Mondini Syndrome Amayambitsa ndi Chithandizo

Chifukwa Chochepa Chodziwika cha Kutaya Kumva

Matenda a Mondini, omwe amadziwikanso kuti Mondini dysplasia kapena malonda a Mondini, amafotokoza momwe chimbudzicho sichidzatha, ndi kutembenukira kamodzi ndi hafu kokha m'malo mwa maulendo awiri ndi theka. Chikhalidwecho chinayamba kufotokozedwa m'chaka cha 1791 ndi dokotala Carlo Mondini m'nkhani yomwe ili ndi mutu wakuti "The Anatomic Section of a Boy Born Blind." Kusindikizidwa kuchokera ku Latin yoyambirira ya nkhaniyi kunasindikizidwa mu 1997.

Nkhani yoyambirira ya Carlo Mondini inali ndi tsatanetsatane yeniyeni ya malformation yomwe imatchedwa dzina lake. Kwa zaka zambiri, madokotala ena agwiritsira ntchito mawuwa pofotokoza zinthu zina zosaoneka bwino. Pokukambirana za malingaliro a Mondini, ndikofunikira kuti tifotokoze momveka bwino za nkhumba ndi zinyumba zina zamkati monga dzina lakuti 'Mondini' lingasokoneze.

Zimayambitsa

Izi ndi zobereka (pakuberekera) chifukwa cha kuchepa kwa kumva. Malinga a malingaliro a Mondini amapezeka pamene pali chisokonezo pakukula kwa khutu lamkati mkati mwa sabata lachisanu ndi chiwiri la kugonana. Izi zingakhudze imodzi kapena makutu onse awiri ndipo ingakhale yopatulidwa kapena imachitika ndi ziphuphu zina zakumutu kapena syndromes. Zizindikiro zomwe zimadziwika kuti zimagwirizanitsidwa ndi malingaliro a Mondini zikuphatikizapo Pendred Syndrome, DiGeorge Syndrome, Klippel Feil Syndrome, Fountain Syndrome, Wildervanck Syndrome, MATENDA OCHITIKA, ndi zina zotero za chromosomal.

Pali zifukwa zomwe malingaliro a Mondini adagwirizanitsidwa ndi autosomal komanso ma autosomal olowa cholowa maonekedwe komanso kukhala yekha.

Kudziwa

Kusanthula kwa malingaliro a Mondini kumapangidwa ndi maphunziro a mafilimu, monga njira zapamwamba zogwiritsira ntchito mafupa a panthawi.

Kumva Kutaya ndi Chithandizo

Kutaya kwakumva komwe kumakhudzana ndi kusintha kwa Mondini kumasiyana, ngakhale kuti nthawi zambiri kumakhala kovuta. Zida zothandizira zimalimbikitsidwa pakakhala zokhutira zokwanira zokhudzana ndi kumva. Nthawi zina zothandizira kumva sizigwira ntchito, cochlear implantation yachitidwa bwino.

Mfundo Zina

Anthu omwe ali ndi malimidwe a Mondini akhoza kukhala pachiopsezo chachikulu cha meningitis. Malformation angapangitse malo ovuta kulowa mmadzi ozungulira ubongo ndi msana. Nthawi zina pakhala zigawo zambiri (kapena zobwerezabwereza) za matenda a meningitis, opaleshoni yotseka mfundoyi ingasonyezedwe.

Malingaliro a Mondini angasokonezenso kayendedwe kabwino ka khutu lamkati. Ana omwe ali ndi malimidwe a Mondini angasonyeze kuchedwa kwachitukuko m'magalimoto awo chifukwa cha kuchepa kwa mavoti ku ubongo wawo. Nthawi zina, zinthu zolimbitsa thupi sizikhoza kuwonekera kufikira munthu wamkulu.

> Zotsatira:

> Hain, T (2012). Mondini ndi Michel Malingaliro a khutu lamkati. Chizungulire ndi Kusamala.

> Taonani, W (1999). Kodi 'Mondini' ndi Dzina Lotani? American Journal of Neuroradiology.

> Mondini C. Minor ntchito ya Carlo > Mondini: > Chigawo cha anatomic cha mnyamata wobadwa wosamva. Am J Otol 1997; 18: 288-293

> Mondini Dysplasia (2012). Ofesi Yofufuza Zachilombo.