mu ubongo.
Matenda a Rasmussen ndi matenda omwe amatha kwa zaka zambiri, nthawi zina pambuyo pa kutupa kwa ubongo wa Rasmussen. Nthawi zina matenda a Rasmussen amatha kuchitika ngakhale kuti sakudziwika bwinobwino ngati pali kalembedwe ka Rasmussen patsogolo pake.
Matenda a Rasmussen, monga encephalitis ya Rasmussen, amadziwika ndi zovuta zomwe zimavuta kuzilamulira ndipo zimachokera ku mbali imodzi ya ubongo. Anthu ena omwe ali ndi matenda a Rasmussen amakhalanso ofooka pa mbali imodzi ya thupi, mavuto a chinenero, kapena vuto ndi luso la kuzindikira malingaliro.
Matendawa amakhudza kwambiri ana a zaka zapakati pa 2-12, koma akhoza kukhudza anthu a msinkhu uliwonse.
Kodi Ndiyenera Kuyembekezera Chiyani?
Kawirikawiri, kupweteka kwa matenda a Rasmussen a encephalitis ndi kovuta kulamulira ndi mankhwala, ndipo nthawi zambiri zimakhudza mbali imodzi ya thupi. Zokwanira zimagwirizanitsidwa ndi kugwedeza ndi kugwedeza mbali imodzi ya thupi, nthawi zambiri kutaya chidziwitso kapena kuchepa.
Ngati muli ndi encephalitis ya Rasmussen, simungakumbukire kugonjetsedwa mwatsatanetsatane, ndipo mwina mumatopa pambuyo pake. Zofooka, mavuto a chinenero, ndi mavuto a chidziwitso nthawi zambiri zimayamba kuchitika patangotha miyezi ingapo kugwa kwayamba, koma zizindikirozi zingachitike msanga kapena ayi.
Kuzindikira za Encephalitis ya Rasmussen
Zingatenge nthawi yaitali kuti mupatsidwe chitsimikizo chotsimikizika cha encephalitis ya Rasmussen. Izi ndi chifukwa palibe mayeso omwe angathe kutsimikizira izi.
Matenda a Rasmussen ndi Rasmussen's syndrome amapezeka malinga ndi zomwe dokotala akukuuzani za zizindikiro zanu zam'chipatala kwa miyezi (kapena ngakhale zaka) pamodzi ndi kuyesa kwa EEG ndi kuyesa kwa MRI ubongo.
EEG imayembekezeredwa kuti iwonetse ntchito yogwira ntchito kumbali imodzi ya ubongo. Koma chitsanzo ichi cha EEG sichinali chokha kwa matenda a Rasmussen, ndipo chotero EEG siyeso yeniyeni, koma imagwiritsidwa ntchito mogwirizana ndi zizindikiro zanu, mayesero ena, ndi zomwe adokotala akuwona pa chikhalidwe chanu.
MRI ya ubongo imayembekezeredwa kusonyeza kusiyana kwakukulu pakati pa mbali ziwiri za ubongo. Kumayambiriro kwa matendawa, mbali imodzi ya ubongo ingasonyeze mtundu wa kutupa womwe umawonekera ngati matenda. Pambuyo pa matendawa, ubongo wa MRI ungasonyeze atrophy kumbali yomwe yakhudzidwa, yomwe kwenikweni ikugwera ubongo chifukwa cha kuwonongeka kwa nthawi yaitali kuchokera ku kutupa. Kuwonekera kwa ubongo wa MRI sikuli kokha kwa abambo a Rasmussen kapena matenda a Rasmussen, ndipo amalingaliridwa pamodzi ndi mkhalidwe wonse kuti atsimikize kuti muli ndi ramussen's syndrome kapena encephalitis ya Rasmussen.
Chithandizo ndi Utsogoleri
Ngati muli ndi encephalitis ya Rasmussen, mwinamwake mumalandira mankhwala osokoneza bongo kuti muthe kuchepetsa kupweteka kwanu. Nthawi zina, steroids amagwiritsidwa ntchito kuchepetsa kutupa mu ubongo. Ngati gulu lanu lachipatala liri ndi chifukwa chokhulupirira kuti muli ndi matenda mu ubongo wanu (matenda opatsirana opatsirana pogonana ) , ndiye kuti mungalandire mankhwala omwe akuwomberetsanso matendawa.
Ngati mutha kugwidwa kapena kufooka kapena vuto lina lililonse lapakhungu, koma palibe umboni wa kutupa, ndiye kuti chithandizo chanu makamaka chidzagwiritsidwe ntchito pochiza matenda anu ndi vuto lanu la ubongo.
Nthawi zina, khunyu ya matenda a Rasmussen ndi ovuta kwambiri kotero kuti mungafunikire kuchitidwa opaleshoni ya khunyu. Kuchita opaleshoniyi kungaphatikizepo kuchotseratu dera lanu lokhudzidwa ngati ubongo wanu uli m'dera linalake la ubongo ukupezeka kuti ukuwonongera zambiri. Kawirikawiri, opaleshoniyi imakhala ndi zotsatira monga kufooka kwapadera kapena kwathunthu kwa mbali imodzi ya thupi. Njira yothandizira opaleshoni ya Rasmussen's syndrome imasankhidwa mosamala kwambiri, ndipo ndi njira yokhayo ngati mukuyenera kusintha moyo wanu wonse.
Kodi Chimachititsa Rasmussen's Encephalitis ndi Rasmussen's Syndrome?
Encephalitis ndi kutupa kwa ubongo. Palibe chodziwika bwino chomwe chimayambitsa chenicheni cha Rasmussen's encephalitis. Pakali pano, dera lachipatala lasankha zowona ziwiri zazikulu:
- Zitha kukhala chifukwa cha matenda omwe amachititsa kuti chitetezo cha mthupi chitetezeke.
- Zingayambidwe ndi zomwe zimangochitika pokhapokha (thupi lidziponya lokha).
Mwamwayi, chifukwa chomwe cha Rasmussen's encephalitis sichidziwika, palibe chitetezo chodziwika cha matenda osadziwika awa.
Mawu Ochokera
Ngati inu kapena wokondedwa wanu muli ndi matenda osadziwika monga a Rasmussen's encephalitis kapena a Rasmussen's syndrome, akhoza kuthandiza kukumana ndi anthu ena omwe ali ndi matenda omwewo. Mungathe kupeza uphungu ndikuphunzira kudzera muzochitika zomwe mumagawana nawo ngati mutalowa nawo gulu lothandizira ndikuyankhula ndi ena omwe angapereke malangizo ndi malangizo pamene mukuyenda moyo ndi matenda a Rasmussen.
> Zotsatira:
> Nabbout R, Andrade DM, Bahi-Buisson N, et al, Chotsatira cha ubwana-nthenda ya khunyu kuyambira msinkhu kufikira munthu wamkulu: Kusintha kwa matenda, Matenda a Epilepsy Behav. 2017 Feb 27. pii: S1525-5050 (16) 30629-1. lembani: 10.1016 / j.yebeh.2016.11.010.