Zizindikiro, Kuzindikira, ndi Chithandizo cha Lupus-Related Vasculitis
Kodi ndondomeko ya vasculitis ndi yani kwenikweni ndipo n'chifukwa chiyani ndifunika kwa anthu omwe ali ndi lupus? Ndi zizindikiro ziti zomwe mungayembekezere ndipo zingachiritsidwe bwanji?
Vasculitis Yogwirizana ndi Lupus - Tanthauzo
Lupus (systemic lupus erythematosus) ndi chikhalidwe chimene ma antibodies amaukira matupi anu. Mankhwalawa amatha kusokoneza pafupifupi makoswe onse a thupi, kuphatikizapo mitsempha ya magazi.
Vutoli ndi losavuta kumvetsa mwa kuphwanya mawu mpaka mu "vascu" kutanthauza zokhudzana ndi mitsempha ya magazi, ndipo "itis" kutanthauza mitsempha ya magazi. Choncho, kupweteka kwa mitsempha ndiko kutupa kwa mitsempha ya magazi yomwe imapezeka chifukwa cha ma antibodies a chitetezo cha mthupi choukira mitsempha ya magazi.
Vasulukiti ingakhudze mtundu uliwonse wa mitsempha ya magazi; mitsempha yomwe imanyamula magazi kuchokera pamtima kupita ku minofu, mitsempha yomwe imawombera magazi ochotsa m'magazi mpaka pamtima, ndipo mitsempha yaing'ono yomwe imakhala ndi mitsempha ya magazi yomwe imaphatikizapo mpweya woipa ndi carbon dioxide, komanso zakudya, zimachitika.
Pafupifupi 11 mpaka 36 peresenti ya anthu omwe ali ndi lupus adzakhala ndi minofu m'madzi ena.
Nchifukwa chiyani Vasculitis ndi Vuto?
Vasculitis akhoza kukhala vuto lalikulu mwa njira zosiyana. Kutupa kwa magazi m'chombo kungayambitse kukhala yopapatiza ndipo kumapangitsa kuti kuchepa kwa magazi kuchepetse ku matenda omwe magazi amatengera.
Nthawi zina mitsempha ya magazi ikhoza kutseka kwathunthu.
Nthawi zina, kutupa kungayambitse mitsempha ya magazi ndi kufooketsa. Zotsatira zake zimatha kuphulika, zomwe zimayambitsa kutaya kwa magazi komanso kuwonongeka kwa minofu.
Zifukwa za Vasculitis
Lupus ndi chifukwa chimodzi chokhacho cha kupweteka kwa mitsempha, ndi autoantibodies mu mitsempha ya magazi yomwe imayambitsa matenda.
Mankhwala amtunduwu amatha kupezeka chifukwa cha kusokonezeka m'kati mwa zombo kapena chifukwa cha matenda a zitsulo zamagazi.
Zizindikiro za Vasculitis Chifukwa cha Lupus
Zizindikiro zosiyana siyana za matendawa zimayenera kudziwika bwino kwa anthu omwe amavutika ndi kutupa: malungo, kutupa, malaise, ndi kutopa. Koma zizindikiro ndi zizindikiro zake nthawi zambiri amadalira malo ndi ziwalo ziti zomwe zimakhala ndi mitsempha ya mthupi zimagwira ntchito komanso kuphulika kwa kutupa. Vasulukiti imakhudza mitsempha yambiri ya thupi m'thupi kwambiri kuposa ena. Mwachitsanzo, impso zimakhudzidwa ndi lupus, koma mitsempha ya mitsempha imakhala yachilendo.
