Cystic fibrosis (CF) ndi matenda omwe anabadwa nawo chifukwa cha chibadwa chomwe chimapangitsa thupi kukhala ndi mchere komanso madzi ndi maselo. Izi zimayambitsa msuzi wambiri womwe umatulutsa mapapo ndi ziwalo za m'mimba. Anthu ambiri amazindikira kuti cystic fibrosis ndi matenda a m'mapapu koma sadziwa kuti mbozi buildup imakhudza ziwalo zina.
Mitundu yokhudzidwa ndi CF ikuphatikizapo:
- Maungulo
- Pancreas
- Chiwindi
- Matumbo
- Sinuses
- Ziwalo zoberekera
Cystic fibrosis ndi imodzi mwa matenda omwe amabwera ndi majeremusi ndipo imakhudza pafupifupi 1 mwa ana onse 2500 obadwa ku United States. Ndilofala kwambiri ku Caucasians ndi Hispanics ndipo kawirikawiri sapezeka mwa anthu a ku Africa kapena ku Asia.
Zizindikiro
Zizindikiro za CF zimasiyana malinga ndi siteji ya matenda ndi ziwalo zomwe zimakhudzidwa.
Zizindikiro zoyambirira:
- Kuwonjezeka kwa kudya
- Kukula kosauka
- Oily, bulky, odetsa tsitsi zamadzimadzi
- Khungu lokoma mchere
- Chifuwa chafupipafupi
- Matenda opatsirana kawirikawiri
- Kuvuta kupuma
Zizindikiro zapamwamba zikuwoneka mwa mawonekedwe a mavuto, kuphatikizapo:
- Kutaya kosawerengeka kosadziwika
- Matenda a shuga
- Pancreatitis
- Matenda a chiwindi
- Kusadziletsa
Kudziwa
Cystic fibrosis imapezeka poyesera magazi, thukuta kapena maselo a fetus kuti akhalepo kwa zinthu kapena majini omwe amapezeka kwa odwala a CF.
Mimba
Ngati oyembekezera akudziwa kapena akukayikira kuti angakhale atanyamula khalidwe la CF , amniocentesis kapena chorionic villus angapangidwe panthawi yomwe ali ndi pakati kuti aone ngati mwanayo ali ndi matendawa.
Mwana wakhanda
Pakalipano, makumi anayi akuphatikizapo cystic fibrosis m'mayesero awo oyesedwa . Magazi amachotsedwa pa chidendene cha mwana asananyamuke kunyumba kuchipatala. Mwazi umatumizidwa ku laboratori ya boma ndipo ngati chosowa chikupezeka kuti dokotala wamkulu ndi dokotala wa m'dera lanu adzadziwitsidwa.
Amuna ndi Ana
Ngati sichikudziwika atabadwa, cystic fibrosis nthawi zambiri imapezeka m'chaka choyamba kapena ziwiri za moyo pamene mwana ayamba kusonyeza zizindikiro zowonetsera. Chiyeso cha cystic fibrosis ndikutenga thukuta. Chifukwa chakuti thupi silingathe kugwiritsa ntchito mchere wonsewo, anthu ambiri omwe ali ndi cystic fibrosis nthawi zambiri amatha kukhala osakwanira kuposa mchere wambiri mu thukuta lawo.
Poyesa thukuta, ma electrode amaikidwa pa khungu la wodwalayo kuti akonze zojambula thukuta. Thuku limasonkhanitsidwa ndipo amatumizidwa ku labotale kuti akayese mchere. Kujambula thukuta sikumvetsa chisoni ndipo kwagwiritsidwa ntchito kwa zaka zambiri kuti mupeze chithandizo cha mankhwala osokoneza bongo.
Chithandizo
Palibe mankhwala a cystic fibrosis. Chithandizo chikuphatikizapo mankhwala, zakudya, zochita masewera olimbitsa thupi, komanso mankhwala ochiritsira kuti athetse mavuto.
