Zotsatira za Gene Yopanda Thupi Thupi
Cystic fibrosis (CF) ndi matenda aakulu, omwe amafupikitsa moyo omwe amapezeka chifukwa cha vuto la chibadwa. Gulu losawonongeka limakhudza mphamvu ya thupi yosamutsira madzi ndi mchere kupita ku maselo omwe amabweretsa thukuta, ntchentche, ndi michere ya m'mimba. Izi zimayambitsa katsekemera, komwe kawirikawiri ndi koonda komanso madzi abwino, kuti akhale obiriwira komanso osakaniza.
Mitsempha yambiriyi imatsegula ziwalo ndi kuwateteza kuti asagwire bwino ntchito. Zotsatira za cystic fibrosis zingakhudze ziwalo zingapo ndi machitidwe.
Zotsatira za Cystic Fibrosis
Mu CF, ziwalo zambiri za thupi ndi machitidwe zimakhudzidwa, kuphatikizapo:
- Njira za kupuma (ziwalo monga mapapo ndi zina mwa thupi zomwe zimakulolani kupuma ndi kufalitsa magazi ozungulira thupi lonse)
- Matenda a m'mimba (okhudzana ndi m'mimba ndi m'matumbo)
- Musculoskeletal system (minofu ndi mafupa)
- Njira yotchedwa Genitourinary system (yokhudza ziwalo zoberekera ndi zogonana)
- Njira zoberekera (njira zamagonana monga madzi, mahomoni, ndi pheromones)
Mabungwe Omwe Amakhudzidwa ndi CF
Zina mwa zikuluzikulu zomwe zimakhudzidwa ndi CF zimaphatikizapo mapapo, zikwangwani, chiwindi ndi ndulu, matumbo ndi ziwalo zoberekera.
Maungulo
Pali mankhwala osokoneza bongo m'mphepete mwa kupuma chifukwa cha kutengeka kwa electrolytes m'matenda a mumsewu.
Ntchentche imamera mosavuta ndipo zimakhala zovuta kuchoka pamsewu, zomwe zingayambitse mitsempha, zimawononga alveoli (mapapu ting'onoting'ono a mpweya) m'mapapo ndikulola kuti tizilombo toyambitsa matenda tizilombo toyambitsa matenda tizilombo toyambitsa matenda.
Cystic fibrosis imayambitsa mavuto m'mapapu pamene msuzi wandiweyani amamanga ndipo amamangika mumtunda.
Izi zikachitika:
Njira zopuma zimatsekedwa ndipo mpweya sungathe kudutsa.
Mabakiteriya amakula mumagulu a ma mucus ndipo amachititsa matenda m'mapapo, mphuno, ndi machimo.
Mankhwalawa amatha kukhala ndi odwala ena a CF.
Pancreas
Nkhanzazi ndi mbali ya dongosolo lakumagazi. Ntchito yake ndiyo kusunga mavitamini omwe amafunika kuti adye chakudya, ndi hormone yotchedwa insulini imene imalamulira shuga ya magazi. Cystic fibrosis imachititsanso kuti maselowa akhale obiriwira.
Izi zikachitika:
Madzi otentha kwambiri amaphwa.
Mavitamini sangathe kudutsa choletsedwa.
Chakudya sichiri bwino ndipo thupi silingathe kutenga zakudya.
Potsirizira pake, kutsekedwa kwa mphukira kungayambitse kupweteka kumene kumawononga maselo opanga insulini ndi kuwaletsa kuti asapange insulini. Insulini sichipezeka kwa maselo, omwe amachititsa kuti shuga ya magazi iwonjezeke. Matendawa amatchedwa shuga wodalirika wa shuga, yomwe imapezeka pafupifupi 15% mwa onse odwala matenda a shuga.
Chiwindi ndi Gallbladder
Ngakhale si zachilendo, mphulupulu zowonjezereka zingathe kutsekanso ntchentche za chiwindi ndi nyongolotsi ndikuziletsa kuti zisagwire bwino ntchito.
Ngati mitsempha ya chiwindi imapitirira kwa nthawi yaitali, chiwindi chikhoza kuwonongeka kwamuyaya.
Ngati mitsempha ya ndulu imakhala yotsekedwa, ndulu imachotsedwa nthawi zambiri.
Matumbo
Nthawi zina matumbo ndilo choyamba chokhudzidwa ndi cystic fibrosis. Pafupifupi 20 peresenti ya ana onse obadwa kumene ali ndi CF, mawonekedwe obisika kwambiri m'matumbo omwe amachititsa kuti matumbo akhale mitsempha ya meconium.
Zida zoberekera
Cystic fibrosis imakhudza ziwalo zoberekera za abambo ndi amai mosiyana ndi njira zotsatirazi:
- Amuna Nthawi zambiri amakhala opanda mphamvu chifukwa chingwe chamtunduwu chimayambitsa kutsekemera komwe kumalepheretsa umuna kutuluka.
- Azimayi nthawi zambiri amatha kukhala ndi pakati koma nthawi zina amachepetsa kubereka chifukwa cha ntchentche yamtundu wa chiberekero imatseka umuna.
Chitsime:
Cystic Fibrosis. Chipatala cha Ana Onse. Zokhudza Zaumoyo.