Njira zina zochepa zomwe zingasokonezedwe zingapangitse kusiyana kwakukulu
Mitsempha yotchedwa muscular dystrophy ndi mndandanda wa matenda a geneim autoimmune omwe amachititsa zofooketsa, kupweteka, ndi kutaya kwa mitsempha yomwe imayendetsa kayendetsedwe kake. Palibe chithandizo chodziwika bwino cha matenda osokoneza bongo, ndipo odwala nthawi zambiri amapita kuchipatala kuti athetse matendawa.
Zomwe Zachilengedwe Zidzakhala Zopangira Matenda a Mitsempha
Pakalipano, kafukufuku wowerengeka adayesa kugwiritsa ntchito njira zina zothandizira pa matenda a mitsempha yotchedwa muscular dystrophy .
Komabe, pali umboni wina wosonyeza kuti mitundu ina ya mankhwala osamalidwa amatha kupereka ubwino kwa odwala matenda a dystrophy, ngakhale kuti ambiri mwa maphunzirowa ndi okalamba. Pano pali kuyang'ana pa zofufuza zingapo zazikulu:
1) Zowonjezera Zakudya
Kafukufuku angapo ang'onoang'ono amasonyeza kuti zakudya zowonjezera zakudya zimapindulitsa odwala matenda a dystrophy. Mwachitsanzo, kafukufuku wa 2006 kuchokera ku American Journal of Clinical Nutrition anapeza kuti supplementation ndi amino acids inathandiza kuti thupi lonse liwonongeke (zomwe zimadziwika kuti Duchenne muscular dystrophy). Phunzirolo linaphatikizapo anyamata 26 ndi Duchenne muscular dystrophy, aliyense mwa iwo amene anachitidwa ndi amino acid supplement kwa masiku khumi.
Kafufuzidwe kafukufuku akuwonetsanso kuti kulenga (amino acid yomwe imathandiza kupereka maselo a minofu ndi mphamvu) ingathandizenso kuteteza matenda a mitsempha. Komabe, mu kafukufuku wa 2005 wa anyamata 50 omwe ali ndi Duchenne muscular dystrophy (yofalitsidwa mu Annals of Neurology ), asayansi adapeza kuti miyezi isanu ndi umodzi yamachiritso ndi zowonjezera mavitamini alephera kuthetsa mphamvu ya minofu mwa ophunzira.
2) Qigong
Qigong imathandizira kukhala ndi moyo wabwino kwa anthu omwe ali ndi matenda osokonezeka maganizo, malinga ndi kafukufuku wina wa 2004 umene unalembedwa mu Disability and Rehabilitation. Phunzirolo linakhudza odwala 28 omwe ali ndi mitsempha yowopsa kwambiri, ena mwa iwo omwe adanena kuti kusintha kwa ubongo, mwakuthupi, ndi m'maganizo (kuphatikizapo kuchepetsa nkhawa) pambuyo pochita qigong.
3) Teyi yobiriwira
Tiyi yaukhondo ingakhale yopindulitsa kwa anthu omwe ali ndi Duchenne muscular dystrophy, malinga ndi kafukufuku woyambirira wofalitsidwa mu American Journal of Physiology: Cell Physiology mu 2006. Poyesedwa pa mbewa, ofufuza anapeza kuti epigallocatechin gallate (antioxidant yomwe imapezeka mu tiyi yobiriwira) Thandizani kuteteza kusokonezeka kwa minofu chifukwa cha kupweteka kwa mitsempha. Komabe, posachedwa kuti tiwone ngati tiyi yobiriwira ingakhale ndi zotsatira zofanana pa anthu.
Maonekedwe a Muscular Dystrophy
Pali matenda oposa 30 omwe amadziwika ngati mitsempha yowopsa. Ngakhale kuti mawonekedwe ena amawoneka kuyambira ali wakhanda kapena ubwana, ena samawonekera mpaka zaka zapakati kapena m'tsogolo mmoyo. Zinthu monga msinkhu wa kuyambira, kukula kwa minofu yofooka, ndi kuchuluka kwa kupitirira kumasiyana malingana ndi mawonekedwe a mitsempha yotupa.
