Myelofibrosis yapamwamba kapena idiopathic, yomwe imadziwikanso kuti agnogenic myeloid metaplasia, ndi matenda a mafupa omwe mafupa amakhala ndi minofu ndipo amabala maselo osadziwika. Idiopathic myelofibrosis ndi chimodzi mwa mavuto a myeloproliferative . Matendawa amakhudza amuna ndi akazi ndipo nthawi zambiri amapezeka kuti ali pakati pa zaka 50 mpaka 70, koma akhoza kuchitika pa msinkhu uliwonse.
Zikuyembekezeka kuti zichitike m'modzi mwa anthu 1,000,000.
Zizindikiro
Anthu pafupifupi 25% omwe ali ndi myelofibrosis idiopathic alibe zizindikiro. Amene ali ndi zizindikiro akhoza kukhala:
- Nkhungu yotambasula, yomwe imayambitsa zovuta kumimba kumtunda-kumanzere kapena kupweteka kumtunda kumanzere
- Zofooka, kutopa
- Kupuma pang'ono
- Kutaya thupi
- Kutuluka kwa usiku
- Magazi osadziwika
Mitundu ina yoopsa ya myelofibrosis ya idiopathic ikhoza kukhala ndi:
- Mankhwala opangidwa ndi maselo a m'magazi omwe angapangidwe kunja kwa fupa mumatupi aliwonse m'thupi
- Kutsika kwa magazi kumathamangira ku chiwindi, kutengera ku chikhalidwe chotchedwa "portal hypertension"
- Mitsempha yolekanitsa yomwe imapezeka m'mimba, yomwe imadziwika kuti imaphageal varices, yomwe imatha kutha.
Kudziwa
Kwa anthu omwe alibe zizindikiro, idiopathic myelofibrosis ikhoza kupezeka pamene kafukufuku wamankhwala amapezeka kuti akupeza nthenda yotambasula komanso zotsatira zowononga magazi. Zotsatirazi zikhoza kusonyeza maselo ofiira ochepa omwe amachititsa kuti magazi asapitirire kuwonjezereka.
Anthu ena, komabe, angasonyeze kusintha pang'ono mu chiwerengero cha maselo a magazi.
Pamene zitsanzo za magazi a munthu payekha zimayang'aniridwa ndi microscope, maselo osadziwika a magazi amatha kuwoneka. Mayeso ena a magazi angakhale osalinso. Pofuna kuthandizira kutsimikizira kuti matendawa ndi a myelofibrosis, chitsanzo cha mafupa (biopsy) chidzatengedwa ndikuyang'anitsidwa pansi pa microscope kuti pakhale ma fibrosis.
Chithandizo
Anthu omwe alibe zizindikiro kawirikawiri samachiritsidwa. Mayeso a magazi amachitika nthawi zonse kuti ayang'ane matendawa.
Kwa omwe ali ndi zizindikiro, chithandizo chimadalira kuthetsa mavuto ndi kuchepetsa chiopsezo cha mavuto. Anthu omwe ali ndi vuto la kuchepa kwa magazi amatha kulandira chitsulo, masewera ndi / kapena kuika magazi. Ena akhoza kumwa mankhwala, monga Deltasone (prednisone) kapena Zometa (zoledronic acid).
Anthu omwe ali ndi maselo ambiri amagazi akhoza kupatsidwa mankhwala, monga Hydrea (hydroxyurea), Agrylin (anagrelide) kapena interferon alfa.
Anthu ena amafunika kuti opaleshoni ichotsedwe (splenectomy), makamaka ngati ikuchititsa mavuto. Mankhwala ena angaphatikizepo mankhwala opatsirana pogwiritsa ntchito mpweya kapena mpweya wa mafupa (stem cell) .
Chiwonetsero
Kawirikawiri, anthu omwe ali ndi myelofibrosis amadzipulumuka kwa zaka zisanu pambuyo pozindikira kuti ali ndi matendawa. Pafupifupi 20 peresenti ya anthu omwe ali ndi matendawa, amakhalabe ndi moyo zaka 10 kapena kuposa. Ziwerengerozi zikuwonjezeka pakapita nthawi monga mankhwala atsopano akupangidwira ndipo kafukufuku amathandiza kudziwa za matendawa.
Zotsatira:
> "Idiopathic Myelofibrosis." Malingaliro a Matenda. 24 Sep 2007. Leukemia & Lymphoma Society.
> Niblack, Joyce. "MF FAQ." MPD-FAQS. 3 Feb 1999. MPD Research Center, Inc.