Matenda a Sweet ndi achilendo omwe amachititsa kupweteka kowawa, makamaka ndi malungo. Kuphulika kumatuluka makamaka pakhungu la manja, khosi, mutu ndi thunthu. Chifukwa cha Sweet's syndrome sichidziwika bwino, koma pali zochitika zambiri zomwe zimadziwika kuti zikuchitika.
Kwa anthu ena, zikuwoneka kuti zimayambitsidwa ndi matenda, kapena mwinamwake zimagwirizanitsidwa ndi matenda opweteka matumbo ndi mimba; mwa ena, zikhoza kugwirizanitsidwa ndi khansa, kawirikawiri imakhala yovuta kwambiri m'maganizo a khansa ya m'magazi; ena amakhalanso ndi mtundu wa Sweet's syndrome.
Matenda a Sweet akhoza kuthawa okha, koma kawirikawiri amachiritsidwa ndi mapiritsi a corticosteroid, monga prednisone. Mtundu wa Sweet's also known as acute febrile neutrophilic dermatosis kapena matenda a Gomm-Button.
Zizindikiro
Matenda a Sweet amadziwika ndi zizindikiro zotsatirazi:
- Fever
- Mphuno yaying'ono yofiira mmanja mwanu, khosi, mutu kapena thumba lomwe limakula msanga, kufalikira m'magulu opweteka mpaka masentimita
- Mphuno imatha kuwoneka mwadzidzidzi pambuyo pa malungo kapena kutentha kwapakati .
Mitundu ya Sweet's Syndrome
Chikhalidwechi chimadziwika ndi mitundu itatu:
Zakale
- Kawirikawiri kwa amayi a zaka zapakati pa 30 ndi 50
- KaƔirikaƔiri amayamba ndi matenda opuma opuma
- Mungagwirizane ndi matenda opweteka m'mimba ndi mimba
- Pafupifupi 1/3 mwa odwala ali ndi kachiwiri ka Sweet's syndrome
Malignancy-Associated
- Khalani mwa wina yemwe amadziwika kale ndi khansa
- Khalani mwa wina yemwe kansa yamagazi kapena chotupa cholimba sichinapezeke kale
- Ambiri amakhala okhudzana ndi mitsempha yambiri ya m'magazi , koma khansa zina zimatha, monga bere kapena colon
Zotsatira za mankhwala
- Ambiri amapezeka kwa odwala amene apatsidwa mankhwala opangira mphamvu ya granulocyte-coloni omwe amaperekedwa kuti apititse maselo oyera a magazi
- Komabe, mankhwala ena amathandizanso; Mankhwala okhudzana ndi Sweet's syndrome akuphatikizapo azathioprine, mankhwala ena opha tizilombo komanso mankhwala ena osakanikirana ndi mankhwala.
Kuyanjana Kunja kwa Khungu
Chifukwa cha Sweet's syndrome, chiwerengero chochepa, ndi zinthu zambiri zomwe zingatheke, sizinthu zonse zomwe zimagwirizanitsidwa ndi matendawa ndizochokera ku matenda enieni.
Izi zati, "Sweet's syndrome" imaganiza kuti ikhoza kuphatikizapo matenda ndi ziwalo zina, kuwonjezera pa khungu. Kuphatikizidwa kwa mafupa ndi mafupa kwatchulidwa, monga momwe kugwirizanirana kwa dongosolo lalikulu la mitsempha-"nthenda-yotsekemera matenda" yafotokozedwa. Maso, makutu, ndi kamwa zingasokonezedwenso. Mphuno yamtundu wofiira ikhoza kuwonjezeka kuchokera ku khutu lakunja, kulowa mu ngalande ndi eardrum. Maso akhoza kuthandizidwa, ndi kutupa, kufiira, ndi kutupa. Zilonda pa lirime, mkati mwa masaya ndi pa chingamu zingakhalepo. Kutupa ndi / kapena kukulitsa kwa ziwalo zamkati za mimba ndi chifuwa chafotokozedwa.
Zowopsa
Matenda a Sweet ndi osowa kwambiri, choncho zifukwa zake zowopsa sizinapangidwe bwino monga momwe zingakhalire ndi matenda ena. Kawirikawiri, amayi amakhala ndi vuto labwino kusiyana ndi amuna, ndipo ngakhale kuti akuluakulu komanso ana angathe kukhala ndi Sweet's syndrome, anthu a zaka zapakati pa 30 ndi 60 ndi omwe ali ndi zaka zambiri.
Kuonjezera apo, zikhalidwe zomwe zimatanthauzira mitundu yomwe ili pamwambazi zikhoza kuonedwa kuti ndizoopsa, kotero Sweet's syndrome nthawi zina imayanjanitsidwa ndi khansa, ikhoza kukhala yogwirizana ndi mankhwala ena, imatha kutsata matenda opuma (ndipo anthu ambiri amanena kuti ali ndi matenda a chimfine, monga zizindikiro zisanachitike) ndipo zingagwirizanenso ndi matenda opatsirana, omwe amachititsa matenda a Crohn ndi matenda a ulcerative.
Azimayi ena apanga vuto la Sweet while pregnancy.
