Mafilimu Pafupipafupi Matenda ndi Matenda Oipa

Mafilimu Amene Amadzetsa Kuzindikira Zambiri Zosakwanira

Matenda ndi matenda nthawi zambiri zimakhala za mafilimu opangidwa ndi mafilimu, opangidwa molakwika, opangidwa ndi TV. Sizomwezo ndi mafilimu asanu awa. Mafilimu onsewa amafotokoza za matenda omwe sali osowa kwambiri omwe ali m'gulu la filimuyi; osati kungokhalira kumangokhalira kuchita zidazo.

Mafilimu owerengekawa anali otchuka kwambiri pakati pa ojambula mafilimu ndi ntchito zovomerezeka kwambiri, pamene ena amanyalanyazidwa ndi anthu; Kuwombera pa radar. Komabe, aliyense wa mafirimu amenewa ayenera kuwona. Iwo ali otsimikiza kuti asinthe malingaliro anu kuti akhale abwino mwa momwe mumawonera ndi kukambirana za matenda aakulu, koma osadziƔika, osowa kwambiri.

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Njovu (1980)
Onetsetsani mafilimu omwe amawadziwitsa za matenda ena omwe sapezeka. Silver Screen Collection / MoviePix / Getty Zithunzi

"Njovu Yamwamuna" ndi filimu ya 1980 yomwe inafotokoza John Hurt, Anthony Hopkins, Anne Bancroft ndi John Gielgud. Pafupi ndi aliyense amene adawona filimuyi imakonda, John Hurt akuwonetsa Joseph Merrick, wotchedwanso "Njovu Man" chifukwa cha zotsatira za zomwe Proteus anali nazo . Zovuta za Merrick zinamupangitsa kukhala munthu wosayenerera. Kukhumudwa kumawala pamene akuwonetsa munthu wanzeru, womvetsa chisoni kumbuyo kwa maski.

Poyambirira, ankaganiza molakwika kuti njovu imadwala matenda a neurofibromatosis , yomwe imakhala ndi mitsempha ya mitsempha. Njovuyi, mosiyana, inalibe mabala ofiira a neurofibromatosis, ndipo mmalo mwake, maphunziro a X-ray ndi CT a Merrick anachita mu 1996 anavumbula kuti zotupa zake zinakula kuchokera ku mafupa ndi khungu, zomwe zimadziwika ndi Proteus syndrome.

Chodziwikiratu ndi ichi kuti Merrick anakhala ndi moyo kuyambira 1862 mpaka 1890, koma matenda a Proteus sanazindikiridwe kufikira 1979. N'kutheka kuti pali mavuto ambiri omwe alipo lero omwe adzawonekere ndikumvetsetsanso m'tsogolo.

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Mafuta a Lorenzo (1992)

Nyuzipepala ya 1992 yakuti "Lorenzo's Oil" nyenyezi Hollywood heavyweights Susan Sarandon ndi Nick Nolte. "Mafuta a Lorenzo" akufotokozera nkhani ya makolo Augusto ndi zovuta za Michaela Odone kuti apeze mankhwala kwa mwana wawo Lorenzo wa adrenoleukodystrophy (ALD), matenda opweteka achibadwa. Mafilimuwa amapereka chithunzi chokhudza mtima, chachisokonezo cha matendawa, omwe ali ndi matenda a mitsempha, koma pali zolakwika zina. Komabe, mudzasangalala chifukwa cha kupambana kwa banja.

Adrenoleukodystrophy ndi matenda obadwa nawo, omwe amachokera ku autosomal recessive pattern yomwe ikugwirizana ndi X chromosome. Choncho, matendawa amapezeka mwa anyamata okha. (Phunzirani zambiri za machitidwe omwe ali nawo m'mavuto a majini .)

Matendawa akupita patsogolo, kuphatikizapo kufa kwa myelin, mofanana ndi matenda ena monga multiple sclerosis . Myelin amachita ngati kuvala pa chingwe cha magetsi, ndipo "chophimba" ichi chikuwonongedwa, kufalikira kwa chidziwitso kudutsa mitsempha kumachepa.

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The Tic Code (1998)

"Tic Code" nyenyezi Christopher Marquette, Gregory Hines ndi Polly Draper. Mnyamata wazaka 10 (Marquette) ndi woseƔera wa saxophone (Hines) amakumana ndikupeza kuti onse awiri ali ndi matenda a Tourette. Komabe, aliyense amachita nawo njira yakeyo. Mnyamatayu wasintha kwa ma teki, koma mwamuna wachikulire amayesera kubisala ndi kumutsutsa maganizo a mnyamatayo.