Mchitidwe wofala kwambiri wa mitsempha yotchedwa disystrophy amadziwika kuti Duchenne muscular dystrophy. Amakhudza kwambiri anyamata, Duchenne muscular dystrophy amayamba chifukwa cha kusowa kwa dystrophin (mapuloteni omwe amathandiza kwambiri kuti asunge umphumphu). Duchenne dystrophy imaoneka pakati pa zaka zitatu ndi zisanu, ndipo nthawi zambiri amasiya odwala kuyenda ndi zaka 12.
Mitundu ina ya mitsempha ya m'mimba imaphatikizapo facioscapulohumeral muscular dystrophy (yomwe imadziwika ndi kufooka kwa minofu ya nkhope, mikono, miyendo, ndi mapewa ndi chifuwa) komanso myotonic muscular dystrophy (yomwe imatchulidwa ndi minofu yaitali, minofu, zovuta za mtima, ndi kusokonezeka kwa endocrine ).
Zizindikiro ndi Zizindikiro za Muscular Dystrophy
Zizindikiro za mitsempha ya m'mimba imasiyanasiyana malinga ndi mawonekedwe a mitsempha yotupa. Mwachitsanzo, zizindikiro za Duchenne muscular dystrophy zingaphatikizepo kuchedwa kwa kayendetsedwe ka magalimoto, kugwa kwafupipafupi, kufooka kumapeto kwenikweni, minofu yaikulu ya mwana wamphongo, ndi kufooka kwa chidziwitso. Matenda otchedwa myotonic muscular dystrophy, amachititsa kuti zizindikiro zikhale zofooka m'maso (kuphatikizapo manja ndi miyendo ndi minofu yomwe imakhudza kulankhula ndi kumeza), mimba, mavuto a kupuma, ndi zovuta za mtima pamene munthu akukula.
Kuchiza kwa Muscular Dystrophy
Chithandizo cha mitsempha ya mitsempha nthawi zambiri chimaphatikizanso mankhwala, kupuma , kulankhula, mankhwala opangira mankhwala, komanso opaleshoni ya mafupa .
Mankhwala ena amagwiritsidwanso ntchito pochizira matenda a mitsempha, kuphatikizapo corticosteroids (kuchepetsa kupwetekedwa kwa minofu), antiticulants (kuchepetsa kupweteka kwa thupi ndi zovuta zina), kuteteza thupi (kuchepetsa kuwonongeka kwa maselo a minofu akufa), ndi maantibayotiki (kuti amenyane ndi matenda opuma) .
Nthaŵi zina, odwala matenda a dystrophy angafunikire kuthandizira mpweya wabwino (kuteteza kupweteka kwa minofu) ndi / kapena pacemaker (kuchiza zovuta za mtima).
Kugwiritsa Ntchito Njira Zina Zochizira kwa Muscular Dystrophy
Ngati mukuganiza za kugwiritsa ntchito mtundu wina uliwonse wa mankhwala ochiritsira pa matenda a muscular dystrophy, nkofunika kukaonana ndi dokotala wanu (kapena mwana wa mwana wanu) musanayambe mankhwala. Kudziletsa kudziletsa ndi mankhwala osagwiritsidwa ntchito mosiyana ndi kupeŵa kapena kuchedwetsa chisamaliro choyenera kungakhale ndi zotsatira zoopsa.
> Zotsatira:
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> Nabukera SK, Romitti PA, Campbell KA, Meaney FJ, Caspers KM, Mathews KD, Hockett Sherlock SM, Puzhankara S, Cunniff C, Druschel CM, Pandya S, Matthews DJ, Ciafaloni E, Starnet M. "Kugwiritsa Ntchito Njira Zowonjezera Mankhwala a Amuna Ndi Duchenne kapena Becker Muscular Dystrophy. " J Mwana Neurol. 2011 Dec 7.
> National Institute of Neurological Disorders ndi Stroke. "Uthenga wa Muscular Dystrophy Page." November 14, 2011.
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