Gulusi 6 Kuperewera kwa Phosphate Dehydrogenase (G6PD) ndi mtundu wochuluka wa hemolytic anemia , mawonekedwe a kuchepa kwa magazi omwe amapezeka pamene maselo ofiira amagawanika mofulumira kuposa momwe amachitira (awa amatchedwa hemolysis ). Mu kulephera kwa G6PD izi zimachitika chifukwa mumapanga kuchuluka kwa G6PD, mavitamini omwe amateteza selo lofiira m'magazi kuwonongeka. Mwamwayi, anthu ambiri omwe ali ndi vuto la G6PD alibe mavuto tsiku ndi tsiku. Komabe, pali mankhwala kapena zakudya zina zomwe zimawonjezera kuchuluka kwa maselo ofiira a magazi. Tiyeni tiwone zinthu zina zomwe zingayambitse mavuto m'magazi awa.
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MaantibayotikiAnthu omwe ali ndi vuto la G6PD amatha kulekerera kwambiri mankhwala opha tizilombo koma ayenera kudziwa ochepa omwe angasankhe kusokonezeka kwa maselo ofiira a magazi omwe amachititsa kuti magazi asapitirire kuchepa kwa magazi. Mankhwala oletsa antibiotics omwe amatchedwa "sulfa" ayenera kupeŵa. Maantibayotiki awa amagwiritsidwa ntchito pochizira matenda a khungu kapena chikhodzodzo. Mtundu wambiri wa maantibayotiki umakhala ndi maina a Septra kapena Bactrim (sulfamethoxazole-trimethoprim).
Mankhwala a "quinolone" ayenera kupewedwanso. Matenda awiri omwe amapezeka m'gululi ndi Cipro (ciprofloxacin) ndi Levaquin (levofloxacin). Maantibayotiki awa amagwiritsidwa ntchito kwambiri kwa akuluakulu kuti athetse matenda opatsirana m'makina ndi chibayo. Maantibayotiki ena omwe ayenera kupewedwa ndi nitrofurantoin ndi dapsone.
Mwamwayi, pali mankhwala ambiri omwe anthu omwe ali ndi vuto la G6PD angathe kuteteza. Onetsetsani kuti mukambirane ndi dokotala wanu ngati muli ndi vuto la G6PD ndipo mukufuna mankhwala oletsa maantibayotiki.
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Mankhwala a MalungoPrimaquine, mankhwala omwe amachiza kapena kuteteza malungo , angayambitse vuto la hemolytic kwa anthu omwe ali ndi vuto la G6PD. Chifukwa cha vutoli, ndibwino kuti anthu ayesedwe kuti asapitirize kupeza G6PD asanayambe kutenga primaquine. Izi zimaphatikizapo kuyamwitsa ana omwe amayi awo amatenga primaquine. Mwamwayi, mankhwala ena ochiza malungo amalekereredwa ndi anthu ambiri okhala ndi vuto la G6PD.
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Mankhwala Operekedwa mu Chithandizo cha KhansaRasburicase ndi mankhwala ogwiritsira ntchito tumori lysis syndrome, vuto lachipatala la khansa ya hematologic monga khansa ya m'magazi, sayenera kugwiritsidwa ntchito kwa anthu okhala ndi vuto la G6PD. Chifukwa cha chiopsezo ichi, ndibwino kuti anthu ayesedwe asanalandire rasburicase. Mofananamo, doxorubicin, mtundu wa mankhwala a chemotherapy omwe amagwiritsidwa ntchito pochizira mitundu yambiri ya khansa, ikhoza kuyambitsa kusungunuka kwa maselo ofiira mwa anthu omwe ali ndi mtundu wina wa kusowa kwa G6PD.
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AspirinAspirin, omwe amagwiritsidwa ntchito popweteka kapena kutupa, ayenera kupeŵa. Anthu ena amatenga aspirin tsiku lililonse ngati gawo la mankhwala awo. Pofuna kupewa aspirin, ndi bwino kukumbukira kuti imapezeka m'magulu ambiri monga Anacin, Bufferin, Ecotrin, Excedrin, BC Powders ndi Goody's Powders. Ikupezeka mu Pepto-Bismol. Kawirikawiri zina pa kupweteka kwapiritsi kumachepetsa monga acetaminophen kapena ibuprofen amalekereredwa popanda nkhani.
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MothballsInde, anthu adagwiritsabe ntchito mothballs. Mothballs ikhoza kukhala ndi mankhwala otchedwa naphthalene omwe angayambitse hemolysis mwa anthu omwe ali ndi vuto la G6PD. Nafthalene ingapezedwe mu fumigants, makamaka omwe ankasunga njoka. Naphthalene ndi mpweya woperekedwa ndi mankhwalawa kotero kuti chiwonongeko chikhoza kubwera kuchokera pakuwombera mpweya kapena kuwatsitsa.
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HennaPali zochitika zina zofalitsidwa zosonyeza kuti henna (kugwiritsidwa ntchito kwa zojambula zosakhalitsa kapena ubweya wa tsitsi) zakhala zikuyambitsa mavuto a anthu omwe ali ndi vuto la G6PD. Ana omwe ali ndi zaka zosaposa miyezi iwiri amawoneka kuti ndi omwe amapezeka kwambiri.
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Nyemba za FavaKulephera kwa G6PD kumatchedwanso favism; makamaka mitundu yoopsa kwambiri ya kusowa kwa G6PD. Izi ndi chifukwa kuyamwa kwa nyemba za nyemba (zomwe zimadziwika kuti nyemba zazikulu) zingayambitse zida za hemolytic kwa odwala omwe ali ndi vuto la G6PD. Ena amanena kuti masamba onse (monga nandolo, mphodza, kapena mapeyala) amapewa, koma ngati izi sizikusoweka sizidziwika.
Mawu Ochokera
Ngati muli ndi vuto la G6PD, sizikutanthauza kuti simungathe kumwa mankhwala. Muyenera kudziwa za mankhwala omwe amapezeka kuti mutha kupewa. Iyi si mndandanda wathunthu wa zinthu zomwe anthu omwe ali ndi vuto la G6PD ayenera kupeŵa. Palinso mankhwala ena omwe amachititsa kuti maselo ofiira aphungu apangidwe ngati ali ndi mlingo waukulu. Zina zimangoyambitsa mavuto m'mabuku ena a G6PD. Onetsetsani kuti mukukambirana za mankhwala anu onse ndi dokotala wanu kuti mutsimikizire kuti sakutsutsana ndi anthu omwe ali ndi vuto la G6PD.> Chitsime:
> Luzaatto L ndi Poggi V. Gulukosi-6-Phosphate Dehydrogenase Deficiency. Mu: Orkin SH, Fisher DE, Ginsburg D, Yang'anani AT, Lux SE ndi Nathan DG (Eds). Hematology ndi Oncology ya Child and Childhood (8th ed). Philadelphia: Elsevier.