Matendawa Nthawi Zina Amadandaula Amatchedwa "Matenda a Chimayi"
Kodi matenda a Creutzfeldt-Jakob (CJD) ndi chiyani?
Creutzfeldt-Jakob (adatchula kuti CROYZ-anamva YAH-cob) matenda ndi matenda osadziwika bwino a ubongo omwe amakhudza munthu mmodzi mwa milioni. Ndi chimodzi mwa mitundu yambiri ya matenda a prion.
CJD ingathenso kutchulidwa kuti matenda opatsirana otchedwa spongiform encephalopathy, vCJD, ndi Jacob-Creutzfeldt matenda.
Kukula
United States ili ndi milandu pafupifupi 200 mpaka 300 pa chaka.
Avereji ya zaka zoyambira ali ndi zaka 60.
Zizindikiro za CJD
Zizindikiro zoyambirira kwambiri zimaphatikizapo kuchotsa maganizo, kutengeka kwa maganizo ndi kusasamala anthu kapena zochitika. Mwamsanga, zizindikiro zina zimaphatikizapo, kuphatikizapo mavuto a kukumbukira , kusintha kwa khalidwe, kusagwirizana bwino, kuyenda mosasinthasintha komanso kuwonongeka.
Pamene matendawa akupitiliza kukula, anthu omwe ali ndi CJD akhoza kukhala ndi malingaliro , kusokonezeka maganizo, kusokonezeka kwa kayendetsedwe ka kayendetsedwe kake, kayendetsedwe kadzidzidzimadzi, manja ndi miyendo yofooka kwambiri, kusowa mphamvu kumeza ndi kulankhula, komanso kufooka kwa maganizo. Pomalizira pake, munthuyo akhoza kulowa mu coma.
Zigawo za CJD
- Zosavuta
CJD imakhala pafupifupi 85 peresenti ya matenda onsewa. Zomwe zimatanthauza kuti palibe chifukwa chodziwikiratu.
- Wokonzeka
Malingana ndi National Institute of Neurological Disorders ndi Stroke, milandu imene anabadwa imakhala pafupifupi 5% mpaka 10 peresenti. The prion protein gene imakhala yachilendo kwa anthu okhala ndi mitundu yonse ya CJD. Kwa odwala omwe ali ndi mawonekedwe a banja, kusintha kwasintha kwapezeka mu prion protein gene yomwe imayambitsa mapuloteni osowa. Anthuwa nthawi zambiri amasonyeza mbiri ya banja la matenda a prion.
- Kupezeka
Pali mitundu itatu ya CJD yomwe inapezedwa. Izi zikuphatikizapo:
- Iatrogenic
Izi zikutanthauza CJD yomwe imagwiritsidwa ntchito kudzera mu njira zamankhwala, monga zida zosagwiritsidwa ntchito kapena zizindikiro za mthupi. - Kuru
CJD ikhoza kupezedwa kudzera mu chiwonongeko, chomwe chimatchedwa Kuru. Izi zinayambira zaka za m'ma 1950, pamene anthu a mtundu wina wa ku Papua, New Guinea anayamba kukhala ndi CJD chifukwa amaliro awo anali amayi ndi ana omwe amadya ubongo wa womwalirayo. Pamene chizolowezicho chaleka, milandu ya CJD yatsika, koma izi zatenga zaka zingapo chifukwa nthawi yowonjezera ya CJD ikuwoneka ngati yayitali zaka 40.
- Zosiyana
CJD yochuluka imalingaliridwa kuti imayamba chifukwa cha kudya nyama yowonongeka ndipo ikhoza kupezeka kwa achinyamata, ndi zaka zapakati pa kuyamba kumene kumachitika pa 28. Izi nthawi zambiri zimatchedwa mliri wamisala kapena bovine spongiform encephalopathy. Matenda a ng ombe amapezeka mumng'ombe; pamene imafalitsidwa kwa anthu, imatchedwa CJD yosiyana. Mtundu uwu wa CJD ndi wochepa kwambiri; milandu itatu yokha yalembedwa ku United States, ndi awiri mwa anthu omwe kale anali kunja kwa dzikolo.
Kuzindikira CJD
Mofanana ndi matenda ena a ubongo, palibe mayeso osavuta kuti azindikire CJD. Cholinga cha dokotala choyamba ndicho kuthetsa zovuta zina zomwe zingayambitse matenda a maganizo, makamaka chifukwa chazifukwa zina zimayambitsa matenda a 'dementia', monga vuto lachilengedwe la hydrocephalus ndi kusowa kwa vitamini B12 .
Mayesero monga matepi a msana , EEG , CT , ndi MRI angagwiritsidwe ntchito kuti athe kupeza mwayi wa CJD.
Kuti atsimikizire kuti akudziƔa, akatswiri ochita opaleshoni angathe kuchita zinthu mwachangu pochotsa ubongo wambiri kuti uwayese. Njira ina ndiyomwe imayendetsa pambuyo pomwalira. Ndi chiwopsezo ndi autopsy, pali chiopsezo kuti dokotalayo atenge kachilombo ka CJD pamene akugwira minofu ya ubongo. Mu CJD yosiyana, pakhala milandu yotsimikiziridwa pambuyo pochotsedwa ndi kuyesedwa kwa matani a munthu.
Ndikofunika kwambiri kuti pakhale ndondomeko zoyenera kutsata panthawiyi.
Kodi CJD Imasiyana Bwanji ndi Alzheimer's?
Kupititsa patsogolo kwa CJD kuli mofulumira kuposa matenda a Alzheimer's . Anthu omwe ali ndi CJD nthawi zambiri amafa masabata angapo mpaka chaka chimodzi. Mu Alzheimer's, kawirikawiri kuchepa kwapang'onopang'ono pakapita zaka zingapo.
Kuchiza kwa CJD
Pakalipano, palibe mankhwala a CJD, ngakhale kuti zizindikiro zina zingathetsedwe ndi mankhwala. Cholinga ndi kupereka chitonthozo ndi chitonthozo. Kafukufuku akupitiriza kuchitidwa pofuna kudziwa zomwe zimayambitsa matenda komanso mankhwala ochiza matenda a CJD.
Zotsatira:
ADAM Creutzfeldt-Jakob Matenda.Adafika pa February 10, 2012. http://adam.about.net/encyclopedia/infectiousdiseases/Creutzfeldt-Jakob-disease.htm
Alzheimer's Association. Matenda a Creutzfeldt-Jakob. Inapezeka pa February 10, 2012. http://www.alz.org/alzheimers_disease_creutzfeldt_Jakob_disease.asp
Creutzfeldt-Jakob Disease Foundation, Inc. Mndandanda wa Zolemba za CJD. Inapezeka pa February 10, 2012. http://www.cjdfoundation.org/fact.html
Creutzfeldt-Jakob Disease Foundation, Inc. Matenda a Creutzfeldt-Jakob ndi zina za Prion Matenda. Inapezeka pa February 10, 2012. http://www.cjdfoundation.org/pamphlets.html
Bungwe la World Health Organization. Matenda a Creutzfeldt-Jakob. Inapezeka pa February 10, 2012. http://www.who.int/topics/creutzfeldtjakob_syndrome/en/