Pali njira zingapo zomwe izi zimachitikira, koma momwe zimayanjanidwira m'mafilimu-ndi mawu osayenera ndi manja-ndizosazolowereka.

Zikondwerero pano pali mankhwala angapo omwe angathandize anthu awa-omwe nthawi zambiri amayang'anizana ndi Tourette pa nthawi yaunyamata kuti ayambe kukwatira.

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Wamphamvu (1998)

"Wamphamvu" ndi filimu yosangalatsa yomwe simunayambe mwamvapo, yowunikira Sharon Stone, Gena Rowlands, ndi Harry Dean Stanton. Kevin ndi mwana wazaka 13 yemwe ali ndi matenda a Morquio, matenda otukuka, ndipo Max, mwana wochepetseka yemwe ali ndi nzeru zochepa-amamverera kuti amawoneka ngati "Godzilla" -momwe amadziwira. Awiriwo amapanga ubwenzi wosayembekezeka pamene Kevin akukhala Max akuwerenga.

Matenda a Morquio omwe amachokera ku autosomal fashion fashion amaonedwa kuti ndi amodzi mwa mucopolysaccaridoses (MPS), matenda omwe amayamba chifukwa cha kuchepa kwa michere yomwe imayenera kuchitika m'thupi. Matenda a Morquio amaonedwa ngati MPS IV, pomwe matenda a Hurler omwe anthu amadziwika nawo amawatcha MPS I kapena II. Matendawa ali ndi mbali zambiri zochokera ku ziphuphu zamphongo ndi zowonongeka, kukhumudwitsa mtima, kuphulika, ndi zina zambiri.

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Chimwemwe Chachisanu ndi chimodzi (1997)

Filamu iyi ya 1997 "Chisangalalo Chachisanu ndi chimodzi" yomwe Firdaus Kanga ndi Souad Faress anamasulidwa ku United Kingdom. Zachokera pa mbiri ya Kanga, yotchedwa "Kuyesa Kukula." Kanga amasewera yekha mufilimuyi. Firimuyi imalongosola nkhani ya mnyamata wina wotchedwa Brit akukula ku India. Iye wabadwa ali ndi matenda omwe amachititsa mafupa ake kukhala otupa ndipo samakula konse kuposa mamita atatu. Brit ndi chinthu chokongola, chodabwitsa, komanso chodziwika bwino chomwe chimayesetsa kugonana ndi mavuto a moyo mwanjira yake yapadera, koma makolo ake ali ndi malingaliro osiyana kwambiri pa umoyo wake.

Ngakhale kuti filimuyi siyikulongosola matenda ena omwe sapezeka (ngakhale kuti ikugwirizana ndi osteogenesis imperfecta m'njira zambiri) ikhoza kuthandizira kuzindikira za matenda angapo ochepa komanso osazolowereka omwe amaphatikizapo mafupa osakanikirana ndi amodzi.

Osteogenesis imperfecta ndi matenda omwe apangidwa "brittle bone matenda." Matendawa amachokera ku vuto linalake la collagen lomwe limapezeka mu fupa, ligaments, ndi diso, ndipo nthawi zambiri imabweretsa mafupa ambiri osweka kuphatikizapo msinkhu. Pali mitundu yosiyana ya matendawa, molimbika mosiyana kwambiri kwa omwe ali ndi matenda ofanana. Mwamwayi, kupita patsogolo kwa chithandizo chamakono, monga matenda opatsirana mitsempha, kumathandiza kusintha miyoyo ya ena mwa anthuwa.

Thupi lalifupi limatchulidwa ngati lachilendo pamene msinkhu wamkulu amakhala ndi masentimita khumi kapena khumi kapena khumi ndipo amakhala ndi zifukwa zambiri.

Kuwonjezera pa mafilimu omwe amawadziwitsa za matenda omwe sapezeka, anthu omwe ali ndi zina mwazimenezi adagwiritsa ntchito chikhalidwe chawo m'njira yodalirika yowonetsa ndalama. Chitsanzo ndi John Ryan Evans , woimba ndi achondroplasia, ndi udindo wake muzinthu zambiri kuphatikizapo momwe Grinch anagonjetsera Khrisimasi .

Zotsatira:

Laibulale ya National National Medicine. Morquio Syndrome. Kusinthidwa 04/20/1. https://medlineplus.gov/ency/article/001206.htm

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