Kudziwa
Matenda a Sweet akhoza kukayikira kapena kudziwika mwa kuyesa kuphulika, komabe, mayesero osiyanasiyana ndi ofunika nthawi zambiri kuti apange matenda ndi / kapena kutulutsa zifukwa zina.
Chitsanzo cha magazi anu chikhoza kutumizidwa ku labotori kuti mukayang'ane maselo akuluakulu achizungu ambiri komanso kukhalapo kwa matenda a magazi.
Khungu lachikopa, kapena kuchotsa khungu kakang'ono ka khungu lomwe lakhudzidwa kuti lifufuze pansi pa microscope, likhoza kuchitidwa. Matenda a Sweet amadziwika bwino: maselo otupa, omwe amakhala ozunguza magazi ambirimbiri a mtundu wa neutrophil, amalowa mkati ndipo amapezeka pamtunda wapamwamba wa khungu.
Zindikirani, opatsirana opatsirana angapangitse zofanana zomwe zimapezeka pakhungu, kotero zanenedwa kuti zingakhale zanzeru kukhala ndi zitsanzo zomwe zimayesedwa mabakiteriya, bowa, ndi mavairasi.
Zomwe zimaphatikizapo kafukufuku pa odwala omwe ali ndi matenda a Sweet ndi maselo oyera a m'magazi ndi ma neutrophils m'magazi ndi mlingo wokwera wa erythrocyte, kapena ESR. Izi zinati, kuwerengera kwa maselo oyera a magazi oyera sikuwonekera nthawi zonse kwa odwala onse omwe ali ndi vuto la biopsy-confirmed Sweet's.
Chithandizo
Matenda a Sweet akhoza kuthawa okha, popanda chithandizo, komabe mankhwala amathandiza ndipo amagwira ntchito mofulumira. Popanda kukanidwa, ziphuphu zimatha kwa milungu ingapo. Mankhwala omwe amagwiritsidwa ntchito pa Sweet's syndrome ndi corticosteroids . Ma oral corticosteroids, monga prednisone , angagwiritsidwe ntchito, makamaka ngati muli ndi malo ochepa chabe a khungu. Mankhwalawa ndi systemic, kutanthauza kuti amapita mu thupi lonse osati khungu chabe.
Mitundu ina ya steroids monga ma creams kapena mafuta opaka mafuta nthawi zina amagwiritsidwa ntchito pazitsamba zochepa, zochepa. Munthu amene ali ndi matenda a Sweet salola kuti corticosteroids ikhale yogwirizana kapena ali ndi zotsatira za mankhwala a corticosteroids nthawi yaitali, pali mankhwala omwe angagwiritsidwe ntchito monga dapsone, iodide ya potassium, kapena colchicine.
Odwala ndi Sweet's syndrome akhoza kukhala ndi mavuto chifukwa cha kulowerera khungu, zochitika za Sweet's syndrome, kapena zonse ziwiri. Mankhwala opha majeremusi angagwiritsidwe ntchito ngati zilonda za khungu zochokera ku chiwopsezo zili pachiopsezo kuti kachilombo ka kachilombo kaye kachiwiri.
Kusamala ku zochitika zilizonse zokhudzana ndi matenda zingakhale zofunikira kwambiri pa chithandizo cha Sweet's syndrome. Mwachitsanzo, zizindikiro zomwe zimagwirizanitsa ndi matenda nthawi zina zimachokera kuchipatala kapena kuchiza.
Mawu Ochokera
Mankhwala monga corticosteroids angapatseni mpumulo ku matenda, komabe kuganizira zinthu zomwe zikugwirizana nazo zingakhale zofunikira. Ngati muli ndi mtundu wa Sweet's syndrome, kamodzi kokha mankhwala osokoneza bongo atachotsedwa, matendawa, koma nthawi zonse, amawongolera komanso mwachangu.
Mwachiwonekere, si onse omwe ali ndi vuto la Sweet ali ndi khansara; ndipo, pakuphunzira ndi anthu 448 omwe ali ndi Sweet's syndrome, 21 peresenti yokha (kapena 96 peresenti 448) anapezeka kuti anali ndi malungo kapena chivundi cholimba. Chodziwitso, komabe, ndikuti Sweet's syndrome nthawi zina ikhoza kutsogolera kupezeka kwa khansara yosadziwika-komanso kuti kubwereza kwa matenda a Sweet's a malignancy kungasonyeze kubwerera kwa khansa.
> Zotsatira:
> Cohen PR. Sweet's syndrome - ndondomeko yambiri ya febrile neutrophilic dermatosis. Orphanet J Rare Dis. 2007; 2: 34. lembani: 10.1186 / 1750-1172-2-34.
> Hussein K, Nanda A, Al-Sabah H, Alsaleh QA. Matenda a Sweet (acute febrile neutrophilic dermatosis) ogwirizana ndi adenocarcinoma ya prostate ndi transitional cell carcinoma ya chikhodzodzo cha mkodzo. J Eur Acad Dermatol Venereol. 2005; 19: 597-599.
> Zokoma RD. Matenda a febrile neutrophilic dermatosis. Br J Dermatol. 1964; 76: 349-356. lembani: 10.1111 / j.1365-2133.1964.tb14541.x.