Tanthauzo, Maonekedwe a Mantle Cell Lymphoma
Kodi mantle cell lymphoma ndi chiyani, ndipo ndiyenera kudziwa chiyani za khansa yamtundu uwu?
Mwachidule
Mantle Cell Lymphoma ndi mtundu wamba wosakhala wa Hodgkin's lymphoma (NHL) . Ndi a 5-7% okha a NHL omwe ali a gulu ili. Ndi lymphoma ya ma lymphocyte B, kapena "B-maselo." Ngakhale zikuwoneka ngati chotupa chocheperachepera, chochepera pansi pa microscope, nthawi zambiri imakula mofulumira ndipo imakhala ngati lymphoma yapamwamba kwambiri.
Amatchedwa 'mantle' cell lymphoma chifukwa choyamba chimayamba mkati mwa gawo la mliri wotchedwa 'mantle'.
Zowopsa
Mantle Cell Lymphoma imafala kwambiri kwa amuna kusiyana ndi akazi komanso akuluakulu. Zaka zakubadwa zomwe zimapezeka ndi zaka zoposa 60. Palibe zifukwa zomveka zopezera mtundu uwu wa lymphoma, ngakhale zifukwa zambiri zomwe zimachokera ku matenda opatsirana ndi mankhwala zimayang'aniranso momwe zingatheke kuti zikhale zovuta za Hodgkin's lymphoma .
Zizindikiro
Mantle cell lymphoma imayamba m'ziwalo zam'mimba. Chinthu choyamba chimene anthu ambiri amachiwona ndi node zofutukuka m'khosi, kubuula kapena zam'mimba. Matendawa amakula mofulumira ndipo nthawi yomwe akuwoneka ndi dokotala, matendawa afalikira kwa ziwalo zina m'thupi. Kwa anthu ena matendawa akukula mofulumira, chinachake cha oncologists chimatcha "indolent" koma izi ndi zosiyana. Mafupa, nthata, ndi mphuno zimakhudzidwa ndi anthu ambiri, ndipo kawirikawiri amakhala maselo a lymphoma m'magazi.
Matumbo angakhudzidwe ndi anthu ena, ndipo amachititsa zizindikiro ngati ululu m'mimba kapena kutsekula m'mimba.
Kudziwa
Mayesero a Mantle cell lymphoma ali ofanana ndi awo a mitundu ina ya lymphoma. Zimaphatikizapo mayesero a magazi, zokopa ndi mayeso a mafupa . Pamene mayeserowa amasonyeza kuti mbali zina za thupi zimakhudzidwa bwanji, matendawa amatha kudziwika .
Anthu ambiri ali ndi nthenda yachitatu kapena IV yomwe yafalitsidwa ku ziwalo zosiyanasiyana za thupi.
Kuchiza
Mantle cell lymphoma amachiritsidwa makamaka ndi mankhwala a chemotherapy, koma momwe amachitira nkhanza zimadalira kwambiri pa msinkhu. Kwa achinyamata, achikulire omwe ali ndi thanzi labwino, mankhwala a chemotherapy omwe amatsatiridwa ndi tsinde lopanda maselo akhoza kukhala njira yabwino, koma amaphatikizapo poizoni. Mankhwala ndi achilendo kupatula ngati matendawa amapezeka msanga, ndipo cholinga cha mankhwala ndikuteteza matendawa kwa nthawi yaitali. Mankhwala ambiri amaphatikizidwa ndi Rituxan (rituximab) ndipo mankhwalawa angagwiritsidwe ntchito pokonzanso chithandizo.
Mankhwala atsopano monga Velcade (bortezomib) ndi Treanda (bendamustine) ndi njira zosagwiritsira ntchito mankhwalawa. Mankhwala ambiri pamodzi ndi mankhwala atsopano akuphunziridwa m'mayesero a kachipatala, ndipo mwinamwake kuti mankhwala atsopano ndi chithandizo cha mankhwala a mantle cell lymphomawill zikhalepo posachedwa.
Popeza kuti matendawa amatha kupita patsogolo, mankhwala monga opaleshoni ndi ma ARV amakhala ndi ntchito yochepa chabe.
Kulimbana
Kulimbana ndi matenda atsopano a lymphoma kungakhale koopsa. Kodi mungayambire pati pamene mukuyamba kupeza? Kwa anthu ena, mankhwala opweteka angakhale abwino kwambiri.
Kwa ena, chisangalalo sichingakhale chosankha chabwino. Ngakhale zili choncho, pali chiyembekezo cha moyo wabwino ndi nthawi yomwe muli nayo. Onani zotsatila izi zokhudzana ndi khansa yomaliza . Pitani kwa achibale ndi abwenzi . Pali gulu lalikulu lothandizira la anthu omwe ali ndi ma lymphomas pa intaneti kwa iwo amene akufuna thandizo la ena omwe ali ndi zofanana. Ndipo kumbukirani kuti kufufuza kukupitirirabe, ndipo pali chitukuko chodalirika chomwe chikuchitika mu matenda a khansa lero.
Zotsatira:
Avivi, I., ndi A. Goy. Kukonzekera Mantle Cell Lymphoma paradigm: Zotsatira za Zochiritsira Zachilendo pa Zamakono. Kafukufuku wa khansa yachipatala . 2015. 21 (17): 3853-61.
Cheah, C., Seymour, J., ndi M. Wang. Mantle Cell Lymphoma. Journal of Clinical Oncology . Inasindikizidwa pa intaneti asanayambe kusindikiza January 11, 2016.
Dreyling, M., Ferrero, S., ndi European Mantle Cell Lymphoma Network. Udindo wa chithandizo chowongolera m'kati mwa selo lymphoma: kodi ndikumera wakufa kapena wamoyo? Haematologica . 2016. 101 (2): 104-14.
Kuwomba, M., ndi J. Armitage. Malo opalesedwa mu mantle cell lymphoma. Oncology . 2013. 27 Perekani 2: 2-6.
Maddocks, K., ndi K. Blum. Njira zakuchipatala mu mantle cell lymphoma. Kuchiza Khansa ndi Kafukufuku . 2015. 165: 251-70.
Martin, P. Ibrutinib - mankhwala atsopano a kachilombo kamene kamatulutsa kachilombo kameneka? Lancet . 2015 Dec 4. (Epub patsogolo pa kusindikiza).
Tucker, D., ndi S. Rule. Ibrutinib ya selo lymphoma. Zam'mbuyo Zam'tsogolo . 2016. 12 (4): 477-91.
Vose, J. Mantle cell lymphoma: 2015 posinthidwa pa matenda, kuika moyo pachiswe, ndi kuchipatala. American Journal of Hematology . 2015. 90 (8): 739-45.