Kukhala ndi mlingo wochepa wa cholesterol nthawi zambiri umawoneka kuti ndi chinthu chabwino cha thanzi. Koma hypobetalipoproteinemia ya banja ndi chizoloŵezi chosabadwa, choloŵa chobadwa chomwe chimayambitsa pang'ono mpaka kufika pang'onopang'ono kwambiri kwa ma diva ya cholesterol. Ikhoza kupanga zizindikiro zomwe zingafunikire kuchitidwa ndi chakudya chapadera ndi supplementation. (Matenda ena omwe mwinamwake amasonyezedwa ndi otsika kwambiri a HDL ndi achilendo a alpha kapoprotein matenda kapena matenda a Tangier .)
Mitundu
Matendawa makamaka amapezeka chifukwa cha kusintha kwa mapuloteni, apolipoprotein b (apoB). Mapuloteniwa amamangiriridwa ku mbali ya LDL ndipo amathandizira kutengera mafuta m'thupi mwa maselo m'thupi.
Pali mitundu iwiri ya hypobetalipoproteinemia: homozygous and heterozygous. Anthu omwe ali otetezeka chifukwa cha vutoli asinthika m'magulu onse awiri a jini. Zizindikiro mwa anthuwa zidzakhala zoopsa ndipo zidzachitika kale m'moyo, makamaka mkati mwa zaka 10 zoyambirira za moyo.
Anthu ena a mtundu wa Heterozygous, ali ndi kachilombo kamodzi kamene kamasintha. Zizindikiro zawo zimakhala zovuta, ndipo nthawi zina, sangadziwe kuti ali ndi matendawa mpaka khungu lawo likamayesedwa ali wamkulu.
Mafuta ochepa a cholesterol, makamaka LDL cholesterol, angachepetse chiopsezo cha matenda a mtima. Komabe, ngati cholesterol yanu ili yochepa kwambiri, ikhoza kuwonongera mavuto osiyanasiyana.
Zizindikiro
Kuwopsa kwa zizindikiro kumadalira mtundu wa mtundu wa hypobetalipoproteinemia womwe uli nawo. Anthu omwe ali ndi chiberekero cha hypobetalipoproteinemia apachibale amakhala ndi zizindikiro zoopsa kuposa mtundu wa heterozygous, umene umaphatikizapo:
- Kutsekula m'mimba
- Kutseka
- Kuthamanga
- Kukhalapo kwa mafuta obiriwira
Kuwonjezera pa zizindikiro za m'mimba, khanda kapena mwana yemwe ali ndi vuto la hypobetalipoproteinemia amasonyeza kuti zizindikiro zina zimakhala zochepa kwambiri m'magazi, mofanana ndi chikhalidwe, abetalipoproteinemia. Zizindikiro izi zikuphatikizapo:
- Matenda a ubongo. Izi zikhoza kukhala chifukwa cha kuchuluka kwa mankhwala a lipids kapena mavitamini osungunula mafuta omwe amazungulira mthupi. Zizindikiro izi zingaphatikizepo kukula kwapang'onopang'ono, osati kutentha kwambiri kwa tendon, kufooka, kuyenda kovuta, ndi kunjenjemera.
- Mavuto ndi kutseka magazi . Izi zikhoza kukhala chifukwa cha mavenda otsika a vitamini K. Maselo ofiira amagazi angayambenso kuwoneka osadziwika.
- Vitamini chosowa. Mavitamini osungunuka (A, K, ndi E) ali otsika kwambiri mwa anthuwa. Lipids ndi ofunika poyamwitsa mavitamini osungunuka m'madera osiyanasiyana a thupi. Pamene lipids, monga cholesterol ndi triglycerides , ali otsika, sangathe kunyamula mavitamini kumene akufunikira.
- Matenda osokonezeka . Izi zimaphatikizapo nkhani ndi maso ndi kukhudzidwa kumverera.
Anthu omwe ali ndi heterozygous hypobetalipoproteinemia angakhale ndi zochepa m'mimba zizindikiro, ngakhale kuti ambiri alibe zizindikiro.
Zonsezi zidzakhala ndi chiwerengero chochepa cha mthupi komanso LDL cholesterol.
Kudziwa
Pulojekiti yamakono idzachitidwa kuti ione kuchuluka kwa kolesteroloni yozungulira m'magazi.
Kuyesedwa kwa kolesteroloni kawirikawiri kumawulula zotsatirazi:
Homozygous
- Mafuta onse a mafuta a m'thupi amodzi <80 mg / dL
- Choleserala cha LDL chikhoza kufika <20 mg / dL
- Maseŵera otsika kwambiri a triglyceride
Heterozygous
- Mafuta onse a kolesteroloni <120 mg / dL
- Choleserala cha LDL chimakhala <80 mg / dL
- Mazira a Triglyceride ndi ovuta (<150 mg / dL)
Mipata ya apolipoprotein B ikhoza kukhala yochepa mpaka yosadalira malingana ndi mtundu wa hypobetalipoproteinemia alipo. Nthendayi ya chiwindi ingathenso kuthandizidwa kuti mudziwe ngati matenda a chiwindi ndi omwe amachititsa kuchepa kwa lipid. Zinthu izi, kuphatikizapo zizindikiro zomwe munthu akukumana nazo, zidzakuthandizira kutsimikiziranso za matenda a hypobetalipoproteinemia.
Chithandizo
Kuchiza kwa hypobetalipoproteinemia ya banja kumadalira mtundu wa matenda. Kwa anthu omwe ali ndi mavitamini, vitamini supplementation-makamaka mavitamini A, K, ndi E-ndi ofunika. Kudyetsa chakudya kumathandizanso pazinthu izi chifukwa chakudya choyenera cha mafuta owonjezera chiyenera kuchitidwa.
Anthu amapezeka kuti ali ndi hypothelipoproteinemia, mankhwala sangakhale osowa ngati alibe zizindikiro za matendawa. Komabe, anthu ena a heterozygous angafunikire kuikidwa pa chakudya chapadera kapena kulandira supplementation ndi mavitamini osungunuka mafuta ngati zizindikiro monga kutsegula m'mimba kapena kutupa-zilipo.
Zotsatira:
Beer MH, Porter RS, Jones TV. Buku la Merck la Kutulukira ndi Thandizo. Mkonzi wa 19, 2011.
Fauci AC, Kasper DL, Longo DL et al. Mfundo za Harrison za Mankhwala a M'kati. 18th edition, 2015.