Myopathy ndi mawu ogwiritsidwa ntchito polongosola matenda a minofu. Ngati mwapezeka ndi myopathy, kapena ngati mukuyesedwa kuti mukhale ndi vutoli, muli ndi mwayi waukulu kuti simunamvepo za myopathy kufikira tsopano, chifukwa sizodziwika ngati matenda ena. Mukhoza kukhala ndi mafunso okhudza njira yothandizira, zomwe muyenera kuyembekezera pogwiritsa ntchito malingaliro ndi chithandizo, komanso ngati ena a m'banja mwanunso akhoza kukhala pachiopsezo cha myopathy.
Kodi Myopathy N'chiyani?
Myopathy amatanthauza matenda a minofu. Pamene munthu ali ndi matenda a minofu, minofu imagwira ntchito mochepa kuposa momwe iyenera kukhalira. Izi zikhoza kuchitika pamene minofu ikukula bwino, ikawonongeka, kapena ikasowa zinthu zofunika.
Mitundu kawirikawiri imagwira ntchito pochita mgwirizano, kutanthauza kukhala wochepa. Minofu yachibadwa imapangidwa ndi mapulotini ndi zigawo zina zomangira zomwe zimayenda motsatizana kuti zithetse minofu. Pamene zina mwazigawozi ndizosavomerezeka, izi zingayambitse myopathy.
Pali zifukwa zosiyanasiyana zosiyana siyana za matenda a minofu, ndipo chifukwa chake, pali myopathies osiyanasiyana. Myopathies aliwonse ali ndi dzina lake lenileni, chifukwa, mayesero ozindikiritsa, kuyerekezera, ndi chithandizo. Myopathies ena amayembekezereka kuwonjezereka pakapita nthawi, pamene ena amakhala osasuntha. Myopathies angapo ali olowa, ndipo ambiri sali.
Zizindikiro
Kawirikawiri, myopathy imayambitsa minofu yofooka. Chizoloŵezi chofala kwambiri cha kufooka chimatchulidwa ngati chofooka chachikulu. Izi zikutanthauza kuti minofu ya manja apamwamba ndi miyendo yapamwamba imakhala yofooka kwambiri kuposa minofu ya manja kapena mapazi. Nthawi zina, myopathy imafooketsa minofu ya kupuma (minofu yomwe imalamulira kupuma).
Makhalidwe ena a myopathy ndi otopa, kusowa mphamvu, ndi kufooka kochulukirapo pamene tsiku likupitirira kapena kufookera kofulumira ndi kuyesayesa.
Kawirikawiri, pamene anthu akhala ndi vutoli kwa zaka zambiri, minofu imayamba kukulirakulira, yomwe imapangitsa kuti minofu iwonongeke, kufooketsa mphamvu ya minofu. Myopathy kawirikawiri amagwirizanitsidwa ndi mawonekedwe osalimba a mafupa, kawirikawiri chifukwa kufooka kwa minofu kumathandiza kuti mafupa asapangidwe bwino.
Kodi Ndingadziwe Bwanji Ngati Ndili ndi Masepathy?
Kawirikawiri, myopathy ndi matenda ovuta kupeza. Ngati muli ndi zizindikiro za myopathy, muli ndi mwayi waukulu kuti mutumizidwe kwa katswiri wa sayansi ya ubongo kapena a rheumatologist, kapena onse awiri, malingana ndi zizindikiro zanu zomwe ziri zotchuka kwambiri.
Kuyezetsa matenda kumaphatikizapo kufufuza mwakuthupi, kuphatikizapo kufufuza khungu lanu, malingaliro anu, mphamvu yanu ya minofu, kuchepetsa kwanu ndi kumverera kwanu. Dokotala wanu atenga mbiri yakale ya zamankhwala ndikukufunsani za mbiri yachipatala ya banja lanu.
Palinso mayesero angapo omwe mungafunike, malingana ndi mbiri yanu ya zachipatala komanso zomwe mwapeza pofufuza. Mayeserowa akuphatikizapo kuyesa magazi, monga kuchuluka kwa magazi (CBC) ndi magulu a electrolyte.
