Scleroderma ndi matenda okhaokha omwe amadziwika bwino . Si matenda amodzi okha, koma chizindikiro cha gulu la matenda ovuta chifukwa cha kukula kosaoneka bwino kwa minofu yomwe imathandiza khungu ndi ziwalo.
Zimayambitsa
Chifukwa chomwe thupi limagonjetsera maselo awo m'thupi lodziwika bwinoli silikudziwika. Ochita kafukufuku samakhulupirira kuti scleroderma imachotsedwa, kaya, koma anthu ochokera m'mabanja omwe ali ndi mbiri yake kapena matenda ena a chifuwa amatha kukhala ovuta kwambiri.
Nthawi zina, scleroderma yathandizidwa kukhala ndi mankhwala ena kapena zowononga-mwa kuyankhula kwina, zochitika zachilengedwe.
Kukula
Scleroderma imakhudza anthu 75,000 mpaka 100,000 ku United States. Malingana ndi American College of Rheumatology, milioni 12 mpaka 20 yatsopano ya scleroderma miliyoni miliyoni imapezeka ku United States chaka chilichonse. Pafupifupi theka la anthuwa ali ndi systemic sclerosis, yomwe imakhudza thupi lonse.
Ndani Amachipeza?
Akazi pakati pa 30 ndi 50 ali ndi zaka 75 peresenti ya milandu ya scleroderma, koma amuna ndi ana a m'badwo uliwonse akhoza kukhalanso. Chikhalidwechi chimakhala pakati pa zaka 25 mpaka 55.
Mitundu ya Scleroderma
Pali mitundu ikuluikulu ya scleroderma : yomwe ili m'derali komanso yowonjezera (yomwe imatchedwanso systemic sclerosis). Malo amtunduwu ndi ochepa kwa khungu lakuya ndi kulimbikitsa, pamene mitundu yowonjezera imakhudza mitsempha ya mthupi ndi ziwalo za mkati.
- Localized Scleroderma: Malo apamtima scleroderma amakhudza kwambiri khungu ndipo amaphatikizidwanso kukhala morphea (zovuta, zikopa zamkati pa khungu) ndi zowonongeka (mzere wosiyana kwambiri wa khungu lofiira nthawi zambiri umakhudza zida, miyendo, kapena pamphumi).
- Matendawa: Kugwiritsidwa ntchito kowonongeka kumagawidwa m'lingaliro laling'ono la scleroderma (kutangoyamba pang'ono, kokha kumadera ena a thupi, kungakhudze ziwalo za mkati pambuyo pake) ndipo kufalikira kwa scleroderma (kutulukira mwadzidzidzi, kufalikira kumakwirira malo akuluakulu ndipo kungakhudze ziwalo za mkati). Sine scleroderma, yomwe ena amaganiza kuti ndi gawo lachitatu la systemic sclerosis, sakhudza khungu.
Zizindikiro Zodziwika: CREST
Anthu omwe ali ndi systemic sclerosis angakhale ndi zizindikiro zomwe zimayendera ndondomeko ya khalidwe, yotchedwa CREST:
- Calcinosis (calcium imayika m'magulu ofanana)
- Zochitika za Raynaud (mitsempha yaing'ono yamagazi kwa zala, zala zazing'ono, mphuno, ndi makutu kumayendedwe ozizira kapena nkhawa)
- Kusokonezeka kwa matenda osokoneza bongo (minofu m'magazi otsika sagwira ntchito bwino)
- Sclerodactyly (khungu lolimba, lolimba, lowala bwino pa zala kapena zala zala)
- Telangiectasias (malo ochepa, mawanga ofiira pa manja ndi nkhope)
Kudziwa
Palibe chiyeso chimodzi chokha chomwe chimakhala ngati chitsimikizo chotsimikizika cha scleroderma. Kuphatikizidwa kwazowunika kuchokera kuthupi, kuyesa magazi, ndi mayesero omwe angathe kuyesa mavuto ndi ziwalo za thupi kuthandizira kudziwa scleroderma . Anthu ambiri omwe ali ndi scleroderma ali ndi mayeso abwino a anti-nuclear antibodies. Mankhwala oyenerera amafunika kupeza chithandizo chabwino.
Njira Zothandizira
Palibe mankhwala a scleroderma. Palibe mankhwala omwe angakhoze kuletsa kuphulika khungu kogwirizana ndi vutoli, koma mankhwala amalamulidwa kuti athetse zizindikiro, zomwe zingaphatikizepo:
- Zochitika za Raynaud
- kupweteketsa mtima
- kuthamanga kwa magazi
- matenda opatsirana m'mapapo
- pulmonary hypertension
- nyamakazi
- minofu yofooka
- mavuto a m'mimba
- mavuto a impso
Mawu Ochokera
Ngati mukudandaula kapena mwapezeka kuti muli ndi scleroderma kapena systemic sclerosis, kupeza matenda oyenera komanso kuphunzira zambiri za matenda anu kungakuthandizeni kuti muziwongolera bwino.
Palibenso chithandizo cha matendawa, koma pali njira zothandiza kuti moyo ukhale wabwino.
Zotsatira:
Scleroderma, Arthritis Foundation
Scleroderma (Systemic Sclerosis), American College of Rheumatology