Mycosis fungoides (MF) ndi yowonjezereka kwambiri ya T-cell lymphomas , gulu la khansa yochepa yomwe imakula pakhungu. Matenda a Sezary, mawonekedwe ochepa kwambiri, amapezeka pafupifupi 5% mwa milandu yonse ya mycosis fungoides. Ku United States, pafupifupi zikwi 1000 zatsopano za mycosis fungoides zimachitika pachaka.
MF imakhudza amuna kawiri nthawi zambiri monga amai, ndipo imafala kwambiri kwa anthu akuda kuposa anthu oyera.
Mycosis fungoides ikhoza kuyamba pa msinkhu uliwonse, koma zaka zambiri zedi ndi zaka 50. Chifukwa cha matendawa sichikudziwika.
Zizindikiro za Mycosis Fungoides
Mycosis fungoides ikukula muzigawo, zomwe zikutanthauza zizindikiro za khungu, kuphatikizapo:
- Gawo lachigamba - Khungu limapanga mapepala apamwamba, ofiira; Anthu omwe ali ndi khungu lamdima amatha kuwoneka ngati zowala kwambiri kapena zamdima. Izi zimakhala zovuta kwambiri. Madera ena akhoza kukwezedwa ndi ovuta, ndipo amadziwika kuti plaques. Zingwe ndi mabala amapezeka nthawi zambiri pamabowo, kubuula, m'chiuno, pansi pa mikono, komanso pachifuwa / pachifuwa.
- Gawo la minofu ya khungu - Red-violet imatulutsa mitsempha (mitsempha) imaonekera ndipo ikhoza kukhala yoboola (ngati bowa) kapena kukhala ndi zilonda zam'mimba.
- Khungu lofiira (erythroderma) siteji - Kuphatikizana ndi ziboliboli ndi zotupa, khungu la munthu likhoza kukhala ndi malo akuluakulu ofiirira omwe ndi ovuta kwambiri komanso osowa. Mabala a khungu pamaso angawoneke, ndipo khungu la mitengo ya palmu ndi mapeyala lingayambitse ndi kusweka.
- Zilonda zamatenda - Panthawiyi, mycosis fungoides imayamba kusuntha kumbali zina za thupi. Malo oyambirira omwe amakhudzidwa ndi amphithi, omwe amatha kutenthedwa, ndipo nthawi zambiri amakhala khansa. Khansa ya MF ingafalikire ku chiwindi, mapapo, kapena mafupa.
Kuzindikira kwa Chikhalidwe
Matendawa amadziwika kuti Alibert-Bazin syndrome kapena granuloma fungoides.
Kawirikawiri, pamakhala zaka zisanu ndi chimodzi kuchokera nthawi yomwe zizindikiro zimayambira mpaka matenda a mycosis fungoides. Ndili ndi matendawa, chisokonezo ndi zinthu zina zimakhala zachilendo pomwe matenda oyambirira a matendawa amafanana ndi dzuwa kapena psoriasis.
Kuti muzindikire bwinobwino mycosis fungoides, khungu la khungu lingatengedwe ( khungu la chikopa ) ndi kufufuza matendawa. Mayesero a Laboratory angathe kuchitidwa kuti adziwe kukula kwa khansara.
Kuti mumvetse magawo osiyanasiyana a matendawa, mayesero osiyanasiyana amachitidwa kuti aunike maselo, magazi ndi ziwalo zamkati. Odwala ambiri amasonyeza zizindikiro zomwe zimangokhala khungu, monga mabala (malo ophatikizira) ndi mapepala (mawanga ochepa kapena 'makwinya').
Kuchiza kwa MF
Ngati mycosis fungoides ili pachiyambi, mankhwala monga steroid creams, mankhwala othandizira, mankhwala a chemotherapy amagwiritsidwa ntchito pakhungu, kapena kuwala kwazitsulo za electron. Cholinga chake ndi kuika khansara ya MF mu chikhululukiro, chomwe chimatha nthawi yaitali.
Ngati matenda a munthu sakulabadira pakhungu, kapena matendawa apita patsogolo, pamakhala njira zochiritsira zomwe zimagwiritsidwa ntchito ngati mankhwala ovomerezeka a alfa interferon kapena chemotherapy . Mwamwayi, palibe mankhwala a mycosis fungoides, kotero kuti nthawi yochuluka yomwe munthu amakhala nayo ndi matendayo imadalira kutalika kwake komwe kwafalikira panthawi yomwe amapezeka ndi mankhwala akuyamba.
Chitsime:
Pinter-Brown, LC (2002). Mycosis fungoides. eMedicine.