Mapazi Akuvina Kudya
Matenda a Opsoclonus-myoclonus (OMS) ndi matenda opatsirana a ubongo. Zimayambitsa mavuto akuluakulu pamagalimoto, kayendetsedwe ka diso, khalidwe, kusokonezeka kwa chinenero ndi mavuto ogona. Nthawi zambiri imabwera mwadzidzidzi ndipo imakhala yachilendo; ngati mwapezeka ndi opsoclonus-myoclonus syndrome, zikhoza kukhalapo m'moyo wanu wonse.
Dzina lake limafotokoza zizindikiro zake: opsoclonus ikungoyendetsa maso ndi maso a myoclonus amatanthauza kusokonezeka minofu. Amadziwikanso kuti "Kinsbourne syndrome" kapena "kuvina-kuvina-mapazi."
Amene ali pangozi
Mu matenda osokonekera , thupi limasokoneza maselo ake abwino. Matenda a Opsoclonus-myoclonus amachokera ku matenda omwe amachititsa kuti thupi likhale ndi ma antibodies omwe ali ndi kachilombo ka HIV kapena chifuwa chotchedwa neuroblastoma. Mulimonsemo, ma antibodies amatha kuwononga maselo a ubongo, ndipo izi zimayambitsa kuwonongeka kumene kumabweretsa zizindikiro.
Matenda a Opsoclonus-myoclonus amapezeka kawirikawiri ana. Ana ali ndi zaka zomwe nthawi zambiri matenda a neuroblastoma amayamba; pafupifupi anayi peresenti ya ana awa adzakhala ndi OMS. Mwana aliyense yemwe ali ndi HIV adzayesedwa kuti awone ngati ali ndi chotupa, ngakhale atakhala ndi kachilombo koyambitsa matendawa kuyambira nthawi ziwiri.
Chithandizo
Chodetsa nkhaŵa kwambiri ndi opsoclonus-myoclonus syndrome ndi matenda oyamba omwe amachiritsidwa ndi kuchiritsidwa kuti akwaniritse chikhululukiro cha matenda ndi ubongo. Ngati mwana ali ndi opsoclonus-myoclonus syndrome ndipo ali ndi chotupa, chotupacho chimachotsedwa opaleshoni. Kawirikawiri, zotupazo zimayambira kale ndipo mankhwala ochizira kapena mankhwala osakanikirana ndi mankhwala sagwiritsidwa ntchito.
Nthawi zina izi zimawathandiza kapena kuthetsa zizindikiro. Kwa akuluakulu, kuchotsa zotupa nthawi zambiri sikuthandiza ndipo zizindikiro zikhoza kuipiraipira.
Mankhwala ena ndi awa:
- Majekesiti a Adrenocorticotrophic hormone (ACTH)
- Matenda a immunoglobulins osatetezeka - kukonzekera malonda a antibodies kuchokera kwa opereka magazi
- Azathioprine (Imuran) - imatsitsa chitetezo cha mthupi, chomwe chimachepetsa kupanga ma antibodies
- Mankhwala odzudzula ndi am'kati, monga prednisone, dexamethasone, ndi hydrocortisone
- Chemotherapy monga cyclophosphamide ndi methotrexate, kwa ana omwe ali ndi neuroblastoma
- Mankhwala apheresis - kusinthanitsa magazi a m'magazi
- Kutuluka kwadzidzidzi - kuyeretsa ma antibodies kuchokera m'magazi kuyesedwa kwa akuluakulu omwe ali ndi HIV.
Njira zochiritsira zomwe zimakhalapo nthawi zambiri zimakhala zofunikira kuti nthawi zonse ziziyenda bwino komanso kuchepetsa chiwopsezo chobwerera.
Kuthamangitsani
Anthu omwe ali ndi mwayi waukulu kwambiri wobwereranso kuchipatala ndi omwe ali ndi zizindikiro zochepa kwambiri. Amene ali ndi zizindikiro zoopsa akhoza kukhala ndi mpumulo wa myoclonus koma amakhala ndi vuto ndi kugwirizana. Matenda ena omwe amabwera chifukwa cha kuvulala kwa ubongo, monga vuto la kuphunzira ndi khalidwe, kusamala-kuchepa kwa matenda osokoneza bongo (ADHD) ndi matenda osokoneza maganizo, amatha kuchitika, ndipo awa angafunike chithandizo chawo.
Ana omwe ali ndi zizindikiro zoopsa kwambiri za OMS akhoza kukhala ndi kuwonongeka kwa ubongo kosatha zomwe zingayambitse kufooka kwa thupi ndi m'maganizo.
Kukula
Opsoclonus-Myoclonus Syndrome ndi yosavuta; Anthu 1 miliyoni okha amakhulupirira kuti ali ndi vuto padziko lapansi. Izi zimawonedwa mwa ana ndi akulu, koma zimakhudza akuluakulu. Amapezeka kawirikawiri kwa atsikana kusiyana ndi anyamata ndipo amapezeka ngati atatha miyezi isanu ndi umodzi.
Zotsatira:
Pranzatelli, M. "Vital Signs: Wokoma Moto." Discove r, 2000.
Pranzatelli, M. "Opsoclonus-Myoclonus Syndrome". National Organization for Rare Disorders, 2016.