Zizindikiro zina zokhudzana ndi ziwalo zosiyanasiyana m'thupi zimaphatikizapo:
Khungu - Vasculitis yokhudzana ndi mitsempha yamagazi ya khungu ikhoza kuchititsa:
- Mazati ofiira kapena ofiira, nthawi zambiri pamilingo (Izi zimachitika pamene mitsempha yaing'ono yamagazi yomwe imakhudzidwa ndi matenda a vasculitis imatha kufooka ndi kusweka)
- Mawanga akuluakulu omwe amawoneka ngati zilonda zazikulu
- Mikoko (yosadziwika)
- Chimake lumpy rash (kawirikawiri)
- Zopweteka kapena zosavuta (Izi zikhoza kuchitika pamene mitsempha yambiri ya magazi imatuluka ndikuyamba kutupa pansi pa khungu)
Zowonjezera - Kuphatikizidwa kwa mitsempha ya magazi (vasculitis) ndi yowonjezeka ndipo ingaphatikizepo:
- Ululu ndi kupweteka chifukwa cha kutupa
- Kutupa ndi kutentha kwa kutentha
Ubongo - Vasculitis wokhudzana ndi dongosolo la mitsempha lakati limakhudza pafupifupi 10 peresenti ya anthu omwe ali ndi lupus ndipo mwina ndi vuto lalikulu kwambiri lokhudzana ndi lupus. Mchitidwe wamanjenje wamkati umasonyeza kuti lupus ikhoza kugwirizana ndi matenda a vasculitis kapena akhoza kukhala zotsatira zenizeni za autoantibodies motsutsana ndi ziwalo zina mu ubongo. Vasculitis mu ubongo zingayambitse zizindikiro zosiyanasiyana kuphatikizapo:
- Mutu
- Kusokonezeka kwa makhalidwe
- Kusokonezeka
- Kugonjetsa
- Sitiroko
Mtima - Zizindikiro zokhudzana ndi mitsempha ya mtima m'mimba mwa lupus ndizosazolowereka, koma zimatha kupweteka pachifuwa, makamaka zomwe zimachitika ndi mphamvu ndipo zimamasulidwa ndi mpumulo.
Mapungulo - Vasulukiti m'mapapu amatha kuyambitsa malungo, chifuwa, ndi chifuwa cha x-ray zomwe zimafanana ndi chibayo. Zingathenso kutulutsa mpweya wa m'mapapo (fibrosis) ndi kupuma pang'ono.
Maso - Vasculitis m'maso okhudzana ndi lupus nthawi zambiri amagwirizanitsidwa ndi mitsempha yaing'ono m'matina. Izi sizimayambitsa zizindikiro nthawi zonse, koma zikachitika zimaphatikizapo:
- Masomphenya a Blurry omwe amadza mwadzidzidzi ndikupitiriza
- Masomphenya ataya
Zovuta za Lupus Vasculitis
Pamene mitsempha yaing'ono imakhudzidwa ndi masculitis ndi lupus, zizindikiro zambiri zimakhala ndi mabala ofiira kapena ofiira pa khungu lotchulidwa pamwambapa. Mavuto aakulu ndi ochepa ndipo angaphatikizepo:
- Mesenteric vasculitis - Pamene ma mesentery ("bulangete" ya minofu yomwe imayika m'mimba) imakhudzidwa, kuwonongeka kwa matumbo kungabwereke komwe kungatengedwe ngati "kupweteka m'mimba".
- Kuchepetsa m'mimba - Kuphatikizidwa kwa mitsempha yambiri ya magazi m'mapapu kungachititse kuti magazi azizizira m'magazi.
- Mimba yambiri ya m'mimba - Kutupa kwa m'mimba ndi kutupa kwa mitsempha iwiri kapena yambiri yomwe imayambitsa kupweteka kwakukulu, achy, ndi zizindikiro zokhudzana ndi mitsempha yokhudzidwa, monga kugwa kwa mapazi.
Kuzindikira kwa Lupus Zokhudzana ndi Vasulitis
Zomwe zimayambitsa matendawa zimakhala zovuta, ndipo zizindikiro zomwezo zimachokera chifukwa cha matenda a mitsempha kapena njira zina (zowononga zotsatira za maantiantibodies pamatenda) omwe amapezeka ndi lupus.
