Zina mwachinsinsi, sarcoidosis ndi matenda osadziwika chifukwa - ngakhale chitetezo cha mthupi komanso maonekedwe a munthu amakhulupirira kuti ndi ofunika. Sarcoidosis, nthawi zina imangotchedwa sarcoid, imayambitsa njira yotupa yomwe imawoneka pansi pa microscope ndipo ingakhudze ziwalo zosiyana za thupi. Sarcoidosis ikhoza kuthana ndi chiwalo chilichonse, koma zikutheka kuti zimakhudza malo awa:
- Maungulo
- Khungu
- Zilonda zam'mimba - makamaka zam'mimba m'chifuwa
Sarcoidosis imadziwikanso chifukwa chakuti imatha kukhudza maso ndi chiwindi. Zosavuta, mtima ndi ubongo zingakhudzidwe, zomwe zimabweretsa mavuto aakulu.
Malingaliro a maselo ndi matenda, chizindikiro cha sarcoidosis chimatchedwa granuloma. Granulomas ndi magulu a maselo omwe, pansi pa microscope, amawoneka ofanana kwambiri ndi omwe thupi limagwiritsa ntchito polimbana ndi matenda monga chifuwa chachikulu.
Sikuti aliyense amene ali ndi sarcoidosis amafuna chithandizo, ndipo nthawi zambiri amatha popanda mankhwala, koma nthawi zina amatha kudwala matenda oopsa. Ngati chiwalo chimakhudzidwa, mwachitsanzo, mankhwala osiyanasiyana omwe amagwiritsidwa ntchito kuti athetse chitetezo cha mthupi angagwiritsidwe ntchito.
Zizindikiro zingagwirizane ndi ziwalo zomwe zimayambitsa matendawa, kapena zikhoza kukhala ndi zizindikiro zowonjezera monga kutopa, kutentha thupi, kutupa kwa mitsempha yam'mimba, ndi kutaya thupi . Kulowa m'mimba kumakhala kofala kwambiri ndipo zizindikiro zimaphatikizapo chifuwa chouma, kupuma pang'ono, kupweteka kapena kupweteka pachifuwa.
Anthu ena omwe ali ndi sarcoidosis amakhala ndi zizindikiro za khungu monga chiphuphu chokhala ndi zofiira zofiira kapena zofiira.
Lymphoma
Lymphoma ndi imodzi mwa "khansa ya magazi," kapena matenda a hematologic malignancies, mawu omwe amakhalanso ndi leukemias ndi myeloma . Lymphoma ndi khansa ya maselo oyera a m'magazi a lymphocyte. Pali mitundu yosiyanasiyana ya lymphoma.
Ambiri, koma osati onse, amayamba kutuluka m'mimba.
Mitundu ikuluikulu ya lymphoma ndi Hodgkin (HL) komanso non-Hodgkin (NHL) lymphoma. Mitundu yonseyi ili ndi mitundu yambiri komanso yowonjezera mkati, yomwe imakhala ndi matenda osiyanasiyana.
Ma Hodgkin ndi omwe si a Hodgkin lymphoma angakhudze mitsempha ya pachifuwa - dera pafupi ndi mtima wotchedwa Mediastinum. Sarcoidosis imaphatikizaponso malo amenewa.
Sarcoidosis ndi Lymphoma
Kwa zaka zambiri, ofufuza akhala akudabwa za kugwirizana pakati pa sarcoidosis ndi lymphoma. Ubalewu umakhala wosamvetsetseka ngakhale lero, pa zifukwa zingapo.
Malinga ndi kagulu ka akatswiri omwe amaphatikizapo Ishida ndi anzake, "The commonty subtype ya malignant lymphoma yokhala ndi sarcoidosis ndi Hodgkin lymphoma, koma kufalikira kwakukulu kwa B-cell lymphoma, follicular lymphoma, ndi multipleeloma zingakhale zovuta ku sarcoidosis-lymphoma syndrome. "Dzina lakuti" Sarcoid-lymphoma syndrome "linaphatikizapo kufotokoza zotsatirazi.
Zozizwitsa zodziwika bwino za sarcoidosis ndi zosakanikirana, zopangidwa ndi maselo a chitetezo cha mthupi omwe ali ndi ma lymphocytes. Zikuwoneka kuti ma lymphomas nthawi zina amakhala ndi "granulomas" mu khansara - ndipo kusinthaku, ngakhale kosawerengeka, kumaganiziridwa kuti mwina kumateteza ku chitetezo cha khansa, osati matenda a systemic, sarcoidosis.
Mapepala omwe asindikizidwa zaka zingapo zapitazo adanena kuti kusiyanitsa pakati pa zokhudzana ndi zotupa ndi zowona sarcoidosis kungakhale kovuta.
Sarcoidosis ndi lymphoma zimatha "kuunika" pa PET zowonongeka, kuwonjezera kuvuta ndi zomwe zingathe kusokoneza gawo limodzi. Ochita kafukufuku akuyitanitsa kuti apitirize maphunziro kuti ayambe ntchito zachipatala za FDG-PET / CT kwa odwala omwe ali ndi sarcoidosis.
Mwachidule, mafunso ambiri okhudza sarcoidosis-lymphoma syndrome sakhala ndi mayankho.
> Zotsatira:
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Mellemkjaer L, Pfeiffer RM, MASE EA, Gridley G, Wheeler W, Hemminki K, Olsen JH, Dreyer L, Linet MS, Goldin LR, Landgren O. Kugonjetsa matenda kwa anthu payekha komanso anthu a m'banja mwathu komanso kulandira mankhwala omwe sali a Hodgkin. Arthritis Rheum . 2008; 58: 657-666.
Reich JM, Mullooly JP, Johnson RE. Kusanthula kugwiritsidwa ntchito kwa sarcoidosis. Chifuwa. 1995; 107: 605-613
National Heart Lung ndi Magazi Institute. Kodi Sarcoidosis Ndi Chiyani? Idapezeka mu January 2016.
Goswami T, Siddique S, Cohen P, BSON wa Cheson. Matenda a sarcoid-lymphoma. Kliniki Lymphoma Myeloma Leuk . 2010; 10: 241-247.