Kodi pali chinthu ngati maselo ofiira ambiri? Pamene anthu ambiri amaganiza za mavuto omwe ali ndi maselo ofiira a magazi, amaganiza za kuchepa kwa magazi , maselo ofiira a magazi ochepa, koma maselo ofiira ambiri angakhalenso vuto. Izi zimatchedwa polycythemia, kapena erythrocytosis. Pali kusiyana pakati pazinthu ziwiri koma nthawi zambiri zimagwiritsidwa ntchito mosiyana.
Vuto la Maselo Ofiira Amagazi Ambiri
Chifukwa chomwe mungaganize kuti ndibwino kuposa momwemo, polycythemia ingayambitse mavuto aakulu. Izi zimayambitsa magazi chifukwa tsopano pali maselo ochuluka omwe ali ndi madzi (otchedwa plasma). Mwazi uwu umakhala wovuta kuyenda m'mitsempha ya magazi ndipo ukhoza kubweretsa zikwapu, matenda a mtima, ziphuphu zamagazi kapena mpweya wamagazi (magazi mu mapapo).
Zizindikiro za Polycythemia
Zizindikiro za polycythemia ndizosavuta ndipo anthu ena alibe zizindikilo ndipo amapezeka pambuyo pa ntchito ya laboratory.
- Kufooka kapena chizungulire
- Kutopa kapena kutopa
- Mutu
- Kuwomba, nthawi zina pambuyo pa kusamba kapena kusamba
- Mavuto Ophatikizana, nthawi zambiri chimphona chachikulu
- Mimba Yamimba
- Kufiira kwa nkhope
Kudziwa
Polycythemia imadziwika ndi kuchuluka kwa magazi . Kuwerengera kwa maselo ofiira a m'magazi (otchedwa RBC), hemoglobin, ndi / kapena hematocrit ndi okwezeka. Ntchito yamagazi idzabwerezedwa kuti iwononge zolakwika za laboratory.
Ndikofunika kuzindikira zomwe zimachitika mosiyana ndi msinkhu komanso kugonana (pambuyo pa kutha msinkhu) ndikukhudza tanthauzo la polycythemia.
Ntchito zina zogwira ntchito zimagwiritsidwa ntchito kuti zitsimikizire ngati chidziwitso chingathe kudziwika. Izi zimaphatikizapo kuchuluka kwa mlingo wa oksijeni (omwe nthawi zambiri amatchedwa ng'ombe yamphongo) komanso kupanga mtima ndi mapapu (chifuwa cha X-ray, EKG, ndi echocardiogram) kuti athetse mphamvu za mpweya wabwino.
Erythropoietin mlingo, mahomoni obisika ndi impso omwe amalimbikitsa kupanga maselo ofiira, akhoza kuyeza. Msuzi wa aspirate ndi mafupa amatha kuchitidwa.
Zonsezi zikhoza kukhala zatsopano kwa inu. Ngati dokotala akuwagwiritsa ntchito, kapena ngati mutalandira lipoti la labwino ndipo mukuvutika kupeza chidziwitso, funsani thandizo. Kuchita kafukufuku wanu kungathandize, koma kukhala ndi mphunzitsi akufotokozerani inu ali ndi phindu lina: iwo adzafotokoza zomwe zotsatira zikutanthawuza motsutsana ndi inu makamaka.
Zimayambitsa
- Polycythemia vera : Ichi ndi chosowa kwambiri cha mafupa. Kawirikawiri, mumakhalanso ndi selo loyera la maselo oyera (leukocytosis) ndi kuchuluka kwa mapiritsi (thrombocytosis). Izi zikhoza kuyambitsidwa ndi kusintha kwa majini wotchedwa JAK2.
- Wokwatirana: Awa ndiwo malo obadwa nawo pamene thupi limapanga maselo ofiira ambiri kuposa momwe akuyembekezeredwa.
- Zinthu zomwe zimayambitsa mpweya wotsika m'magazi (hypoxia), monga:
- Matenda osokoneza bongo (COPD)
- Matenda a mtima
- Kugonana ndi mpweya
- Kuthamanga kwa magazi
- Mimba yotchedwa erythropoietin, monga:
- Hepatocellular carcinoma (khansa ya chiwindi)
- Renal cell carcinoma (khansa ya impso)
- Kutupa kwa adrenal glands
- Nthawi zina mphutsi mu impso
Ana obadwa kumene angakhalenso ndi polycythemia yomwe nthawi zambiri imakhudzana ndi
- Zinthu zomwe zimagwirizanitsidwa ndi mpweya wochepa mu utero
- Mphindi mpaka mapasa kuikidwa magazi: Mu chikhalidwe ichi, mapasa awiri amalandira magazi ochuluka kuchokera ku pulasitiki kusiyana ndi inayo.
Chithandizo
- Kuwunika: Ngati mankhwala osokoneza bongo, dokotala wanu akhoza kungokuonani
- Kuchiza kwa vuto lomwe likuchititsa polycythemia
- Phlebotomy: Magazi amachotsedwa pamtunda panthawi yeniyeni kuti athetse mavuto. Magazi amalowetsedwa ndi saline wamba (chimbudzi chomwe chimaperekedwa mu mitsempha).
- Hydroxyurea: Hydroxyurea, mankhwala am'thupi, angagwiritsidwe ntchito ngati phlebotomy silingaloledwe. Hydroxyurea ikhoza kuchepetsa kuchuluka kwa magazi: maselo oyera a magazi, maselo ofiira a magazi, ndi mapuloletsiti.
- Interferon-alpha: Interferon-alpha ingagwiritsidwe ntchito pofuna kulimbitsa chitetezo chanu cha mthupi kuti chiteteze kuwonjezereka kwa maselo ofiira a magazi.
- Aspirin: Aspirin ikhoza kugwiritsidwa ntchito kuchepetsa chiopsezo chotsekedwa. Aspirin imateteza mapiritsi kuti asatseke.
- Ruxolitinib: Ruxolitinib ingagwiritsidwe ntchito kwa odwala omwe ali ndi kusintha kwa JAK2 ndipo samalola kapena samayankha mankhwala a hydroxyurea.