Kuyeza magazi kumaphatikizapo mlingo wa erythrocyte sedimentation (ESR) ndi mayeso a antitinuclear antibody (ANA), omwe amayeza kutupa. Creatine kinase m'magazi akhoza kuyesa kusokonezeka kwa minofu. Mayeso a chithokomiro, mayesero a zamagetsi ndi a endocrine angafunike.
Mayeso ena otchedwa electromyography (EMG) ndi mayesero a magetsi omwe amayesa minofu kugwira ntchito pogwiritsa ntchito singano zomwe zimazindikira makhalidwe angapo a minofu yanu ndi kayendetsedwe kake. Nthawi zina, mayesero apadera kwambiri monga minofu yowonongeka ndi ma genetic angathandize kupeza mitundu ina ya myopathy.
Mitundu
Mthepathiro yowonongeka imatanthawuza kukhumudwa kumene munthu amabadwa nawo.
Zambiri mwazimenezi zimakhulupirira kuti ndizobadwa kapena zidutsa kudzera m'mabanja. Ndipo, pamene zizindikiro za congenital myopathies zimayamba nthawi yaying'ono, siziri choncho nthawi zonse. Nthawi zina matenda ochiritsira odwala samayamba kuonetsa zizindikiro mpaka munthu ali wachinyamata kapena wamkulu.
Myopathies omwe amabadwa nawo ndi awa :
- Myopathy wa Mitochondrial : Ichi ndi matenda omwe amachititsa chirema mu gawo lopanga mphamvu ya selo, lotchedwa mitochondria . Pali mitundu yambiri ya myopondrial myopathy, ndipo pamene ingayambitsidwe ndi kusintha kwa chibadwidwe (zosafunikira mu majini) zikhoza kuchitika popanda mbiri ya banja nkomwe.
- Msopathy : Ichi ndi gulu la matenda omwe amachititsidwa ndi mavuto amadzimadzimadzi omwe amalepheretsa ntchito ya minofu. Pali nthenda zosiyanasiyana zosiyana siyana zomwe zimayambitsa matenda a myopathi omwe amachokera ku majini omwe amachititsa kuti mavitamini omwe ali ofunikira azisuntha.
- Mphulupulu ya Nemaline : Ichi ndi gulu la mavuto omwe amapezeka ndi kukhalapo kwa nyumba zotchedwa 'namaline ndodo' mu minofu. Mthepine yamaline nthawi zambiri imakhudzana ndi kupuma kwa minofu.
Myopathies a Congenital ndi awa:
- Myopathy wapakatikati : Ichi ndicho chosowa choyambitsa matenda omwe amachititsa kufooka, mavuto a mafupa, ndi kusintha kwa mankhwala ena. Kuopsa kwa matendawa kumasiyana, kufooka kwakukulu pakati pa anthu ena ndi kufooka kochepa kwa ena.
- Matenda a mitsempha : Iyi ndi gulu la matenda omwe amayamba chifukwa cha kuchepa kwa minofu kapena maselo osokonezeka. Mwachidziwitso, minofu ya dystrophy si myopathy, koma nthawi zambiri imapezeka mu zizindikiro, choncho potero mungayambe kafukufuku wa zachipatala pofuna kudziwa ngati muli ndi myopathy kapena mitsempha yotupa. Kusiyanitsa kwakukulu pakati pa myopathy ndi kupweteka kwa thupi kumakhala kuti minofu siigwira bwino bwino mu myopathy, pamene minofu imayamba kufooketsa mthupi.
Myopathy ikhozanso kuyambitsidwa ndi matenda osiyanasiyana omwe amabweretsa mavuto osiyanasiyana kuphatikizapo zinthu ndi minofu yopunduka.
Myopathies omwe amapezeka kawirikawiri ndi awa:
- Kuwotcha / kudzipangitsa munthu kukhala ndi vutoli : Izi zimachitika pamene thupi limadzipweteka, limapangitsa kuti minofu imachepa kapena kusokoneza minofu. Pali gulu la myopathies lomwe limadziwika ndi kutupa kapena pafupi ndi minofu. Zina mwa zinthuzi zikuphatikizapo polymyitisitis , dermatomyositis, sarcoidosis, lupus, ndi rhumumidematenda ya nyamakazi.
