Kudziwa Adani Wanu
Kuwonongeka kwa mphuno chifukwa cha matenda opatsirana mobwerezabwereza ndilo vuto lalikulu la imfa kwa anthu omwe ali ndi cystic fibrosis . Kudziwa zina mwa zovuta zomwe mungakumane nazo zingakuthandizeni kukonzekera mavuto omwe mukukumana nawo ndikukonzekera njira zothetsera mavuto anu. Zamoyo izi sizichitika nthawi zambiri mwa anthu abwinobwino, koma zimakhala zovuta makamaka kwa iwo omwe ali ndi CF.
Aspergillus
Aspergillus ndi bowa limene limapezeka nthawi zambiri m'chilengedwe, choncho zimakhala zovuta ngati sizingatheke kuti musagwirizane nazo. Kwa anthu ambiri, Aspergillus ndi yopweteka koma kwa 15 peresenti ya anthu omwe ali ndi cystic fibrosis, amatha kuika moyo wawo pachiswe chomwe chimatchedwa brinkpulmonary aspergillosis (ABPA).
Pankhaniyi, mudzakhala ndi Aspergillus mu ntchentche m'mapapu anu koma sizowonongeka. M'malomwake, zimayambitsa kuteteza thupi kwambiri ndi ma antibodies komanso maselo a chitetezo cha m'thupi, zomwe zimayambitsa chibayo cha eosinophilic. Zizindikiro zimaphatikizapo chifuwa ndi zobiriwira zobiriwira kapena zofiirira mumtundu wanu. Mudzakhala ndi zizindikiro za mphumu za kuphulika komanso kuyendetsa ndege. Mukakumana ndi mavuto aakulu, mumakhalanso ndi malungo, mutu, komanso kusowa chakudya. Amapezeka ndi khungu lopanda khungu la Aspergillus antigen ndi kuyesa magazi kwa Aspergillus precipitins ndi IgE antibodies ndi chifuwa X-ray kapena CT.
Chithandizo chili ndi prednisone yamlomo monga corticosteroids yosamalidwa sichigwira ntchito bwino kwa ABPA. Ngati ABPA ikupitirizabe, mukhoza kupatsidwa mankhwala osokoneza bongo. Odwala amatsatiridwa ndi chifuwa cha X-rays, kuyesayesa kwa pulmonary, ndi mayeso a labu monga kuwonongeka kwa mapapo kungapitirize kuchitika popanda kusintha kwa zizindikiro. Pali chiopsezo chokhazikika cha pakati pa airways, chomwe chimatchedwa bronchiectasis, ndi kupweteka kwa mapapo.
Pseudomonas aeruginosa
Anthu oposa theka la anthu onse omwe ali ndi cystic fibrosis amatha kulimbana ndi matenda a mapapu chifukwa cha mabakiteriya Pseudomonas aeruginosa pa nthawi ina. Ndipotu, ndiyo nyama yomwe imapezekapo makamaka m'magulu okhudzana ndi mapapo a CF. Choncho P. aeruginosa ndi mabakiteriya omwe amafa chifukwa cha anthu ambiri omwe ali ndi CF.
P. aeruginosa ndi mabakiteriya wamba omwe amapezeka ponseponse m'nthaka, madzi, madontho, ndi zina zotentha, kotero sungapewe. Zimandivuta kuchotsa pamene zimalowa m'kati mwa kupuma.
Maonekedwe a antibiotic tobramycin, omwe amadziwika kuti TOBI, amagwiritsidwa ntchito pochizira matenda akuluakulu a Pseudomonas anthu omwe ali ndi cystic fibrosis. Dothi louma TOBI Podhaler lapangidwanso.
Burkholderia cepacia
Burkholderia cepacia , yomwe nthawi zambiri imatchedwa Pseudomonas cepacia , ndi yovuta koma yoopsa kwa anthu omwe ali ndi cystic fibrosis. Ngakhale kuti simukukumana ndi Burkholderia cepacia , muyenera kumvetsetsa zomwe zili komanso kuchepetsa chiopsezo chanu .
Ngakhale zili m'deralo, zovuta zomwe zimawopsyeza anthu tsopano zikuwonetsedwa kuti zimafalitsidwa kuchokera kwa munthu ndi munthu. Amatha kupangitsa mapapu kukhala othetsera matendawa ndipo amayambitsa matenda omwe amachepetsa pang'onopang'ono m'mapapo. Ikhozanso kufalikira mthupi lonse lomwe limayambitsa matenda a cepacia ndi kuchepa kwa mapapo. Izi zingachititse imfa. Amachiritsidwa ndi mankhwala osakaniza monga momwe zingakhalire osagonjetsedwa ndi maantibayotiki ambiri.
MRSA
Staphylococcus aureus (MRSA ) yosagonjetsedwa ndi Methicillin , ikukhala vuto lofala kwambiri kwa anthu omwe ali ndi cystic fibrosis. MRSA ikhoza kupezeka pa khungu, mabala, mumtsuko, ndi ziwalo zina zambiri za thupi koma mapapo ndi malo ambiri omwe ali ndi matenda a MRSA kwa iwo omwe ali ndi CF.
MRSA imafalikira kudzera mwachindunji komanso mwachindunji kulankhulana ndipo ingapezeke mmudzi kapena kuchipatala. Kuchita kulamulira bwino kwa matenda kungathandize kuchepetsa chiopsezo.
> Zotsatira:
> Gautam, V .; Singhal, L .; ndi Ray, P. " Burkholderia cepacia complex: Beyond pseudomonas ndi acinetobacter." Ind J Med Microb. 2011; 29 (1): 4-12.
> MALO A NKHANI Allergic Bronchopulmonary Aspergillosis (ABPA). Merck Manual Professional Version. http://www.merckmanuals.com/professional/pulmonary-disorders/asthma-and-related-disorders/allergic-bronchopulmonary-aspergillosis-abpa#.
> Ramphal R. Matenda Chifukwa cha Mitundu ya Pseudomonas ndi Zogwirizana. Mu: Kasper D, Fauci A, Hauser S, Longo D, Jameson J, Loscalzo J. eds. Mfundo za Harrison za Internal Medicine, 19e . New York, NY: Hill ya McGraw; 2015.