Matenda a Hirschsprung ndi omwe amachititsa kuti m'mimba asatuluke kapena kuti asokonezeke.
Matenda a Hirschsprung
Matenda a Hirschsprung ndi achilendo, omwe amapezeka pafupifupi 1 pa 5,000 alionse.
Zimayambitsidwa chifukwa cha kusowa kwa maselo a ganglion (maselo a mitsempha) kumapeto kwa colon ndi rectum. Kawirikawiri peristalsis amafuna maselo a gangliyoni, kotero popanda iwo, simungatengere mapangidwe ofanana ndi matumbo a m'matumbo omwe amasuntha zinthu motsatira, kuwapangitsa kuti alowe mgwirizano ndi kutseka chigawo cha chitukukocho.
Izi zimabweretsa kuvomereza, chomwe ndi chizindikiro choyamba cha matendawa.
Matenda a Hirschsprung
Ana obadwa kumene amatha kupitako matumbo awo oyambirira (black tarry meconium) mkati mwa maola makumi awiri ndi anai oyambirira a moyo.
Ambiri mwa ana omwe ali ndi matenda a Hirschsprung adzachedwa kuchepetsa meconium. Ena amatha kudzimbidwa kosatha m'mwezi woyamba wa moyo. Njira iliyonse, ikhoza kutsogolera m'mimba, ndi zizindikilo zambiri, kuphatikizapo:
- kusungidwa m'mimba
- kusanza, komwe kungakhale kopanda pake
- kudya moperewera
- kulemera kolemera
Kuyeza kwa Matenda a Hirschsprung
Kuyezetsa kumene kungatheke kuti apeze matenda a Hirschsprung ndipo akuphatikizapo:
- x-rays, zomwe zingasonyeze kusokonezeka kwa m'mimba komanso kutayika kwa mpweya ndi mpweya mu rectum
- a barium enema, omwe angasonyeze malo otha kusintha kapena malo omwe ali pakati pa malo oyenera ndi malo ovuta omwe akukhudzidwa ndi kusowa maselo a ganglion
- manometry, chiyeso chomwe chimayesa kuthamanga kwa anal sphincter mkati mwa rectum
Pofuna kutsimikizira kuti matendawa ndi otani, chiwerengero cha rectal biopsy chachitika, chomwe chiyenera kusonyeza kuti palibenso maselo a ganglion kumapeto kwa colon ndi rectum.
Kuyesera kukayikira kwa Hirschsprung kawirikawiri kumayambira ndi enam barium.
Ngati barium enema ndi yachibadwa, ndiye kuti mwanayo ali ndi Hirschsprung. Ana omwe ali ndi enema osumalidwa bwino kapena omwe amalephera kuchipatala nthawi zonse kuti adziwe kuvomeredwa ayenera kukhala ndi kachilombo koyambitsa.
Matenda a Hirschsprung
Chithandizo cha matenda a Hirschsprung ndi kukonzanso opaleshoni, yomwe imakhala yoyamba kupanga colostomy ndiyeno kenako kuchotsa mbali ya coloni popanda maselo a ganglion ndikugwirizanitsa ziwalo zathanzi pamodzi.
Nthawi zina n'zotheka kuchita zokopa zokhazokha kapena ngakhale kuchita opaleshoni laparoscopically.
Mtundu wokonza opaleshoni ungadalire pazochitika za mwana wanu. Mwachitsanzo, ana ena amadwala kwambiri akayamba kupeza opaleshoni imodzi.
Zimene Mukuyenera Kudziwa Zokhudza Matenda a Hirschsprung
Zinthu zina zoti mudziwe za matenda a Hirschsprung ndizo:
- amatchedwanso congenital aganglionic megacolon
- Ndizofala kwambiri kwa anyamata
- Ikhoza kugwirizanitsidwa ndi Down syndrome , Waardenburg syndrome, neurofibromatosis, ndi syndromes zina ndipo amaganiza kuti zimayambitsidwa ndi kusintha kwa majini osiyanasiyana
- ngakhale kuti nthawi zambiri matenda a ana akhanda amawoneka, nthawi zina Hirschsprung akudandaula kuti ali ndi ana okalamba omwe ali ndi chidziwitso chokhazikika, makamaka ngati sakanakhala ndi matumbo okhaokha popanda kuthandizira mavitamini awo okhaokha popanda kuthandizidwa ndi mankhwala osowa kapena osowa kapena osakhala ndi chidziwitso chochuluka mpaka atamaliza kuyamwa kuyamwa.
- anatchulidwa kuti Harald Hirschsprung, katswiri wa matenda opatsirana amene anafotokoza ana awiri ali ndi matendawa mu 1887 Copenhagen
Gastroenterologist ndi dokotala wa odwala angapindule pozindikira ndi kuchiza mwana wanu ndi matenda a Hirschsprung.
> Zotsatira:
Matenda a Hirschsprung. Matenda a m'mimba ndi Matenda a Chiwindi (Kuyambira Chachinayi), 2011, masamba 576-582.e2
Matenda a Hirschsprung. Opaleshoni ya Ana (Chisindikizo cha Seventh), 2012, masamba 1265-1278