Kuzindikira Guillain-Barré Syndrome

Zimene Muyenera Kuyembekezera Panthawi Yomwe Mukuyesa

Guillain-Barré ndi matenda osadziwika omwe thupi lawo limakhala lolakwika chifukwa cha mitsempha ya mthupi ndipo imatumiza ma antibodies omwe amachititsa mitsempha imeneyi. Chotsatira chofala kwambiri ndi kufooka ndi kufooka komwe kumayambira pa nsonga zala zala ndi zala zazing'ono ndikufalikira mkati mthupi.

Pafupifupi 30 peresenti ya nthawi, kufooka kumeneku kumakula kwambiri moti wodwala sangathe kupuma payekha.

Iwo sangathe kumeza chakudya kapena makola popanda "kutsika chubu" komanso m'mapapu awo. Pazifukwa izi, Guillain-Barré akhoza kuika moyo wake pangozi ndipo amafunikira chidwi kwambiri ndi akatswiri azachipatala, nthawi zambiri kuchipatala. Pano mudzapeza momwe madokotala amadziwira ngati wodwalayo ali ndi matenda a Guillain-Barré.

Kufufuza Kwambiri

Pambuyo polemba mbiri yosamala kuti aone ngati Guillain-Barré ndizotheka, dokotalayo adzafufuza zowonjezera pazowunika. Chifukwa chakuti mitsempha ya phokoso yowonongeka ku Guillain-Barré, zovuta , monga kugwedezeka kwa mawondo wamba, kaŵirikaŵiri kulibe. Dokotala amayesanso kuyesa mikono ndi miyendo kuti awone ngati ali ofooka ndikuyesera mayesero kuti awone ngati pali mtundu uliwonse wamantha. Madokotala okhudzidwa ndi Guillain-Barré adzamvetsera mwatcheru chifukwa cha mitsempha yowopsa chifukwa ngati izi zowonongeka, zingapangitse kufunikira kotizira kapena kutsegula mpweya kuti wodwala apitirize kupuma.

Electromyography ndi Nerve Conduction Studies (EMG / NCS)

Pamene njira yamanjenje yowopsa imadwala ndi matenda, imasintha mtundu wa zizindikiro zamagetsi zomwe zimatumizidwa ndi kulandiridwa mu dongosolo. Poyerekeza kusintha kumeneku ndi zipangizo zamakono, madokotala sangathe kunena ngati chinachake chili cholakwika, komanso kuti ndi zigawo ziti za mitsempha zomwe zimakhudzidwa kwambiri.

Kudziwa izi kungathandize kutsogolera zosankha za mankhwala, komanso kupereka dokotala lingaliro la momwe matenda aakulu alili komanso kuti adzalandira nthawi yaitali bwanji kuti adziwe.

Mwachitsanzo, ngati wina ali ndi zofooka zomwe zikufalikira kumtunda ngati Guillain-Barré akhoza, maphunzirowa akuthandizira kudziwa ngati axon kapena tsamba la myelin la mitsempha likugwedezeka. Myelin amayendayenda ndi axon ndipo amathandiza zizindikiro zamagetsi kuyenda mofulumira kuposa momwe iwo angafunire. Ngati magetsi amayenda modabwitsa pang'onopang'ono kudzera mu mitsempha, madokotala angaganize kuti myelin ikugwedezeka, momwemo mtundu wofala kwambiri wa Guillain-Barré ndiye chifukwa.

Komano, ngati axon ikuukira, chizindikiro chochepa cha magetsi chidzachidutsa. Ngati izi zimayesedwa ndi maphunziro opanga mitsempha, imodzi mwa mitundu yosaoneka bwino ya Guillain-Barré ikhoza kukhala ndi udindo. Ngati izi zimakhudza zovuta zonse komanso magetsi a mitsempha, wodwalayo akhoza kukhala ndi mpweya wothamanga kwambiri (AMSAN), zomwe zimakhala zovuta kwambiri zomwe zimafuna mankhwala amphamvu komanso mankhwala ambiri kuti athe kuchira.

Lumbar Puncture

Muzovuta zapadera zomwe zimakhudza dongosolo la manjenje, kuchuluka kwa mapuloteni m'thupi la cerebrospinal fluid (CSF) akhoza kukhala wapamwamba.

Pachifukwa ichi, kuponyedwa kwa lumbar kungapangidwe. Kuwombera mchere kungathandizenso kutulukira ena omwe angayambe kutsanzira Guillain-Barré, monga matenda.

Mayesero a Magazi

Si zachilendo kuti madokotala azipanga mayeso a magazi kuti athandize matenda a Guillain-Barré. Nthawi zina, izi zingathandize kupeza wodwalayo ali ndi udindo. Mwachitsanzo, kusiyana kwa Miller-Fisher kwa Guillain-Barré kawirikawiri kumagwirizanitsidwa ndi antibody wotchedwa GQ1b. Kupeza wodwala uyu kumatsimikizira kuti Miller-Fisher ali ndi matenda osiyanasiyana, ndipo amachititsa kuti dokotalayo akhale wochenjera kwambiri panthawi yowonjezera.

Mayeso a magazi amathandizanso potulutsa zina zomwe zingawonekere mofanana ndi matenda a Guillain-Barré.

Malingana ndi mbiri ndi kuyezetsa thupi, dokotala akhoza kuyesa zizindikiro za khansa , matenda, kapena poizoni, monga mercury.

Ndikofunika kudziwa chomwe chikuyambitsa vuto kuti musapeze kupereka mankhwala osayenera. Kupeza chithandizo cha Guillain-Barré kumapangitsa akatswiri azachipatala kuganizira za chithandizo choyenera, ndipo angakupatseni inu zambiri zokhudza zomwe mungayembekezere kuti matendawa akupita, momwe mungapezere msanga, ndi thandizo lanji lomwe mudzafunikira kuti mubwererenso mapazi kachiwiri.

Zotsatira:

Ropper AH, Samuels MA. Adams ndi Victor's Principles of Neurology, 9th ed: The McGraw-Hill Companies, Inc., 2009. McCabe MP, O'Connor EJ.

Yuen T. Choncho, Continuum: Matenda a Mthupi, Matenda a Mthupi, Volume 18, Number 1, February 2012.