Kuchepetsa matenda oopsa kwambiri ndi matenda aakulu koma palibe mankhwala, malinga ndi National Heart, Lung, ndi Blood Institute. Mapiritsi afupipafupi omwe amawopsa kwambiri amatha kuchitidwa kapena amapezeka chifukwa cha chikhalidwe china.
Zimayambitsa matenda opatsirana
Kuchepetsa matenda oopsa kwambiri (kapena kuthamanga kwa magazi m'mapapo) ndizosavuta koma matenda aakulu kwambiri.
Vutoli, losagwirizana ndi kuwonjezereka kwa magazi (hypertension), limayambitsidwa ndi kutaya kwa mapapu komanso kutayika kwa kusintha kwa thupi (mapulaneti) omwe amachititsa kuti magazi abwererenso m'mapapo.
Mafupa Ophatikizidwe Ophatikizidwa ndi Kuthamanga Kwambiri Kwambiri
Kuchulukitsa matenda oopsa kumakhudzana ndi zikhalidwe zingapo. Odwala omwe ali ndi vuto lalikulu la mapapo (fibrosis monga momwe amachitira scleroderma ndipo nthawi zina zimakhala ndi nyamakazi ), pali mphamvu ya m'mapapo yotsika kwambiri kuti mtima uwonjezere kupsinjika kofunikira kuti ukankhire magazi kupyolera mu mitsempha ya pulmonary m'mapapu. Odwala ena amayamba kupanikizika chifukwa cha kupopera kwa mitsempha. Izi zikhoza kuwonedwa muzochitika monga scleroderma (nthawi zambiri mu mawonekedwe ochepa otchedwa CREST) kapena kawirikawiri lupus (systemic lupus erythematosus). Posachedwa mtundu uwu wamapiritsi wambiri waumphawi unapezeka kuti umagwirizanitsidwa ndi mankhwala osokoneza bongo omwe sali pamsika.
Zizindikiro
Zizindikiro za matendawa zikuphatikizapo kupuma ndi kupweteka pachifuwa. Kusanthula kungatanthauzidwe ndi ultrasound ya mtima (ie echocardiogram) yosadziwika. Catheterization ya mtima (catheterization ya mtima) yomwe imakhala ndi zoopsa zamankhwala nthawi zambiri zimatsimikiziridwa kuti zitsimikiziridwa.
Chithandizo
M'mbuyomu, panalibe mankhwala ochepa omwe angapezeke chifukwa cha vutoli lomwe linasokonekera.
Mwamwayi, pali mankhwala atsopano omwe angathandize odwala omwe ali ndi matendawa kuphatikizapo:
- epoprostenol (mankhwala ochepa omwe amafunika kupitilira kulowetsedwa ndi lalikulu IV)
- treprostinil (yomwe imayendetsedwa ndi kuperewera kwapakati pa subcutaneous)
- bwana wamwamuna (wapatsidwa mlomo)
- sildenafil (yoperekedwa pamlomo)
- iloprost (inalumikizidwa)
Mankhwala othandizira amaphatikizapo mpweya, ochepa magazi, diuretics ndi kukonzanso mtima kwa cardiopulmonary. Ngati mukupezeka ndi vuto ili, ndibwino kuti muwone mapapo dokotala yemwe ali ndi luso la matendawa.
Yankho loperekedwa ndi Scott J. Zashin, MD, pulofesa wothandizira wathandi ku University of Texas Southwestern Medical School, Division of Rheumatology, ku Dallas, Texas. Dr. Zashin nayenso akupita kuchipatala ku chipatala cha Presbyterian ku Dallas ndi Plano. Iye ndi mnzanga wa American College of Physicians ndi American College of Rheumatology ndi membala wa American Medical Association. Dr. Zashin ndi mlembi wa Arthritis Popanda Mavuto - Chozizwitsa cha Anti-TNF Blockers ndi wolemba wa Matenda a Matenda a Nyamakazi .