Aplasia cutis congenita ndi matenda a khungu omwe amachititsa kuti ana azibadwa ndi khungu losowa. Aplasia cutis congenita ikhoza kuchitika palokha kapena ngati chizindikiro cha matenda ena monga matenda a Johanson-Blizzard ndi Adams-Oliver. Aplasia cutis congenita akhoza kulandira kapena kuchitika popanda mbiri ya banja la chikhalidwecho. Matendawa amakhudza amuna ndi akazi a mafuko onse ndipo amapezeka pafupifupi 1 peresenti 10,000.
Ochita kafukufuku samadziwa kuti majeremusi amachititsa kuti apasia cutis congenita, koma akuganiza kuti majini omwe amakhudza khungu angasinthe. Nthawi zina, vutoli lingayambidwe chifukwa chokhala ndi methimazole, mankhwala omwe amagwiritsidwa ntchito pochiza hyperthyroidism . Zilombo zina zimayambanso chifukwa cha kachilombo kapena kuvulaza mwana pamene ali ndi mimba. Ngati vutoli liloledwa , nthawi zambiri limadutsa ndi kholo limodzi.
Zizindikiro ndi Zizindikiro
Mwana yemwe wabadwa ndi mabala oundana a congenita sadzasowa khungu, makamaka pa scalp (70 peresenti ya anthu). Zosangwanika zoperewera zimatha kuchitika pamtengo, mikono, kapena miyendo. Ana ambiri amakhala ndi khungu limodzi lokha; Komabe, zizindikiro zambiri zingatheke. Malo okhudzidwawo amakhala odzazidwa ndi kachigawo kakang'ono kofiira, kamene kamveketsedwa, ndipo sichiwotchedwa. Malo otseguka angawoneke ngati chilonda kapena chilonda chotseguka. Nthawi zina chikopa chosowa chimachiza mwana asanabadwe.
Chigamba chosowa nthawi zambiri chimakhala chozungulira koma chikhonza kukhala chozungulira, chophatikizapo, kapena chokhala ndi nyenyezi. Chigambachi ndi chachikulu bwanji, chimasiyana.
Ngati aplasia cutis congenita ikupezeka pamphuno, pangakhale chilema cha gaga pansi pa chosowa chosowa. Pankhaniyi, nthawi zambiri pamakhala tsitsi lopotoka pozungulira patch, yomwe imadziwika ngati chizindikiro cha tsitsi la tsitsi.
Ngati fupa lasokonezeka, pali chiopsezo chowonjezeka cha matenda. Ngati fupa lathyoledwa kwambiri, chophimba cha ubongo chikhoza kufotokozedwa ndipo chiopsezo cha magazi chiwonjezeka.
Kupeza Kuzindikira
Aplasia cutis congenita amapezeka chifukwa cha khungu la khanda. Ziphuphu zingathe kuzindikiridwa atangobereka kumene. Ngati chigambachi chisanachiritsidwe mwana asanabadwe, tsitsi silidzasowa kumalo omwe akukhudzidwa. Palibe mayesero apadera a ma laboratory omwe amafunika kuti azindikire mkhalidwewo. Ziphuphu zazikulu kwambiri zamapiko, makamaka omwe ali ndi chizindikiro cha tsitsi la tsitsi, ziyenera kufufuzidwa chifukwa chotheka mitsempha kapena zofewa.
Chithandizo
Kawirikawiri, mankhwala okhawo omwe amafunika kuti aplasia cutis congenital ndi kuyeretsa bwino dera lomwe likukhudzidwa ndi kugwiritsa ntchito siliva sulfadiazine kuti tipewe kutseka. Malo ambiri omwe amakhudzidwa amadzichiritsa okha patatha milungu ingapo, zomwe zimapangitsa kuti azikhala ndi tsitsi lopanda tsitsi. Zofooka zazing'ono zazing'ono zimatchulidwanso paokha m'chaka choyamba cha moyo. Opaleshoni ikhoza kupewedwa kupatula ngati malo omwe akusowa pakhungu ndi aakulu, kapena mbali zingapo za scalp zimakhudzidwa.
Zotsatira:
Crowe, M. (2005). Aplasia cutis congenita. eMedicine
National Organisation for Disorder Disorders. Aplasia Cutis Congenita