Ngati mwauzidwa kuti muli ndi matenda ambiri a endocrine neoplasia (MEN), ndiye mukudziwa kuti pali kufufuza kwakukulu komanso chithandizo cha vutoli.
Tanthauzo la AMEN
Ambiri otchedwa endocrine neoplasia (AMEN) ndi matenda omwe amadziwika ndi kukhala ndi chotupa chimodzi cha ziwalo za endocrine nthawi imodzi. Pali mitundu yosiyanasiyana ya zotupa za endocrine zomwe zimadziwika kuti zikuchitika palimodzi, ndipo mndandanda uliwonsewu umagawidwa ngati mmodzi mwa mitundu yosiyana (MEN) syndromes.
Ziphuphu zomwe zimakhala ngati gawo la matenda a Edzi amodzi zingakhale zoopsa kapena zosautsa. Matenda a Benign ndi zotupa zochepa zomwe zingayambitse zizindikiro zachipatala koma zimakula pang'onopang'ono, osati kufalikira kumbali zina za thupi ndipo sizifa. Matenda opweteka kwambiri , omwe ali ndi khansa yomwe imatha kukula mofulumira, ingafalikire ku mbali zina za thupi, ndipo ikhoza kupha ngati sichitsatiridwa.
Zizindikiro
Pali ma syndromes atatu omwe amaonedwa kuti ndiwo amodzi omwe amadziwika ndi syndromes. Matenda aliwonse amayamba chifukwa cha mtundu wambiri wosalongosoka, zomwe zikutanthauza kuti chotupacho chimagwirizanitsa ndi mabanja monga cholowa. Mayi syndromes amatchedwa AMENI 1, MEN 2A, ndi AMEN 2B.
Amuna 1: Anthu omwe amapezeka ndi AMENI 1 ali ndi zotupa za ntchentche, nthenda ya parathyroid, ndi ziphuphu. Kawirikawiri, zotupazi ndi zabwino, ngakhale kuti sizingatheke kuti zikhale zoipa.
Amuna 1 Zizindikiro: Zizindikiro za AMENI 1 zimatha kuyamba ali mwana kapena akakula.
Zizindikiro zake zimakhala zosiyana chifukwa zotupa zimaphatikizapo ziwalo za endocrine zomwe zingathe kupanga zotsatira zambiri pa thupi. Matenda onsewa amachititsa kusintha kosasintha kokhudzana ndi kutayika kwa mahomoni.
- Matenda opuma amachititsa mutu , kusamba kwa msambo, kusabereka, kuyamwa mkaka, ndi kupitirira kwa mafupa.
- Matenda opweteka amachititsa ululu m'mimba, kusanza, kutsegula m'mimba, ndi zilonda.
- Zikodzo za parathyroid zimayambitsa ma calcium okwera kwambiri, omwe angapangitse impso miyala kukhala chizindikiro choyamba choonekera.
Amuna 2A: Anthu omwe ali ndi AM 2 ali ndi zotupa za chithokomiro, zotupa zamatenda, ndi zotupa za parathyroid.
AMENYE 2A Zizindikiro: Zizindikiro za AMENYE 2A zimayamba pakukula; kawirikawiri pamene munthu ali ndi zaka 30. Mofanana ndi ma syndromes ena a MEN, zizindikiro zimachokera ku kuchitapo kanthu kwa zotupa za endocrine.
- Matenda a chithokomiro kaŵirikaŵiri amayamba kuwoneka m'mimba mwa MEN 2A, ndipo amatha kupweteka kapena kupanikizika m'dera la khosi, ndipo amatha kukhala oipa.
- Matenda a adrenal, otchedwa pheochromocytoma , makamaka amaphatikizapo gawo la adrenal gland wotchedwa adrenal medulla. Pheochromocytoma ikhoza kuyambitsa kuthamanga kwa magazi, kuthamanga mtima kwa mtima, ndi thukuta.
- Matenda a parathyroid angabweretse mchere wambiri wa calcium, ndipo zizindikirozo zingakhale ndi ludzu lokwanira komanso kukodza nthawi zambiri.
Amuna 2B: Izi ndizosazolowereka pamatenda oterewa ndipo amadziwika ndi chifuwa cha chithokomiro, chiberekero cha adrenal, neuromas (cysts) m'kamwa komanso minofu, zosaoneka bwino za mafupa, ndi msinkhu wamtali ndi wamtundu wodabwitsa womwe umatchedwa marfanoid Mawonekedwe.