Mankhwala amalamulidwa kuti:
- Pewani ndi kuteteza matenda opatsirana
- Pitirizani kutseguka ndikuthandizani ndi kupuma
- Tulutsani ndi kuchotsamo timitengo tambiri
- Thandizani thupi kutenga zakudya
Ndondomeko ya zakudya ndi zakudya zimaperekedwa kuti:
- Ikani mavitamini osasungidwa
- Onetsetsani kuti chakudya cha calorie chikukumana ndi zofuna zamphamvu
- Onetsetsani kuti chakudya chokwanira chokwanira chokwanira ndikukula bwino
- Bwezerani mchere umene wataya mwa thukuta
Kuchita masewera olimbitsa thupi ndi mankhwala akulamulidwa kuti:
- Limbikitsani mtima ndi mapapo
- Mamasulidwe ndi omveka bwino
- Pitirizani kupirira ndi chikhalidwe chonse cha thupi
- Yonjezerani kuchuluka kwa mpweya woperekedwa ku makoswe
Zimayambitsa
CF imayambitsa vuto ku cystic fibrosis transmembrane conductance regulator ( CFTR ) jini. Ntchito ya CFTR yeniyeni ndiyo kupanga mapuloteni omwe amayendetsa kayendetsedwe ka mchere ndi madzi mkati ndi kunja kwa maselo athu onse.
Aliyense wa ife ali ndi makope awiri a CFTR gene chifukwa tili ndi mmodzi mwa makolo athu onse. Nthawi zina mafupa a CFTR omwe timalandira kuchokera kwa makolo athu ndi achilendo, koma sizikutanthauza kuti tidzakhala ndi CF.
Ngati munthu adzalandira:
- 2 mitundu yachibadwa ya CFTR: Iye sadzakhala ndi CF ndipo sadzakhala wonyamulira.
- 1 yachibadwa CFTR jini ndi 1 yachilendo CFTR jini: Iye sadzakhala ndi CF koma adzanyamula jini wosalongosoka ndipo akhoza kuzipereka kwa ana ake.
- 2 majeremusi osadziwika a CFTR: Adzakhala ndi matenda a CF.
Kupewa
Chifukwa cystic fibrosis ndi matenda obadwa nawo, sangathe kulepheretsedwa. Komabe, kukhalapo kwa kachilombo koyipa kwa CFTR kungapezeke ndi mayeso a magazi. Asanayambe mwana , amuna omwe amadziwa kapena akuganiza kuti mmodzi kapena onse awiri angakhale ndi vuto la CF ayenera kufufuza uphungu kuti athe kudziwa momwe angapewere matenda a CF.
Kukhala ndi Matenda a Kystic
Sizinali kale kwambiri kuti ana omwe anali ndi cystic fibrosis sankakhala moyo woposa ana. Tsopano, zambiri zimadziwika za matenda omwe sankadziwika kale. Chidziwitso chimenechi chachititsa kuti anthu azikhala ndi moyo wathanzi komanso wopindulitsa mpaka atakula. Anthu omwe amakhala ndi cystic fibrosis amafunika kusamala kwambiri ndi matenda. Ayeneranso kutenga mavitamini a m'mimba, mankhwala opatsirana pogwiritsa ntchito maantibayotiki, ndi mankhwala ena m'miyoyo yawo yonse. Amuna kawirikawiri amalephera, amayi sangakhale ochepa koma amatha kukhala ndi pakati.
Ngati Mwana Wanu Akudziwika
Dokotala wanu wa banja kapena adokotala adzapitirizabe kusamalira mothandizidwa ndi gulu la akatswiri. Mwinamwake iye adzakulozerani inu ku cystic fibrosis pakati panu. Ngati sichoncho, funsani kutumizidwa. Malo ogwiritsira ntchito mankhwala a cystic fibrosis amagwiritsidwa ntchito ndi madokotala ndi akatswiri a zachipatala omwe amadziwika bwino ndi matendawa ndipo ali okonzekera bwino kuyang'anira mwana wanu ndikupereka chithandizo malinga ndi kafukufuku wamakono. Pakatikati, mwana wanu adzawona gulu la operekera kuphatikizapo katswiri wamapiritsi (katswiri wamapapo) ndi wodyetsa zakudya. Chitsimikizo cha cystic fibrosis ndi malo abwino kuti mudziwe zambiri zokhudza malo omwe mumakhala nawo komanso chuma chanu.
Chitsime:
Cystic Fibrosis. National Heart Lung ndi Magazi Institute: Matenda ndi Mavuto Index. August 2007.