Matenda a Marfan ndi matenda omwe anthu ambiri amabadwa nawo, omwe amachititsa chigoba, mtima, mitsempha ya magazi ndi maso. Anthu omwe ali ndi matenda a Marfan amakhala otalika komanso ofooka, ndipo miyendo ndi miyendo yawo ndi yaitali kuposa nthawi zonse. Nthawi zambiri amakhalanso ndi zala (zomwe zimachitika kuti madokotala azitcha arachnodactyly), kupopera kosavuta kwa msana ( kyphoscoliosis ), ndi kusokoneza diso la diso .
Matenda owopsa kwambiri a Marfan syndrome ndi ofanana ndi mtima ndi mitsempha; makamaka, ndi aneurysm ya aorta . Aneurysm ndi kusuntha (kutsegula kunja) kwa khoma la chotengera cha magazi. Kusungunuka kumeneku kumafooketsa kwambiri khoma la aorta, ndipo kumapangitsa kuti izi zitheke mosavuta (chikhalidwe chomwe madokotala amatcha dissection). Kuthamangitsidwa kwa Aortic ndizochitika mwamsanga zachipatala, ndipo zingayambitse imfa mwadzidzidzi mwa anthu omwe ali ndi matenda a Marfan.
Popeza kuti tsokali likhoza kuchitika panthawi yomwe mtima umagwedezeka, kuchita masewera olimbitsa thupi, makamaka, kungachititse kuti matenda a aortic asokonezeke. Pa chifukwa chimenechi, achinyamata omwe ali ndi matenda a Marfan ayenera nthawi zambiri kuchepetsa kuchita nawo masewera.
Sikovuta kwa achinyamata kuti amve kuti ntchito yawo ya thupi iyenera kuchepetsedwa. Mwamwayi, anthu ambiri omwe ali ndi matenda a Marfan akhoza kukhala achangu, koma ndi zoletsedwa.
Ndikofunikira kuti othamanga achinyamata adziŵe malire awo.
Malingaliro Odzidziwitsa Ambiri Kwa Atsikana Achinyamata Omwe Ali ndi Marfan Syndrome
Malingaliro ovomerezeka pakuchita nawo masewera olimbirana othamanga kwa othamanga omwe ali ndi Marfan syndrome anasindikizidwa ndi msonkhano wa 2005 wa Bethesda pa Zovomerezeka Zopindulitsa kwa Ochita Masewera Olimbitsa Thupi.
Pano pali chidule chazomwe akuyamikira:
Ochita masewera omwe ali ndi matenda a Marfan ayenera kukhala ndi mapulotechete miyezi isanu ndi umodzi kuti ayang'anire mizu ya aorta.
Ngati palibe mizu yambiri ya aortic kapena zovuta zina za mtima, ndipo palibe mbiri ya banja ya aortic dissection, iwo akhoza kutenga nawo mbali zomwe zimatchedwa zochepa, zolimbitsa thupi masewera - zinthu zomwe sizimasowa "kupasuka" kwapamwamba kwambiri zolimbitsa thupi. Zitsanzo za ntchito zoyenera zikuphatikizapo golf, bowling, hikingl, ndi tebulo tennis.
Ngati pali umboni wa mizu ya aortic, kapena mbiri ya banja ya aortic dissection, ndiye kuti ntchito yochepa kwambiri, monga golf kapena bowling, ndi yoyenera.
Anthu omwe ali ndi matenda a Marfan akulangizidwa kuti asatenge ntchito zoopsa - kucheza ndi masewera ndi zofunikira zomwe zimafuna kuchita masewera olimbitsa thupi omwe amachititsa njira ya Valsalva (monga kulemera kwa kulemera).
Anthu ena omwe ali ndi matenda a Marfan angathe kuchotsedwa mwachipatala ndi madokotala awo (ngati chiopsezo chawo chimaweruzidwa kuti ndi otsika), kuti achite nawo masewero enaake monga masewera a mpira, mpira, mpira wothandizira, ndi njinga.
Chochititsa chidwi ndi kuti msonkhano wa Bethesda unayankhula makamaka kwa anthu omwe akuchita nawo masewera olimbirana, okwera mpikisano.
Makamaka, amapereka malangizo kwa masukulu ndi mabungwe ena omwe ochita masewera omwe ali ndi matenda a Marfan angakhale akuyang'ana kuti athe kutenga nawo mbali pa mapulogalamu awo. Sindinayankhe mwachindunji wothamanga wokondwerera.
Komabe, mayankho a Bethesda akhozabe kupereka malangizo kwa osewera osangalala ndi madokotala awo. Kwa aliyense amene ali ndi matenda a Marfan amene akufuna kuchita masewera, nthawi zamakono zingagwiritsidwe ntchito kutsogolera ntchito yoyenera yogwiritsira ntchito.
Mawu Ochokera
Anthu omwe ali ndi matenda a Marfan amakhala ndi chiopsezo chachikulu kwa moyo wawo wonse chifukwa cha zoopsa za mtima, ndipo amafunanso kuti azitsatiridwa nthawi zonse.
Zoletsa zolimbitsa thupi zimalangizidwa kwa aliyense ali ndi Marfan syndrome. Komabe, mlingo woletsedwa udzasiyana pakati pa munthu ndi munthu, ndipo ambiri amatha (ndipo akulimbikitsidwa) kuti azisangalala ndi moyo wathanzi ndi zoyenera.
> Zotsatira:
> Hiratzka LF, Bakris GL, Beckman JA, et al. 2010 ACCF / AHA / AATS / ACR / ASA / SCA / SCAI / SIR / STS / SVM Malangizo Othandizira Kuzindikira ndi Utsogoleri Wa Odwala Amene Ali Ndi Matenda A Thoracic Aortic: lipoti la American College of Cardiology Foundation / American Heart Association Task Force on Practice Malangizo, bungwe la American Association for Psychological Surgery, American College of Radiology, American Stroke Association, Society of Cardiovascular Anesthesiologists, Society of Cardiovascular Angiography and Interventions, Society of Interventional Radiology, Society of Thoracic Surgeons, and Society for Vascular Medicine. Kuthamanga kwa 2010; 121: e266.
> Maron, BJ, Ackerman, MJ, Nishimura, RA, et al. Task Force 4: HCM ndi Other Cardiomyopathies, Mitral Valve Prolapse, Myocarditis, ndi Marfan Syndrome. J Am Coll Cardiol 2005; 45: 1340