- Myopathy yoopsa : Izi zimachitika pamene poizoni, mankhwala, kapena mankhwala amachititsa kuti thupi limangidwe kapena kugwira ntchito.
- Mphuphu ya Endocrine : Izi zimachitika pamene matenda a mahomoni amachititsa kuti minofu izigwira ntchito. Zomwe zimayambitsa mavuto ndi ubongo kapena adrenal.
- Mankhwala opatsirana : Izi zingachitike pamene matendawa amachititsa kuti minofu isagwire bwino ntchito.
- Myopathy yachiwiri ndi kusalinganizana kwa electrolyte : Matenda a electrolyte, monga apamwamba kwambiri kapena otsika potaziyamu, akhoza kusokoneza ntchito ya minofu.
Kodi Ndiyenera Kuyembekezera Chiyani Ngati Ndili ndi Myopathy Kapena Myopathy?
Kawirikawiri, congenital myopathy ikuyembekezereka kuwonjezereka kapena kukhazikika pamapeto pa nthawi ndipo sichiyenera kuyembekezera. Myopathies omwe sali obadwa, monga matenda opatsirana, amadzimadzi, kapena myopathies, amatha kusintha makamaka chifukwa cha myopathy bwino.
Kumvetsetsa bwino vuto lanu ndikofunika kuti mukhale ndi zotsatira zabwino kwambiri. Ngati muli ndi mtundu wa myopathy umene suyenera kuwongolera, muyenera kumvetsera kwambiri zinthu monga atrophy, zilonda zapanikizika, ndi kuonetsetsa kuti mukugwira nawo ntchito yeniyeni kuti muthe kuchita bwino.
Chithandizo
Palibe mankhwala othandiza omwe angayambitsenso kapena kuchiritsa minofu yanu kuti athe kuchiritsa. Ngati pali chifukwa chodziwikiratu, monga vuto la endocrine, kukonza chifukwa chingathandize kusintha zizindikiro za myopathy, kapena mwina zingathandize kuti izi zisapitirire.
Kawirikawiri, kuthandizira kupuma ndi chinthu chofunika kwambiri pa myopathy, kuti kupuma kwanu kusamalike bwino.
Kodi Banja Langa Lidzakhala ndi Myopathy Ngati Ndili Ndi Chizoloŵezi Chochita Maso?
Inde, ma myopathies ena alidi olowa. Ngati muli ndi myopathy cholowa, ndiye kuti muli ndi mwayi kuti ena mwa abale anu, ana anu, zidzukulu, ndi ana amasiye, kapena achibale ena akhozanso kukhala ndi myopathy. Ndikofunika kuti banja lanu lidziwe za matenda anu, monga momwe matenda oyambirira amathandizira kuti athe kupeza chithandizo cham'mbuyomu ndi chithandizo chowathandiza.
Myopathies ena omwe satchulidwa mwachindunji kuti ndi obadwa kapena obadwa nawo angakhalebe ndi chizoloŵezi choyenda m'mabanja, kotero banja lanu likhoza kukhala loopsa kwambiri ngakhale mutakhala ndi myopathy omwe sudziwika kuti ndiwo choloŵa chawo.
Mawu Ochokera
Myopathy sizofala kwambiri. Matenda a mitsempha akhoza kuwononga moyo wanu. Komabe, anthu ambiri amene amapezeka ndi myopathy amatha kusunga miyoyo yopindulitsa, kuphatikizapo kukhala ndi ntchito yokhutiritsa komanso kukhala ndi banja losangalala komanso labwino.
> Zotsatira:
> Lundberg IE, Miller FW, Tjärnlund A, Bottai M, J, Kuzindikira ndi kusinthana kwa mdipathie yotupa kwambiri, Intern Med. 2016 Jul; 280 (1): 39-51