Kupititsa patsogolo mu kufufuza kwa Biogenetic Kuwonjezera Moyo Wosatha
Cystic fibrosis (CF) ndi matenda osokoneza bongo omwe amakhudza moyo wabwino komanso nthawi ya moyo kwa anthu omwe ali ndi matendawa. Ngakhale kuti matendawa ndi osowa kwambiri (omwe amangogwira anthu pafupifupi 30,000 ku US), amachitabebe kuti ndi imodzi mwa matenda omwe amachititsa kuti anthu azivutika kwambiri.
Ngakhale kuti chiwerengero cha anthu omwe ali ndi CF chikhalabe chochepa kuposa chiwerengero cha anthu ambiri, kumvetsetsa za matendawa, komanso njira zothandizira kwambiri , zayamba kusintha zinthu.
Zoyembekeza za Moyo Zimapeza mwa Anthu Amene Ali ndi Cystic Fibrosis
Mu 1938, pamene CF inayamba kudziwika kuti ndi matenda, ana ambiri omwe anapezeka ndi matendawa anamwalira asanabadwe tsiku loyamba. Pofika zaka za m'ma 1950, anthu omwe ali ndi CF amakhala ndi moyo wautali koma nthawi zambiri sankatha msinkhu wawo. Pamene zinthu zinayamba kusintha m'zaka za m'ma 1980, pamene anthu akukhala pakati pa zaka makumi awiri mphambu makumi asanu ndi awiri, mpaka pamene anapeza CFTR gene mu 1989 tinayamba kuona kusintha.
Masiku ano, omwe ali ndi zidziwitso zowonjezera za machitidwe a chibadwa cha CF, tili ndi njira zothetsera matendawa, kuteteza matenda, komanso kusintha mapuloteni kwa anthu omwe ali ndi matendawa.
Chotsatira chake, chiwerengero cha moyo wa anthu omwe ali ndi CF lero ndi 37.5. M'dziko lotukuka, chiwerengerochi ndi chapamwamba kwambiri ndi chiwerengero chapakati pa zaka 42 mpaka 50.
Chifukwa cha kupititsa patsogolo mankhwala ndi biotechnologies, ofufuza amanena kuti ana omwe akubadwa masiku ano akhoza kukhala ndi moyo wabwino kuposa tsiku lawo lakubadwa.
Moyo Wowonjezereka Umagwiritsidwa Ntchito Kugwiritsa Ntchito Maantibayotiki
Pafupifupi 80 peresenti ya anthu omwe ali ndi cystic fibrosis adzalandira matenda ndi Pseudomonas aeruginosa , mabakiteriya omwe amagwiritsidwa ntchito ambiri akuona kuti kufalikira kulikonse padziko lonse lapansi.
Anthu omwe ali ndi CF ali ndi chiopsezo chachikulu cha P. aeruginosa , matenda omwe angayambitse kupuma komanso ngakhale imfa.
Ndipotu, 50 peresenti ya anthu omwe ali ndi CF omwe amapita kuchipatala cha P. aeruginosa adzafa chifukwa cha matendawa.
Mwamwayi, pali mankhwala ambiri masiku ano omwe angathe kuchiza ndikuletsa matenda a P. aeruginosa . Izi zikuphatikizapo antibiotics tobramycin, levofloxacin, ciprofloxacin, azithromycin, ndi cephalosporins. Kusankha mankhwala nthawi zambiri kumayesedwa pofuna kuzindikira momwe vuto la Pseudomonas lingakhudzire kusankha ma antibiotic osiyanasiyana.
Administration ikusiyana ndi mtundu ndi siteji ya matenda. Kawirikawiri tobramycin kapena ma levofloxacin amatha kuperekedwa kwa miyezi pang'onopang'ono kuti zisawononge kukula kwa bakiteriya. Mankhwala a oralipiploxacin ndi azithromycin angagwiritsidwe ntchito popewera matenda kapena kuchiza matenda omwe alipo.
P. aeruginosa amatha kupatsidwanso ndi mtundu wa penicillin wotchedwa ureidopenicillin.
Zina Zowonjezera pa Chithandizo cha Cystic Fibrosis
Kuphatikiza pa mankhwala othandiza kwambiri ochiza ma antibayotiki, kupititsa patsogolo kwina kwapangidwa pochiza matenda a mapaipi ndi a CF. Zikuphatikizapo:
- Mankhwala osokoneza bongo amachititsa kuthana ndi vuto la chimbudzi chifukwa cha ntchentche m'matumbo.
- Pulmozyme (dornase alfa) yomwe imayambitsa ntchentche yomwe imayendetsa misewu
- bronchodilators (inhalants zomwe zimachititsa ndime za pamsewu kutseguka)
- mankhwala abwino oletsa kupweteka
- mchere wotchedwa hypertonic saline kuti uwonjezere kuchuluka kwa sodium yotayika mumlengalenga
Zinthu zonsezi zimapangitsa kuti anthu omwe ali ndi CF aziwonjezeka kwambiri.
Mawu Ochokera
Cystic fibrosis ndi matenda osiyana kwambiri ndi zaka 20 kapena 30 zapitazo. Lero, anthu omwe ali ndi CF akhoza kukhala moyo wokhutira ndi wokhutiritsa, kupita ku koleji, kupeza ntchito, ndi kukonzekera banja. Zomwe zimatengeradi ndizigawo zisanu ndi chimodzi kuti mupeze moyo wathanzi ndi wathanzi:
- kumvetsetsa mankhwala anu ndi kuwagwira monga momwe amachitira
- kuonetsetsa kuti chakudya choyenera ndi choyenera ndi 50 peresenti yowonjezerapo ndalama zowonjezera
- kumwa zakumwa zambiri kuti mukhale osungunuka bwino
- kupanga mapulogalamu olimbitsa thupi omwe ali nawo kutsutsana ndi maphunziro a cardio
- kupeĊµa matenda mwa kusamba m'manja nthawi zonse, kupeza katemera, ndikupewa ena omwe akudwala
- kuwona dokotala wanu nthawi zonse kuti muonetsetse kuti mukusamalidwa kosalekeza
Pamapeto pake, cystic fibrosis si chilango cha imfa chomwe chinalipo, ndipo, mwa chisamaliro choyenera ndi chithandizo, palibe chifukwa chomwe simungapitirire kuyembekezera mu umoyo ndi kuchuluka kwa moyo.
> Chitsime:
> O'Sullivan, B. ndi Freedman, S. "Cystic fibrosis." Lancet . 2009; 373 (9678): 1891-1904.