Angioimmunoblastic T-cell lymphoma (AITL) ndi mtundu wamba wosakhala wa Hodgkin lymphoma (NHL ) . Zimachokera ku T-maselo , omwe ndi mtundu wa selo loyera la magazi omwe ali ndi udindo woteteza thupi ku matenda. Zikhoza kutchulidwa ATCL ndipo kale ankatchedwa angioimmunoblastic lymphadenopathy.
Kodi Angioimmunoblastic Imatanthauza Chiyani?
Mawu akuti 'angio' amatanthauza mitsempha ya magazi.
Lymphomayi ili ndi zinthu zina zachilendo kuphatikizapo kuwonjezeka kwa mitsempha yaing'ono yopanda magazi m'magawo omwe akukhudzidwa. 'Immunoblast' ndi mawu ogwiritsidwa ntchito ku maselo a immune (kapena maselo a mitsempha). Ndiwo maselo omwe amakula mochulukira ku ma lymphocyte, koma nambala yambiri imakhala m'magazi, okonzeka kufalikira pamene ma lymphocytes ambiri akufunika. Ngati mmalo mwake iwo amakula mu mawonekedwe awo aang'ono ndipo samakula, ali ndi khansa. Matenda a T-T cells m'thupi la AITL ndi immunoblasts.
Ndani Amakhudza?
Angioimmunoblastic T-cell lymphoma imangopanga 1% mwa onse omwe si a Hodgkin lymphoma. Zimakhudza anthu achikulire, omwe ali ndi zaka zakubadwa omwe amazindikira kuti ali ndi zaka 60. Ndikofala kwambiri mwa amuna kuposa akazi.
Zizindikiro
Mu AITL, pali zizindikiro za lymphoma zomwe zimaphatikizapo kutambasula kwa mitsempha yam'mimba (nthawi zambiri imamva pamtsetse, pamimba, ndi kubuula), komanso malungo, kutaya thupi, kapena kutuluka usiku.
Komanso, angioimmunoblastic T-cell lymphoma ili ndi zizindikiro zambiri zachilendo. Izi zimaphatikizapo ziphuphu zamphuno, kupweteka pamodzi, ndi zolakwika zina zamagazi. Zizindikirozi zimagwirizana ndi zomwe zimatchedwa chitetezo cha mthupi m'thupi, chokhazikitsidwa ndi mapuloteni ena osadziwika omwe amapangidwa ndi khansa. Kawirikawiri matendawa amapezeka chifukwa matendawa amaletsa chitetezo cha mthupi.
Lymphoma imeneyi imakhalanso yovuta kwambiri kuposa mafupa ena ambiri omwe si a Hodgkin. Kuphatikizika kwa chiwindi, nthenda, ndi fupa lapafu ndilofala. B-zizindikiro zimawoneranso mobwerezabwereza. Zinthu izi, mwatsoka, zikhoza kusonyeza zotsatira zosauka pambuyo pa chithandizo.
Kuzindikira ndi Mayesero
Monga ma lymphomas ena, matendawa a AITL amachokera ku lymph node biopsy . Pambuyo pa matendawa, mayesero angapo amayenera kuchitidwa kuti adziwe kutalika kwa lymphoma. Izi zikuphatikizapo CT scans kapena PET scan , test bone ya mnofu komanso kuyesa magazi.
Ngati pali khungu la khungu, kachilombo kamatulukanso khungu kuti adziwe zinthu zina zomwe zimathandiza kuzindikira matendawa.
Chithandizo
Njira yoyamba yothandizira matendawa amachititsa kuti zizindikiro zowononga thupi zimathamangitse, kuthamanga, kuphwanya magazi, komanso kuwonongeka kwa magazi. Steroids ndi othandizira ena ambiri apezeka kuti ndi othandiza kuchepetsa zizindikirozi.
Kamodzi kafukufukuyo atatsimikiziridwa ndipo kufufuza kwa stage kumamaliza, chemotherapy yayamba. CHOP ndiyo mankhwala omwe amagwiritsidwa ntchito kwambiri. Komabe, matendawa amabwereranso ndipo amatha miyezi ingapo yoyamba matenda. Mankhwala owonjezera a lymphomayi ndi ovuta.
Pali njira zingapo zomwe zayesedwa, kuphatikizapo fupa la fupa kapena masentimita ochepa. Zotsatira za matenda zimakhala zoipitsitsa kuposa mitundu yowonjezereka ya lymphoma yapamwamba kwambiri.
Zotsatira:
Khansa: Mfundo ndi Zolemba za Oncology 7th Edition. Okonza: VT DeVita, S Hellman ndi SA Rosenberg. Lofalitsidwa ndi Lippincott Williams ndi Wilkins, mu 2005.
Thandizo la Pulogalamu T / NK Neoplasms. Wolemba JP Greer. Lofalitsidwa m'nyuzipepala ya Hematology mu 2006.
Mankhwala Osapanga Matenda Omwe Ambiri Osati a Hodgkin-Othandizira Zaumoyo (PDQ®) National Cancer Institute. Idasinthidwa pa January 15, 2016.