Mayeso a magazi angayang'ane zizindikiro zosadziwika za kutupa. Mayesero kuphatikizapo kuwerengera kwathunthu kwa magazi, ntchito ya impso, ndi mayesero a chiwindi cha chiwindi amachitanso. Zojambula za mtima ndi ubongo (monga echocardiogram kapena MRI angiography) zingasonyeze kuti ali ndi mafilimu okhudzana ndi lupus. Maphunziro awa a labati ndi masewero amawerengedwa mogwirizana ndi mbiri yosamala ndi kuyesedwa kwa thupi kuti abwere ndi matenda a vasculitis.
Nthaŵi zina biopsy yachitidwa kuti mudziwe ngati kuwonongeka kwa minofu kukugwirizana ndi kupweteka kwa mthupi.
Mankhwala Othandizira Amuna Okhudzana ndi Mafupa Okhudzana ndi Lupus
Mitundu yambiri ya maambukomu amatha kuchiritsidwa ngati atayang'ana msanga chisanachitike kuwonongeka kwa thupi. Corticosteroids ndi mankhwala ena osokoneza bongo amayamba kugwiritsidwa ntchito kuchepetsa kutupa kwa mitsempha ya mitsempha. Nthawi zina, pamene mankhwala a steroid sagwira ntchito, mankhwala monga omwe amagwiritsidwa ntchito kwa anthu omwe ali ndi khansa ya m'magazi ndi amphine (mwachitsanzo, rituximab ) angakhale othandiza.
Kuti mudziwe ngati munthu ali ndi vasculitis, katswiri wa zaumoyo adzayang'ana mbiri yachipatala, kuchiritsa thupi ndikupempha mayesero ena apadera, mosasamala mtundu wa vasculitis, kuphatikizapo kuchuluka kwa magazi, urinalysis, ndi chiyeso cha ntchito ya chiwindi.
Kuthamangitsidwa mu Lupus Associated Vasculitis
Nthaŵi zambiri, kupanga matenda ndi kuyamba mankhwala kungachepetse kutupa m'mitsempha ya mitsempha yokhudzana ndi matenda a shuga. Komabe, nthawi zina, vutoli likhoza kukhala ndi mavuto aakulu, monga okhudzana ndi mapangidwe amphamvu. Ngakhale mankhwala amatha kukhala othandiza, kupweteka kwa mitsempha ndi matenda aakulu omwe amachititsa kuti olamulira asamachiritse, osati kuchiza.
Pansi pa Lupus Zokhudzana ndi Kutupa
Vasculitis yokhudzana ndi lupus ikhoza kukhala ndi zizindikiro zambirimbiri, komanso zimayambitsa mavuto aakulu okhudzana ndi chotengera cha magazi. Matendawa angakhale ovuta ndipo kawirikawiri amapangidwira mothandizidwa ndi zotsatira.
Ngakhale kuti mankhwalawa amatha kukhala ovuta kwambiri, mankhwala osokoneza bongo amatha kuchepetsa kutupa ndipo zingathandize kupewa mavuto ena.
Popeza chithandizo chamankhwala choyambirira chingapangitse kusiyana ndi matenda a lupus, kukhala ndi ubale wabwino ndi dokotala komanso kukhala wothandizira pawekha kungasinthe. Onani malangizowo kuti muzikhala ndi lupus tsiku ndi tsiku .
> Zosowa
- > Barile-Fabris, L., Hernandez-Cabrera, M., ndi J. Barragan-Garfias. Vasculitis mu Lupus Erythematosus Yoyenera. Malipoti Amakono a Rheumatology . 2014. 16 (9): 440.
- Kasper, Dennis L .., Anthony S. Fauci, ndi Stephen L .. Hauser. Mfundo za Harrison za Mankhwala a M'kati. New York: Maphunziro a Mc Graw-Hill, 2015. Print.
- > Shinjo, S., ndi E. Bonfa. Kutupa kwa Vasupitis mu Lupus Erythematosus Yoyamba: Kuyanjana ndi Anti-Ribosomal P Protein Antibody ndi Raynaud Phenomenon. Clinical Rheumatology . 2011. 30 (2): 173-7.