Matenda a Zizindikiro Zosakanikirana
Matenda osokoneza bongo (MCTD) ndi matenda omwe amadzimadzimadzimodzinso ndi zizindikiro zina zitatu zomwe zimagwiritsidwa ntchito ndi matenda a mitsempha - njira yeniyeni ya lupus erythematosus , scleroderma , ndi polymyositis.
Chifukwa
Chifukwa cha MCTD sichikudziwika. Pafupifupi 80 peresenti ya anthu omwe ali ndi MCTD ndi akazi. Matendawa amakhudza anthu a zaka zapakati pa zisanu ndi zisanu ndi zisanu ndi zitatu (80) ali ndi zaka zambiri pakati pa achinyamata kapena anthu omwe ali ndi zaka makumi asanu ndi awiri (20).
Pakhoza kukhala ndi chigawo cha chibadwa koma sichibadwa mwachindunji.
Zizindikiro
Zizindikiro zoyambirira za matenda osokoneza ubongo zimakhala ngati zizindikiro zogwirizana ndi matenda ena othandizira kuti zikhale ndi matendawa ndipo zingaphatikizepo izi:
- Kutopa
- Kupweteka kwa minofu kapena kufooka
- Chisoni chophatikizana
- Kutentha thupi kwambiri
- Zochitika za Raynaud
Zizindikiro zochepa zomwe zimagwirizanitsidwa ndi MCTD zimaphatikizapo kwambiri polymyositis (makamaka kumakhudza mapewa ndi manja apamwamba), kupweteka kwa nyamakazi, aseptic meningitis, myelitis, kupweteka kwala zala, zala, kutentha kwa malungo, kupweteka kwa m'mimba, ubongo wa m'mimba, vuto lomeza, kupuma pang'ono, ndi kutaya kwa kumva. Mapapu amakhudzidwa mpaka 75 peresenti ya anthu omwe ali ndi MCTD. Pafupifupi 25 peresenti ya odwala omwe ali ndi MCTD ali ndi vuto la impso.
Kudziwa
Kuzindikira matenda osokoneza ubongo kungakhale kovuta kwambiri. Makhalidwe atatuwa-systemic lupus erythematosus, scleroderma, ndi polymyositis-kawirikawiri samachitika panthawi yomweyo.
M'malo mwake, nthawi zambiri amatha kukhala limodzi pambuyo pake.
Komabe pali zifukwa zinayi zomwe zingapangitse kuti munthu azindikire kuti ali ndi matenda a MCTD m'malo modwala matenda enaake:
- Kukula kwakukulu kwa anti-U1 RNP (ribonucleoprotein) m'magazi
- Kusakhala ndi nkhani zina zomwe zimagwirizanitsidwa ndi systemic lupus erythematosus, monga mavuto a impso ndi mavuto akuluakulu a mitsempha
- Matenda amphamvu komanso mapiritsi othamanga kwambiri (osadziwika mu systemic lupus kapena scleroderma)
- Zochitika za Raynaud, ndi manja otupa (osagwirizana ndi systemic lupus)
Ngakhale kuti kukhalapo kwa anti-U1 RNP ndi chinthu chodziwika kwambiri chomwe chimapangitsa kuti matenda a MCTD adziwe, kukhalapo kwa wodwala m'magazi kungathe kutsogolera zizindikiro.
Chithandizo
Chithandizo cha matenda osokoneza bongo amachititsa kuti zizindikiro ziziyenda bwino komanso kuyendetsa zotsatira zoopsa za matendawa, monga kukhudza thupi. Mwachitsanzo, kupatsirana kwapopeni kumafunika kuchiritsidwa ndi mankhwala osokoneza bongo. Zizindikiro zotupa zikhoza kukhala zochepa mpaka zovuta, ndipo chithandizochi chiyenera kusankhidwa chifukwa cha kuuma. Kutupa kwakukulu kochepa, NSAID kapena corticosteroids ya dozi yaing'ono ingaperekedwe. Kutentha pang'ono kumakhala kofunika kwambiri kwa corticosteroids. Ngati pali mbali yothandizira thupi, zimakhala zovuta kuti munthu asatengedwe.
Chiwonetsero
Ngakhalenso ndi matenda oyenerera komanso ochiritsira oyenera, zimavuta kupanga. Momwe wodwalayo amachitira zimatengera kuti ndi ziwalo ziti zomwe zimakhudzidwa, kuuma kwa kutupa, ndi kukula kwa matendawa. Malingana ndi Cleveland Clinic, anthu 80 peresenti amakhalabe osachepera zaka 10 atapezeka kuti ali ndi MCTD.
Kuvomereza kwa MCTD kumawonjezereka kwa odwala omwe ali ndi makhalidwe omwe amamangiriridwa ku scleroderma kapena polymyositis.
Ndikofunika kuzindikira kuti pangakhale nthawi yotalikira yomwe ilibe chizindikiro, ngakhale popanda mankhwala kwa MCTD.
> Zotsatira:
> Bennett R. Anti-U1 RNP Matenda a M'magulu Okhudzana ndi Matenda Aakulu. Zaposachedwa.
> Firestein GS, Kelley WN. Kelleys Textbook of Rheumatology . Philadelphia, PA: Elsevier / Saunders; 2013.
> Gunnarsson R, Hetlevik SO, Lilleby V, Molberg Ø. Matenda osokoneza bongo. Ntchito Yabwino & Kafukufuku Wachipatala . 2016; 30 (1): 95-111. onetsani: 10.1016 / j.berh.2016.03.002.
> Matenda Ogwedezeka Osakaniza. Clinical Cleveland.