Zizindikiro zoyambirira ndi zapamwamba za CF, Matenda a Progressive ndi Genetic
Kawirikawiri, zizindikiro za cystic fibrosis zimakula pamene matendawa akuchuluka. Matendawa, omwe amayamba chifukwa cha jini yolakwika, amachititsa kuti ntchentche ikhale yambiri m'mapapu (kutseka maulendo a m'mphepete mwa ndege ndikuwatsogolera ku matenda, kuwonongeka kwa mapapo, ndi kupuma kwa mpweya), kuperewera kwa thupi (kuteteza thupi kuti lisamawononge bwino zakudya kutenga zakudya), ndi ziwalo zina.
Kachilombo kosavomerezeka sikulola thupi kusamutsa madzi ndi mchere kupita ku maselo, ndipo zimapangitsa kuti zisawonongeke (kawirikawiri ndi zochepa thupi komanso madzi abwino mwa anthu omwe ali ndi thanzi labwino kwambiri komanso amodzi mwa anthu omwe ali ndi CF). Mitsempha yambiriyi imatulutsa ziwalo ndipo zimateteza thupi kukhala losavuta.
Zizindikiro Zakale za Cystic Fibrosis
Nthaŵi zambiri, makanda omwe ali ndi cystic fibrosis (CF) amawoneka ngati ana a thanzi chifukwa matendawa samayambitsa zochitika zosaoneka poyamba. Pafupifupi 20 peresenti ya nthawiyi, makanda omwe ali ndi CF adzakhala ndi vuto lalikulu la m'mimba pa kubadwa komwe kumatchedwa meconium ileus. Izi zimangokhalapo ngati mwana ali ndi CF, choncho ngati izi zimachitika nthawi zambiri zimakhala ngati chizindikiro choyamba cha matendawa.
Zizindikiro za Common Cystic Fibrosis
Ngati cystic fibrosis sichidziwike pa kubadwa, zizindikiro zina zimayamba kuonekera chaka choyamba kapena ziwiri za moyo, monga:
- Zovuta Zolemera Zolemera. Mitsempha ya m'magazi ndi matumbo a m'mimba amachititsa kuti thupi lisamagwire bwino ntchito. Zakudya zomwe amadya zimadutsa m'thupi popanda zakudya zambiri zowonjezera, zomwe zimayambitsa kukula kosauka. Ngati mwana sanabwererenso kulemera kwake kwa masabata 4-6 kapena akuwonetsa chitsanzo chopitiriza kukula, dokotala akhoza kuyamba kukayikira CF.
- Matenda Aakulu. Chifukwa chakuti zakudyazo sizingapangidwe ndi zakudya, ubongo umayesa kukwaniritsa zofunikira za thupi mwa kutumiza zizindikiro za njala. Anthu omwe ali ndi cystic fibrosis nthawi zambiri amakhala ndi chilakolako chofuna kudya ndipo akhoza kudya chakudya chochuluka popanda kupindulitsa.
- Bulky, Oily, Mankhwala Osokoneza Bongo. Njira yosagwira ntchito yogaya zakudya imakhala ndi vuto linalake lokuta mafuta ndi mapuloteni. Zambiri mwa zomwe zimakhala ndi ubwino wambiri woperekera zakudya zimatulutsidwa ndi matumbo, zomwe zimapangitsa kuti thupi likhale losaoneka bwino lomwe limakhalapo kwa odwala omwe ali ndi CF.
- Matenda Okhudzidwa ndi Otsitsimula Nthawi Zambiri. Kusuta, kupuma kovuta, ndi matenda opatsirana kawirikawiri ndizo zizindikiro zoyamba zomwe makolo amawona ndi ana omwe ali ndi CF.
- Khungu Labwino. Chibadwa cha jini chimene chimayambitsa cystic fibrosis chimasokoneza mphamvu ya thupi kuti isunthire mchere mkati ndi kunja kwa maselo. Mchere umene sungathe kulowetsedwa umatulutsidwa kudzera pakhungu ndi thukuta la thukuta, zomwe zimayambitsa chizindikiro cha salty chowotcha thukuta. Nthawi zina, pangakhale mchere wonyezimira womwe umasungira pakhungu. Mchere wotchedwa salt excretion ndi glands zotuluka thukuta ndiwo maziko a mayeso omwe amapezeka kwambiri kuti agwiritsidwe ntchito ndi mankhwala a cystic fibrosis.
Zizindikiro Zapamwamba ndi Mavuto a CF
Zizindikiro zapamwamba za cystic fibrosis sizinali zizindikiro za matenda omwewo, koma zizindikiro za kuwonongeka kumene CF kumayambitsa pa nthawi. Panthawi yomwe izi zikuwonekera, anthu ambiri amadziwa kale kuti ali ndi cystic fibrosis ndipo akhala akudwala matendawa kwa nthawi ndithu. Mavuto otsatirawa ndi zizindikiro za CF:
- Kuchedwa Kutha msinkhu. Nthawi zina kutha msinkhu kumawoneka kwa atsikana omwe ali ndi cystic fibrosis chifukwa cha zakudya zoperewera.
- Kusadziletsa. Amuna ambiri omwe ali ndi cystic fibrosis ali osabereka chifukwa chotsekemera kumatseka ubwamuna. Azimayi amatha kusabereka chifukwa cha umuna wochuluka wa chiberekero womwe umalepheretsa umuna kulowa mu ziwalo zoberekera.
- Matenda a shuga. M'kupita kwa nthaŵi, kuwonongeka kwa mphukira ndi cystic fibrosis kumapangitsa kuti asiye kutulutsa insulini yokwanira. Pafupifupi 15 peresenti ya anthu omwe ali ndi cystic fibrosis omwe amafika pokhala achikulire adzakhala ndi shuga ya shuga ya insulini.
- Matenda a Chiwindi. Kutsekemera kwa bile mu chiwindi kumayambitsa kuwonongeka ndi chiwindi mwa pafupifupi 5% a odwala cystic fibrosis. Ngati kuwonongeka kwa chiwindi kumachitika, kawirikawiri kumawoneka akuluakulu.
- Matenda a Gallbladder. Nkhumba imasungira chinthu chotchedwa bile chomwe chimapangidwa ndi chiwindi ndi zothandizira mu chimbudzi cha mafuta. Kwa anthu ambiri omwe ali ndi cystic fibrosis, bile ndi yowopsya ndipo sangathe kudutsa mu ndudu ya bile kuchoka mu ndulu . Nthawi zambiri izi sizimabweretsa zizindikiro, koma pafupifupi 10 peresenti ya cystic fibrosis idzakhala ndi mazuru omwe amafunikira opaleshoni.
- Pancreatitis. Pamene bile imatuluka m'matumbo, imalowa m'mimba mwaching'ono kudzera mumatope omwe amagawanika nawo. Ngati galasi imachoka mu ndulu ndikugwiritsidwa ntchito m'kati mwa njira zamtundu wina, zotsekemera za pancreatic sizingatheke. Izi zimapangitsa kupweteka ndi kupweteka kwambiri kwa kapangidwe kotchedwa pancreatitis, komwe kumafuna opaleshoni.
Chitsime:
Cystic Fibrosis Foundation. About Cystic Fibrosis. 10 April 2016