Matenda Opita Patsogolo
Matenda oyambirira a lateral sclerosis (PLS) ndi matenda osokoneza bongo . PLS imakhudza maselo a mitsempha m'thupi omwe amayendetsa kuyenda mwadzidzidzi kwa minofu, yotchedwa motor neurons. Pakapita nthawi, ma neuroni amatha kutaya mphamvu zawo, zomwe zimayambitsa zofooka zopanda kupweteka komanso zofooka za minofu.
Sidziwika chifukwa chake PLS imapezeka, kapena momwe maselo amanjenje amawonongera.
Matenda oyambirira otchedwa sclerosis akuoneka kuti akuyamba zaka 40 mpaka 50. Sikudziwika kuti ndi anthu angati padziko lapansi amene amakhudzidwa ndi PLS, koma ndizosavuta.
Zizindikiro
Kutaya kwa maselo a mitsempha kumayambitsa minofu kuti ikhale yolimba komanso yovuta kusuntha. Kawirikawiri, mavuto a minofu amayamba miyendo ndikusunthira thupi ku thunthu, mikono, ndi minofu pamaso ndi pamutu. Kupititsa patsogolo kwa PLS kumasiyanasiyana kuchokera kumlandu kupita ku zochitika-Ena angapite mofulumira mkati mwa zaka zingapo kapena pang'onopang'ono kwa zaka makumi angapo.
Zizindikiro Zoyamba. Nthawi zambiri, chizindikiro choyamba cha PLS ndi kufooka kwa minofu ndi kuuma kwa miyendo ya m'munsi. Zizindikiro zina zoyambirira zimaphatikizapo:
- Mwendo umodzi umakhudzidwa kwambiri kuposa wina, ndi kupititsa patsogolo kwa mwendo wina
- Kusinthasintha, kupuma kolimba kwa miyendo chifukwa cha kupweteka kwa minofu yosafunika (spasticity)
- Zovuta kuyenda ndi kusunga bwino, monga kudumpha kapena kupunthwa
- Kugwedeza minofu yokhudzidwa
- Kusokoneza
Zizindikiro Zowonjezereka. Anthu okhudzidwa akhoza kukhala ndi zovuta kwambiri kuyenda. Kugwiritsiridwa ntchito kwa ndodo kapena chipangizo chomwecho chothandizira kuyenda kungakhale kofunikira. Nthawi zina, zizindikiro zina zingayambitse chitukuko cha minofu. Zizindikiro zina zingakhalepo:
- Kusambira kwa minofu m'manja kapena pansi pa ubongo.
- Mafupa opsinjika m'mimba, kumbuyo, kapena khosi
- Vuto loyendetsa mikono ndi kuchita ntchito monga kuphatikiza tsitsi kapena kutsuka mano
- Zovuta kupanga mawonekedwe (dysarthria) kapena kulankhula
- Kuvuta kumeza (dysphagia)
- Kutaya kwa chikhodzodzo kumapeto kumapeto kwa msana wambiri
Zizindikiro zimakula pang'onopang'ono.
Kudziwa
Palibe chiyeso chapadera choyambirira cha matenda oyambitsidwa m'mimba, choncho nthawi zambiri matendawa amapezeka chifukwa chothetsa zifukwa zina zomwe zimayambitsa zizindikiro. Chifukwa amyotrophic lateral sclerosis (ALS, kapena matenda a Lou Gehrig) amadziƔika kwambiri, ndipo chifukwa chakuti matenda awiriwa amasonyeza zizindikiro zofanana, PLS nthawi zambiri imasokonezeka ndi ALS.
Chithandizo
Palibe mankhwala pakalipano kwa PLS, kotero mankhwala amawongolera kuthetsa zizindikiro za matendawa. Chithandizo cha PLS chili ndi:
- Mankhwala monga Baclofen ndi Tizanidine kuti athe kuchepetsa mitsempha ya minofu
- Mankhwala osokoneza bongo athane ndi kutaya kwa chikhodzodzo
- Thandizo lachilengedwe ndi la ntchito kuti lichepetse mpweya, kupititsa patsogolo kayendetsedwe kake, ndi kupereka zipangizo zothandizira kuyenda ndi kudya
- Thandizo la kulankhula lothandiza poyankhula
- Orthotics ndi nsapato zimaphatikizapo kuthetsa mavuto a gait ndi mapazi
Thandizo
Matenda oyambirira a lateral sclerosis amachititsa kulemala kwapang'onopang'ono komanso kutaya ntchito koma sichikhudza maganizo kapena kuchepetsa moyo wa odwala mwachindunji. Pa chifukwa chimenechi, magulu othandizira monga Spastic Paraplegia Foundation kwa odwala ndi mabanja awo ndi ofunika kuwongolera kulemetsa zakuthupi ndi zamaganizo za matendawa.
> Zotsatira:
National Institute of Neurological Disorders ndi Stroke. NINDS Primary Primary Sclerosis Information Page.
Spastic Paraplegia Foundation. About PLS.
Spastic Paraplegia Foundation. Mankhwala ndi Mankhwala.
National Organization for Rare Diseases. Pambuyo Pambuyo Pambuyo.