SPS Zimayambitsa Mitundu Yopweteka ndi Mafupa
Matenda a munthu wodwala (omwe amatchedwanso Moersch-Woltmann syndrome) kapena SPS ndi matenda omwe amachititsa kuti misala ikhale yovuta kwambiri. Kafukufuku amasonyeza kuti matenda okhwima a munthu ndi matenda osokoneza bongo, ndipo anthu omwe ali ndi matenda nthawi zambiri amakhala ndi matenda omwe amadziwika nawo monga mtundu wa shuga 1 kapena thyroiditis .
Matenda a munthu wodwala amakhudza amuna ndi akazi ndipo angayambe pa msinkhu uliwonse, ngakhale kuti matendawa ali ochepa.
Sikudziwika bwino kuti ndi anthu angati omwe akuvutika nacho.
Zizindikiro za Munthu Wopweteka Syndrome
Zizindikiro za matenda okhwimitsa munthu angaphatikizepo:
- Kupsinjika kwa minofu mu thunthu ndi miyendo yomwe imabwera ndi kupita-izi zimayambitsa kuuma kwachisoni kapena kupweteka, chithunzi chowongolera chowongolera, ndi kuyenda mwendo wokhoma
- Minofu yambiri yammimba ndi miyendo pamene munthuyo akudabwa, kukhudzidwa, kukwiya, kapena kuda nkhawa
- Mzere wobwerera m'mbuyo (lordosis) ndi ziwalo zofooka m'thupi, patapita nthawi
- Kugwa pang'onopang'ono minofu yadzidzidzi (ingayambitse mavuto ena okhudzana ndi zina)
Kuzindikira kwa Munthu Wopweteka Syndrome
Zizindikiro zimasonyeza kuti akudwala matendawa. Komabe, chifukwa ndi matenda osadziwika bwino, mwina matendawa ndi Parkinson, matenda a multiple sclerosis , fibromyalgia , kapena matenda a maganizo.
Nthawi zina matendawa amatsimikiziridwa ndi kukhalapo kwa anti-GAD antibodies, kapena mitundu ina ya ma antibodies pamene matendawa amagwirizanitsidwa ndi khansa zina.
Komabe, 35 peresenti ya odwala omwe ali ndi matenda okhwima a munthu alibe mankhwala omwe amakhala nawo komanso alibe khansa.
Mayesero ena angapangidwe, monga hemoglobin A1C kuti ayang'ane matenda a shuga kapena mahomoni otulutsa chithokomiro (TSH) kuti ayang'ane chithokomiro. Kuyesedwa kwa minofu (electromyography kapena EMG) kungapangidwenso.
Kuchiza kwa Munthu Wopweteka Syndrome
Ngakhale palibe chithandizo cha matenda okhwima a munthu, pali mankhwala omwe alipo. Mankhwala monga azathioprine (Azasan), diazepam (Valium), gabapentin (Neurontin), tiagabine (Gabitril), kapena baclofen (Lioresal) angagwiritsidwe ntchito. Zizindikiro mwa omwe ali ndi khansa zowonjezereka zimatha kusintha pambuyo pa chotupacho chitachotsedwa ndipo chithandizo cha steroid chimaperekedwa. Kusinthanitsa kwa plasma (plasmapheresis) kumathandiza kuchepetsa zizindikiro mwa anthu ena, koma chithandizochi chimakhala chosungiratu kwa anthu omwe akuwopsya kupuma. Kwa ena, kuteteza immunoglobulin (IVIg) kumathandiza. Thandizo la thupi lingathandize kuthetsa zizindikiro zokhudzana ndi kuthamanga kwa mitsempha yaitali, koma zingathenso kuyambitsa minofu ya minofu. Corticosteroids ingathandizenso, ngakhale kuti ayenera kupatsidwa mosamala kwa anthu omwe ali ndi shuga.
Zotsatira:
"NINDS Munthu Wokhudzidwa ndi Tsamba la Chidziwitso." Kusokonezeka. 14 Feb 2007. National Institute of Neurological Disorders ndi Stroke. http://www.ninds.nih.gov/disorders/stiffperson/stiffperson.htm.
Rodgers-Neame, Nancy. "Munthu Wopweteka Syndrome." eMedicine. 20 Mar 2006. WebMD. http://www.emedicine.com/neuro/topic353.htm.
Mankhwala a antiantibodies a puloteni 128-kd syaptic m'mayi atatu omwe ali ndi matenda okhwima ndi khansa ya m'mawere. Foni; Limodzi; Chithunzi; Chithunzi; Tallini G; Fassetta G; Bates D; Cartlidge N; Bottazzo GF; Chojambula; et al. SO N Engl J Med 1993 Feb 25; 328 (8): 546-51
Kusagwirizana kwa ma autoantibodies mu vuto la munthu. AU Grimaldi LM; Nthumwi; Braghi S; Quattrini A; Furlan; Bosi E; Comi GSO Ann Neurol 1993 Jul; 34 (1): 57-64.
Steroid-omvera ndi okhudzidwa-munthu matenda okhwima: matenda ndi ma electrophysiological maphunziro a milandu iwiri. Foni; Cosi V; Zandrini C; Moglia ASO Ital J Neurol Sci 1988 Dec; 9 (6): 559-66.