AMENYE 2B Zizindikiro: Zizindikiro zimayambira muubwana, nthawi zambiri asanakwanitse zaka 10. Chizindikiro chodziwika bwino cha MEN 2B ndi mawonekedwe aatali, okongola. Neuromas amawoneka ngati kukula mkati ndi kuzungulira mkamwa, ndipo anthu okhala ndi Amuna 2B akhoza kukhala ndi vuto m'mimba ndi m'mimba, kuphatikizapo zizindikiro za khansa ya chithokomiro ndi pheochromocytoma.
Kudziwa
Dokotala wanu angakhale okhudzidwa kuti mutha kukhala ndi matenda a ANTHU pogwiritsa ntchito chithunzithunzi cha chotupa cha endocrine, limodzi ndi mbiri ya banja lanu. Simukusowa kukhala ndi zotupa zonse za siginito za amuna omwe ali ndi HIV kwa dokotala wanu kuti aganizire ANTHU. Ngati muli ndi chotupa choposa chimodzi, kapena ngakhale muli ndi chotupa chokhacho chokhudzana ndi Amuna, ndiye kuti dokotala wanu angakuyang'anitseni matenda ena asanakhale owonetsa.
Mofananamo, mbiri yakale ya banja sichifunika kuti anthu azidziŵa, chifukwa munthu akhoza kukhala woyamba m'banja. Matenda omwe amachititsa kuti anthu azidziwika, ndipo kuyesa kwa majeremusi kungakhale njira yotsimikiziranso kuti matendawa ndi otani.
Palinso kusiyana kwakukulu ndi vuto lililonse la Amuna-mukhoza kukhala NDI AMAMUNTHU ngakhale mutakhala kuti simukugwirizana bwino ndi matenda.
Chithandizo
Chithandizo cha ma syndromes onse a MEN chimadalira pa zinthu zingapo zosiyana. Sikuti aliyense amene amapezeka ndi MEN 1, MEN 2A, kapena MEN 2B ali ndi matenda omwewo. Kawirikawiri, mankhwala akugwiritsidwa ntchito pa zolinga zazikulu zitatu, zomwe zimaphatikizapo kuchepetsa zizindikiro, kupezetsa zotupa msanga, ndikupewa zotsatira za zotupa zakupha.
Ngati muli ndi zizindikiro zowonongeka kwa mahomoni, mudzafunikira chithandizo cha zizindikirozi. Matenda a endocrine nthawi zambiri amasinthasintha m'kupita kwa nthawi, chifukwa ziwalo za endocrine zimagwira ntchito molingana ndi kulingalira kwabwino ndi zolakwika. Izi zikutanthauza kuti mahomoni omwe amatha kugwira ntchito mopitirira muyeso angathe kuthetsa kapena kupangitsa kuti mahomoni ena apangidwe m'thupi. Choncho, ngakhale mutalandira chithandizo cha mahomoni kwa kanthawi, mungafunike mankhwala osiyana kapena kusintha kwa mlingo wanu m'tsogolomu.
Mbali zina zofunika za chithandizo cha MEN zimaphatikizapo kuyang'anitsitsa ndi kuyang'anitsitsa kuti adziwe zotupa zatsopano ndikuwona zolakwika zonse mwamsanga. Matenda opweteka angafunikire kuwachiritsidwa ndi opaleshoni kapena chemotherapy musanapangitse mavuto aakulu a thanzi.
Mawu Ochokera
Mtundu uliwonse wa chotupa ukhoza kuwopsya. Ndipo kukhala ndi chotupa choposa ndi choopsa kwambiri. Ngati mwauzidwa kuti muli ndi multipleoprosia neoplasia, ndiye kuti mukudandaula kwambiri za zizindikiro zomwe zingayambitsenso ndikutsatira kuti ndibwino kuti mukhale ndi thanzi labwino.
Chowona kuti syndromes za MEN zimadziwika ndi kusankhidwa zimapangitsa kuti mkhalidwe wanu ukhale wodalirika kuposa momwe ungawonekere. Ngakhale kuti izi ndizochepa zachilombo, zimasuliridwa mwatsatanetsatane ndipo pali njira zothetsera matendawa. Ngakhale kuti mukusowa chithandizo chamankhwala chokhazikika, pali njira zothandiza zothetsera vuto lanu ndipo mukhoza kutsimikizika kuti ndi chithandizo chamankhwala chokwanira, mutha kukhala ndi zotsatira zabwino.
> Chitsime:
> Wasserman JD, Tomlinson GE, Druker H, et al. Mitundu Yambiri ya Endocrine Neoplasia ndi Hyperparathyroid-Ma Jaw Tumor Syndromes: Zochitika zachipatala, Zachibadwa, ndi Zowonongeka Pachiyambi. Clin Cancer Res . 2017 Jul 1; 23 (13): e123-e132.